Rituximab therapy in pulmonary alveolar proteinosis improves alveolar macrophage lipid homeostasis [PDF]
Rationale Pulmonary Alveolar Proteinosis (PAP) patients exhibit an acquired deficiency of biologically active granulocyte-macrophage colony stimulating factor (GM-CSF) attributable to GM-CSF specific autoantibodies. PAP alveolar macrophages are foamy,
Barna, Barbara P +7 more
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Von Hippel-Lindau protein is required for optimal alveolar macrophage terminal differentiation, self-renewal, and function [PDF]
The rapid transit from hypoxia to normoxia in the lung that follows the first breath in newborn mice coincides with alveolar macrophage (AM) differentiation.
Brandi, Paola +12 more
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Macrophages and lipid metabolism [PDF]
Distinct macrophage populations throughout the body display highly heterogeneous transcriptional and epigenetic programs. Recent research has highlighted that these profiles enable the different macrophage populations to perform distinct functions as ...
Remmerie, Anneleen, Scott, Charlotte
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OBJETIVO: Apresentar as características clínicas, tratamento cirúrgico e achado histológico de um caso de lipoidoproteinose. DESCRIÇÃO DO CASO: Criança do sexo masculino, cinco anos de idade, branco, que procurou atendimento odontológico na Universidade.
BRESAOLA, Marco Dapieve +6 more
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Idiopathic desquamative interstitial pneumonia in a child: a case report. [PDF]
Desquamative interstitial pneumonia is a rare form of interstitial lung disease in children. Respiratory symptoms appear progressively, are often subtle, and diagnosis is often delayed by a mean of 6 months after onset.
Aubert, J.D. +4 more
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Whole lung lavage combined with Granulocyte-macrophage colony stimulating factor inhalation for an adult case of refractory pulmonary alveolar proteinosis [PDF]
BACKGROUND: Whole-lung lavage (WLL) is classically the first-line treatment for symptomatic pulmonary alveolar proteinosis (PAP). However, some patients require multiple WLLs because of refractory nature of their PAP. In this instance, these patients may
Hong yan Yu +4 more
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Primary pulmonary alveolar proteinosis [PDF]
Introduction. Pulmonary alveolar proteinosis is an uncommon disease characterized by the accumulation of surfactant proteins and phospholipids within the alveolar spaces. Acquired disease can be idiopathic (primary) and secondary.
Aćimović Slobodan +5 more
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Pulmonary alveolar proteinosis - a case report [PDF]
Efst á síðunni er hægt að nálgast greinina í heild sinni með því að smella á hlekkinnPróteinútfellingar í lungnablöðrum (pulmonary alveolar proteinosis, PAP) eru oftast af óþekktum orsökum en meingerð sjúkdómsins er rakin til skertrar átfrumuvirkni í ...
Eyþór Björnsson +7 more
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Innate immune activation by inhaled lipopolysaccharide, independent of oxidative stress, exacerbates silica-induced pulmonary fibrosis in mice [PDF]
Acute exacerbations of pulmonary fibrosis are characterized by rapid decrements in lung function. Environmental factors that may contribute to acute exacerbations remain poorly understood.
AG Heppleston +55 more
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From the definition of Silicosis at the 1930 Johannesburg conference to the blurred boundaries between pneumoconioses, sarcoidosis and pulmonary alveolar proteinosis (PAP) [PDF]
The 1930 International Labour Office Conference on silicosis in Johannesburg identified silicosis by setting a medicolegal framework to its nosology: as with other occupational illnesses, its medical content was fixed under economic pressure.
Catinon, Mickaël +4 more
core +1 more source

