Results 71 to 80 of about 2,073,323 (298)

Cost Pass‐Through in Crisis: Evidence From the German Malt‐Beer Supply Chain

open access: yesAgribusiness, EarlyView.
Abstract Global agri‐food supply chains are increasingly exposed to geopolitical shocks, climate volatility, and market consolidation, factors that disrupt traditional price relationships and reshape market power dynamics. Nowhere is this more visible than in the brewing sector, where agricultural raw materials meet complex industrial processing and ...
Nikolas Bublik, Lukáš Čechura
wiley   +1 more source

Pharidae H. Adams & A. Adams 1856

open access: yes, 2021
Published as part of Giacomino, Sebastián & Signorelli, Javier H., 2021, Systematic redescription of Solen (Ensisolen) tehuelchus and Ensis macha (Bivalvia: Solenoidea) from Argentina, southwestern Atlantic Ocean, pp.
Giacomino, Sebastián   +1 more
openaire   +2 more sources

Differentiating the Clinical and Variant Spectrum of Hardikar Syndrome From Other MED12‐Related Developmental Disorders

open access: yesAmerican Journal of Medical Genetics Part A, EarlyView.
ABSTRACT The rare X‐linked female‐restricted Hardikar syndrome (HDKR, OMIM # 301068) is characterized by multiple congenital anomalies including orofacial clefts, gastrointestinal, genitourinary, and cardiac anomalies, but cognitive and neurobehavioral development is rarely impaired.
Tinne Warmoeskerken   +4 more
wiley   +1 more source

Phenotype Expansion of Malan Syndrome: New Cases and a Review of the Literature

open access: yesAmerican Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Malan syndrome is an ultra‐rare overgrowth syndrome caused by pathogenic variants or deletions in nuclear factor one X (NFIX) located at 19p13.2. Here, we report a comprehensive literature review and phenotyping of known patients with Malan syndrome and present a novel cohort of eight patients.
Alex F. Nisbet   +10 more
wiley   +1 more source

Adams County Grave-Stonecutters, 1770-1918

open access: yes, 2001
Stonecutting in Adams county followed all the general developmental trends and stages exhibited by the craft in other parts of Pennsylvania. Adams county, nonetheless, evolved its unique approach to gravestone art, for rural early American stonecutters ...
DeLong, Nancy
core  

Logarithmic structures on topological K-theory spectra

open access: yes, 2013
We study a modified version of Rognes' logarithmic structures on structured ring spectra. In our setup, we obtain canonical logarithmic structures on connective K-theory spectra which approximate the respective periodic spectra.
Sagave, Steffen
core   +1 more source

Diagnostic Odyssey of Atypical Long‐Chain 3‐Hydroxyacyl‐CoA Dehydrogenase Deficiency (LCHADD) Explained by Three Allelic Products From Two Pathogenic Variants

open access: yesAmerican Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Long‐chain 3‐hydroxyacyl‐CoA dehydrogenase deficiency (LCHADD) is an autosomal recessive mitochondrial defect of long‐chain fatty acid β‐oxidation, caused by biallelic pathogenic variants in HADHA or HADHB. We report a 22‐year‐old male with an atypically mild presentation of LCHADD who was referred to the Undiagnosed Diseases Network (UDN ...
Yutaka Furuta   +9 more
wiley   +1 more source

Presidential Rhetoric: How John Adams and George W. Bush Used Religion to Effectively Communicate with Their Respective Constituency [PDF]

open access: yes, 2006
President George W. Bush’s affiliation with the conservative and political Christian right helped him win the presidential elections of 2000 and 2004. During the past six years, Bush has courted this vast voting public by referencing Christian doctrine ...
Fisher, Beth
core   +1 more source

Response of an Infant With Presumed Multiple Acyl‐CoA Dehydrogenase Deficiency (MADD) to Ketone Supplementation

open access: yesAmerican Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Multiple Acyl‐CoA Dehydrogenase Deficiency (MADD) is an autosomal recessive inborn error of metabolism caused by biallelic pathogenic variants in one of three known genes: ETFA, ETFB, and ETFDH. It can cause multisystem dysfunction, including cardiomyopathy in severe cases.
Yutaka Furuta   +17 more
wiley   +1 more source

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