Severe Supravalvular Aortic Stenosis Treated With Double Patch Aortoplasty: A Case Report [PDF]
Severe supravalvular aortic stenosis in a young patient is a rare but critical condition requiring timely diagnosis and intervention. We report a 15‐year‐old girl presenting with exertional dyspnea, chest pain, and palpitations.
Birat Kadel +4 more
doaj +4 more sources
Supravalvular aortic stenosis is frequently associated with other congenital abnormalities such as pulmonary artery branch stenosis, unusual facies, retarded physical development, abnormal dentition, and mental retardation. Stenosis of the origins of the brachiocephalic vessels may be found in a significant percentage of cases.
E A, Kupic, H L, Abrams
semanticscholar +7 more sources
We report an extremely rare case of Williams–Beuren (WB) syndrome in a 10-year-old boy with supravalvular aortic stenosis (SVAS) secondary to a large fibrocalcific eccentric shelf in the ascending aorta with fibrocalcific severe supravalvular pulmonary ...
Debasish Das +5 more
doaj +2 more sources
Supravalvular aortic stenosis mimicking hypertrophic obstructive cardiomyopathy: a case report. [PDF]
Background Hypertrophic cardiomyopathy (HCM) is a relatively common genetic disorder often associated with left ventricular outflow tract (LVOT) obstruction. However, the presence of certain structural abnormalities such as supravalvular aortic stenosis (
Sharma A, Kaplan E, Betz Y, Ayers M.
europepmc +2 more sources
Association between cardiopulmonary bypass duration and early major adverse cardiovascular events after surgical repair of supravalvular aortic stenosis. [PDF]
Background Patients who underwent surgical repair of supravalvular aortic stenosis (SVAS) are at high risk for postoperative major adverse cardiovascular events (MACE).
Zhang S +9 more
europepmc +2 more sources
Anesthetic considerations in supravalvular aortic stenosis: A case series
Supravalvular aortic stenosis (SVAS), characterized by elastin arteriopathy, presents either as a localized narrowing at the sinotubular junction or as a diffuse form with additional involvement of the ascending aorta, aortic arch, and its branches ...
Virendra Kumar +3 more
doaj +2 more sources
This case report describes the clinical presentation, the necropsy findings, and genetic results of a 13‐year‐old Warmblood mare presented with colic and a bilaterally loud, holosystolic murmur.
Veronique Saey +7 more
doaj +2 more sources
Comparison of autologous aortic tissue and pericardial patch for neo-pulmonary artery reconstruction during arterial switch operation: a single-surgeon experience [PDF]
Background This study aimed to compare the early and mid-term outcomes of neo-pulmonary artery (PA) reconstruction using autologous aortic tissue versus pericardial patch in patients undergoing arterial switch operation (ASO), with a specific focus on ...
Serkan Secici
doaj +2 more sources
Resistant Secondary Hypertension and Severe Pulmonary Hypertension in a Young Adult due to a Rare Cause. [PDF]
ABSTRACT Shone's complex (SC), a rare congenital cardiovascular malformation featuring multilevel left‐sided obstructive lesions, presents particular diagnostic challenges in adult populations. The complex interplay between congenital anatomical defects and acquired cardiovascular adaptations in adult SC patients requires multidisciplinary management ...
Su T +5 more
europepmc +2 more sources
Clinical course and outcomes of supravalvular aortic stenosis in adults [PDF]
Background Supravalvular aortic stenosis (SVAS) is a rare condition with limited data on patients beyond childhood. This study aims to investigate the clinical course and outcomes of SVAS in adults.Methods All adult (≥18 years) patients with SVAS ...
Jolien W Roos-Hesselink +10 more
doaj +2 more sources

