Results 21 to 30 of about 3,081 (242)

Adult-onset Still's disease

Autoimmunity Reviews, 2014
First described in 1971, adult-onset Still's disease (AOSD) is a rare multisystemic disorder considered as a complex (multigenic) autoinflammatory syndrome. A genetic background would confer susceptibility to the development of autoinflammatory reactions to environmental triggers.
Gerfaud-Valentin, Mathieu, Jamilloux, Yvan, Iwaz, Jean, Sève, Pascal   +3 more
openaire   +5 more sources

Adult Onset Still's Disease and Rocky Mountain Spotted Fever

Case Reports in Medicine, 2010
Adult Still's Disease was first described in 1971 by Bywaters in fourteen adult female patients who presented with symptoms indistinguishable from that of classic childhood Still's Disease (Bywaters, 1971).
Paul Persad, Rajendrakumar Patel, Niki Patel   +2 more
doaj   +1 more source

ADULT-ONSET STILL’S DISEASE: ASPECTS OF THE HEMATOLOGY CLINIC

Сибирский научный медицинский журнал, 2019
The analysis of literature data on modern approaches in the diagnosis and treatment of adult-onset Still’s disease has been performed. A clinical case of Still’s disease associated with lymphadenopathy syndrome was demonstrated.
M. M. Agakishiev, I. I. Mulina, A. M. Popova, I. N. Nechunaeva, L. M. Maslova, I. B. Kovynev, T. I. Pospelova   +6 more
doaj   +1 more source

Association Between Peripheral Eosinophilia and Clinical Characteristics of Adult-onset Still’s Disease with Persistent Eruption: A Retrospective Study

Acta Dermato-Venereologica, 2021
Persistent eruption occurs in a subset of patients with adult-onset Still’s disease. In our experience, a considerable proportion of these patients present with peripheral eosinophilia.
Jia-Wei Liu, Tian Chen, Wei Liu, Ru-Xuan Chen, Yue-Tong Qian, Yan Tan, Dong-Lai Ma   +6 more
doaj   +1 more source

Pneumonitis in Adult Onset Still’s Disease: Uncommon or Under Diagnosed?

Acta Médica Portuguesa, 2017
The adult onset Still’s Disease is an uncommon entity characterized by multiple clinical manifestations. Pneumonitis, less often considered, deserves particular emphasis given the need for differential diagnosis and because it can progress to severe ...
Silvia Fernandes, Margarida Almeida, José Alberto Pereira da Silva, José Carlos Romeu   +3 more
doaj   +1 more source

Adult-Onset Still’s Disease Presenting as Macrophage-Activation Syndrome With Critical Illness in the Third Trimester of Pregnancy: A Case Report

Critical Care Explorations, 2021
BACKGROUND:. We report a case of a young woman with adult-onset Still’s disease presenting as macrophage-activation syndrome complicated by shock and respiratory failure during the third trimester of pregnancy. CASE SUMMARY:. A previously healthy 26-year-
Andrew T. Peters, MD, Michelle H. Prickett, MD   +1 more
doaj   +1 more source

Association between adult-onset still’s disease and COVID-19: A report of two cases and brief review

SAGE Open Medical Case Reports
Adult-onset still’s disease is a rare multisystemic autoinflammatory disorder with an estimated annual incidence of 0.16–0.62 per 100,000 individuals worldwide. It is typically considered a diagnosis of exclusion.
Sarah Fet-He, Gabriel Ibarra Lecompte, Alejandro José Quiroz Alfaro   +2 more
doaj   +1 more source

European Standard Clinical Practice Guideline and EXPeRT Recommendations for the Diagnosis and Management of Gastroenteropancreatic Neuroendocrine Neoplasms in Children and Adolescents

Pediatric Blood &Cancer, EarlyView.
ABSTRACT Pediatric gastroenteropancreatic neuroendocrine neoplasms (GEP‐NENs) are extremely rare and clinically heterogeneous. Management has largely been extrapolated from adult practice. This European Standard Clinical Practice Guideline (ESCP), developed by the EXPeRT network in collaboration with adult NEN experts, provides (adult) evidence ...
Michaela Kuhlen, Calogero Virgone, Antje Redlich, Michael Abele, Ricardo Lopez‐Almaraz, Tal Ben‐Ami, Ewa Bien, Gianni Bisogno, Maja Mazic Cesen, Andrea Ferrari, Malgorzata A. Krawczyk, Yves Reguerre, Dominik T. Schneider, Ines B. Brecht, Charlotte Rigaud, Bilgehan Yalcin, Rainer Claus, Christian Vokuhl, Constantin Lapa, Jörg Fuchs, Segolene Hescot, Thomas Walter, Julien Hadoux, Daniel Orbach   +23 more
wiley   +1 more source

Health‐Related Social Needs in Children With Sickle Cell Disease Are Associated With Worse Health‐Related Quality of Life

Pediatric Blood &Cancer, EarlyView.
ABSTRACT Background Children with sickle cell disease (SCD) face multiple acute and chronic medical complications that may impact their quality of life as reported by patients themselves. Health‐related social needs (HRSNs), such as food and housing insecurity, are common in people with SCD, but the association between HRSNs and patient‐reported ...
Sarah J. Marks, Molly Sonenklar, Cerelia Donald, Cecelia Valrie, Wally Smith, India Sisler   +5 more
wiley   +1 more source

Are Fertility Preservation Procedures Before Gonadotoxic Therapy and Hematopoietic Stem Cell Transplantation Feasible and Safe in Very Young Children? A Retrospective Cohort Study

Pediatric Blood &Cancer, EarlyView.
ABSTRACT Background Fertility preservation (FP) is increasingly integrated into the care of pediatric patients exposed to gonadotoxic therapy or conditioning for hematopoietic stem cell transplantation (HSCT), yet perioperative data in infants and toddlers remain scarce.
Kerstin Saalabian, Yannick Braun, Till‐Martin Theilen, Anke Barnbrock, Theresa Rohm, Fabienne Hammant, Nicole Sänger, Aynura Abbasova‐Semiz, Jan‐Henning Klusmann, Thomas Klingebiel, Udo Rolle, Peter Bader, Henning C. Fiegel, Andrea Jarisch   +13 more
wiley   +1 more source