Results 11 to 20 of about 8,291 (140)

全基因體定序對兒童神經疾病的診斷率和治療影響

open access: yesDevelopmental Medicine &Child Neurology, Volume 63, Issue 8, Page e1-e4, August 2021., 2021
目的 探討全基因體定序 (WGS) 對兒童神經疾病的診斷率及治療影響。 方法 從 2016 年 1 月至 2019 年 12 月, 使用全基因體定序對疑似患有遺傳性神經疾病的兒科病人進行評估。符合條件的病人依其臨床表現型分為四組: 神經發展障礙病人、癲癇病人、神經肌肉疾病病人及運動障礙病人。我們描述全基因體定序的診斷率及經全基因體定序確診後對病人治療的影響。 結果 共有 214 例病人 (男性 128 例, 女性 86 例) 接受了全基因體定序檢測, 病人平均 (SD) 發病年齡為 13.8 (27.6) 個月, 範圍為 1 天至 15 年 5 個月, 接受全基因體定序檢測的平均 (SD) 年齡為 71.7 (58.9) 個月, 範圍從 8 天到 18 歲。 43.9 ...
李 秀芬, 遲景 上, 蔡 啟仁
wiley   +1 more source

Reliably predicting pollinator abundance: Challenges of calibrating process‐based ecological models

open access: yesMethods in Ecology and Evolution, Volume 11, Issue 12, Page 1673-1689, December 2020., 2020
Abstract Pollination is a key ecosystem service for global agriculture but evidence of pollinator population declines is growing. Reliable spatial modelling of pollinator abundance is essential if we are to identify areas at risk of pollination service deficit and effectively target resources to support pollinator populations.
Emma Gardner   +18 more
wiley   +1 more source

A Multifunctional Reducing Molecular Dopant for 16% Efficient Tin Perovskite Solar Cells

open access: yesRare Metals, EarlyView.
ABSTRACT Although lead‐based photovoltaics have seen remarkable progress, tin‐based perovskite solar cells (Sn‐PSCs) continue to face challenges due to their limited power conversion efficiency and insufficient operational stability. The primary cause of this performance gap is the susceptibility of Sn2+ to oxidation, which promotes rapid defect ...
Xianyong Zhou   +12 more
wiley   +1 more source

连续雷击引发无间隙金属氧化物避雷器热崩溃的仿真分析

open access: yesDianci bileiqi, 2022
连续雷击是一个近年引起关注的变电站防雷新热点,位于变电站线路开关断口外线路侧的无间隙金属氧化物避雷器(包括高抗中性点避雷器)成为连续雷击侵入波防护的薄弱环节。笔者以某变电站高抗中性点避雷器在连续雷击下热崩溃故障作为案例,建立模型对避雷器吸收能量进行仿真分析,结果表明:在连续雷击工况下,避雷器电阻片累计吸收能量而发热易造成电阻片劣化;在电阻片劣化基础上,如果避雷器承受正常系统电压或者承受持续振荡电压,续流增大,最终发展到热崩溃的风险很高;在连续雷击风险较高的地区,应提高避雷器对连续雷击的能量吸收能力 ...
李谦   +4 more
doaj  

Exceptional Electromagnetic Wave Absorption in High‐Entropy Carbides Enabled by Lattice Distortion Engineering

open access: yesRare Metals, EarlyView.
ABSTRACT The growing concern over human health issues, driven by increasingly severe electromagnetic pollution from 5G communication, has made the urgent development of high‐performance electromagnetic wave (EMW) absorbing materials. Although carbide‐based materials are promising because of their conductive and polarization losses, existing single ...
Chenqiang Duan   +9 more
wiley   +1 more source

基于IGBT的新型固态直流断路器设计与分析

open access: yesGaoya dianqi, 2022
直流断路器是柔性直流输电系统组网的关键设备,对直流输配电网的安全性、稳定性有着重要的意义。文中提出了一种基于绝缘栅双极型晶体管(insulated gate bipolar transistor,IGBT)的新型固态直流断路器拓扑,在提高断路器切断电流能力的同时,提高了避雷器和IGBT的使用寿命。通过引入接地引流二极管,减轻避雷器吸收能量的压力,加快电流分断的速度。基于所提拓扑设计了10 kV的直流断路器模型,在PSCAD/EMTDC中进行了验证,仿真结果表明:基于所提出的方案,最大开断电流可达5kA ...
丁璨   +4 more
doaj  

SWEET1‐mediated glucose transport is crucial for energy availability in Arabidopsis

open access: yesNew Phytologist, Volume 249, Issue 4, Page 1816-1830, February 2026.
Summary The stress‐responsive hormone abscisic acid (ABA) is known for its inhibitory effects on various physiological processes, including seed germination, often resulting in energy deprivation. Interestingly, ABA‐induced germination inhibition can be alleviated by exogenous glucose (Glc), mimicking a functional interplay between ABA and sugar ...
Xueyi Xue   +3 more
wiley   +1 more source

Securing Bangladesh's Nuclear Future: Is the Regulated Asset Base Model the Answer to Address Project Corruption?

open access: yesJournal of Critical Infrastructure Policy, Volume 7, Issue 1, Spring/Summer 2026.
ABSTRACT Bangladesh's goal of achieving high‐income status by 2041 requires dependable, low‐emission, and affordable energy. With near‐universal grid coverage and increasing demand, nuclear energy is a strategic asset for long‐term baseload supply. However, the existing financing model, typified by the country's most expensive $12.65 billion Rooppur ...
Hafiz Ahmed
wiley   +1 more source

Investigations of Nucleation Mechanism in Initial Period for Direct Electroless Nickel-boron Plating on Magnesium Alloy and Electrochemical Properties of Plating Solution [PDF]

open access: yes, 2009
镁合金具有优良的性能,但是其耐蚀性差的特点限制了在生产和生活方面的广泛应用。本文研究了前处理后镁合金表面状态的变化,并利用扫描电子显微镜(SEM)、X射线衍射仪(XRD)、划痕试验以及电化学方法等技术综合表征在最优工艺条件下获得的镀层的形貌、结构、结合力和耐蚀性等性能。采用元素分析和镀层形貌相结合的方法探讨镀层初期形核机理。运用电化学手段,利用循环伏安技术研究了不同镀液组分浓度以及不同电极表面对镀液电化学性能的影响。 研究结果表明酸洗处理后,镁合金表面获得了一层银白色且具有网状结构的氧化膜 ...
彭淑合
core  

Optimization simulation and crushing experiment of anti-impact energy absorption component of hydraulic support column [PDF]

open access: yes
Hydraulic support, being the primary supporting equipment in coal mining operations, is frequently subjected to rock burst pressure. Hence, the anti-impact energy absorption components play a pivotal role in safeguarding the hydraulic support system ...
Liyong TIAN   +4 more
core   +1 more source

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