The Role of Partial Nephrectomy without Arterial Embolization in Giant Renal Angiomyolipoma
Angiomyolipoma is a benign neoplasm composed of varying admixtures of blood vessels, smooth muscle cells, and adipose tissue. Because of an increased risk of spontaneous haemorrhage, surgical approach is needed greater than 4–8 cm size.
Enis Rauf Coskuner +2 more
doaj +1 more source
The Risks of Renal Angiomyolipoma: Reviewing the Evidence
Renal angiomyolipoma (RAML), though a rare benign tumor, may impose a significant morbidity or even mortality due to its unique characteristics and the complications subsequent to its treatment.
R. Seyam +5 more
semanticscholar +1 more source
Everolimus Versus Sirolimus for Angiomyolipoma Associated with Tuberous Sclerosis Complex: A Multi-Institutional Retrospective Study in China [PDF]
luo cong +8 more
openalex +1 more source
MicroRNA-21 is Induced by Rapamycin in a Model of Tuberous Sclerosis (TSC) and Lymphangioleiomyomatosis (LAM) [PDF]
Lymphangioleiomyomatosis (LAM), a multisystem disease of women, is manifest by the proliferation of smooth muscle-like cells in the lung resulting in cystic lung destruction. Women with LAM can also develop renal angiomyolipomas.
Henske, Elizabeth Petri +6 more
core +2 more sources
Femoral PEComa Treated With Combined Surgery and Radiotherapy: A Case Report
ABSTRACT Perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal tumor, and primary involvement of the bone is exceptionally uncommon. In this report, a case of malignant PEComa arising from the femur in an elderly patient is described.
Yanluqi He +4 more
wiley +1 more source
BackgroundPatients with tuberous sclerosis complex (TSC) often have multiple TSC-associated hamartomas, particularly in the brain and kidney.MethodsThis was a post hoc analysis of pediatric patients being treated for subependymal giant cell astrocytomas (
J. Bissler +8 more
semanticscholar +1 more source
Epithelioid Angiomyolipoma in a Pediatric Patient: Case Report and Review of Literature
We report a case of a 17-year-old girl with tuberous sclerosis complex who underwent partial nephrectomy for a newly discovered 7.5-cm renal mass subsequently determined to be an epithelioid angiomyolipoma, a rare variant of angiomyolipoma that can be ...
Michael H. Johnson +3 more
doaj +1 more source
Interventional treatment of renal angiomyolipoma:immediate results and clinical and radiological follow-up of 4.5 years [PDF]
Background Renal angiomyolipoma is rare, but many of these patients may have an acute debut with severe bleeding. These patients need urgent treatment with interventional embolization as an attractive option.
Andersen, Poul Erik +4 more
core +2 more sources
Angiomyolipoma of the Thoracic Wall: An Extremely Rare Diagnostic Challenge
Extrarenal angiomyolipoma (AML) is an extremely uncommon lesion, accounting for less than 9% of all angiomyolipomas. We present a previously unreported case of a rarely located gigantic extrarenal angiomyolipoma at the posterolateral chest wall of a 35 ...
Georgios Gemenetzis +4 more
doaj +1 more source
Non-canonical functions of the tuberous sclerosis complex-Rheb signalling axis [PDF]
The protein products of the tuberous sclerosis complex (TSC) genes, TSC1 and TSC2, form a complex, which inhibits the small G-protein, Ras homolog enriched in brain (Rheb).
Henske, Elizabeth Petri +1 more
core +1 more source

