Results 201 to 210 of about 60,528 (234)

Familial Supravalvular Aortic Stenosis

Archives of Pediatrics & Adolescent Medicine, 1964
The modern techniques of the cardiology laboratory have resulted in marked improvement in diagnostic ability with concomitant refinement in diagnostic criteria. 1-3 In aortic stenosis, these advances now permit precise differentiation into valvular, subvalvular, and supravalvular lesions. 4,5 Congenital supravalvular aortic stenosis, apparently first
R, EISENBERG, D, YOUNG, B, JACOBSON, A, BOITO   +3 more
openaire   +2 more sources

A Rare Cause of Supravalvular Aortic Stenosis: Aberrant Fibrous Band Formation Connecting the Left Coronary Cusp to the Sinus Wall

Echocardiography
Transesophageal echocardiography (TEE) revealed that supravalvular aortic stenosis was caused by an aberrant fibrous band bridging the left coronary cusp and the sinus wall.
Chen Chen, Xiaojing Ma, Yafeng He, Juan Xia, Dandan Chen   +4 more
semanticscholar   +1 more source

Supravalvular aortic stenosis repair in a 3-year-old child with Williams syndrome using an interdigitating slide aortoplasty.

Multimedia Manual of Cardio-Thoracic Surgery
Several techniques for the surgical correction of congenital supravalvular aortic stenosis have been devised. We describe the step-by-step surgical approach of a slide aortoplasty to correct localized supravalvular aortic stenosis in a 3-year-old child ...
M. Notenboom, Lennie van Osch-Gevers, P. C. van de Woestijne, Y. Taverne   +3 more
semanticscholar   +1 more source

De Novo Elastin Assembly Alleviates Development of Supravalvular Aortic Stenosis—Brief Report

Arteriosclerosis, Thrombosis and Vascular Biology
BACKGROUND: A series of incurable cardiovascular disorders arise due to improper formation of elastin during development. Supravalvular aortic stenosis (SVAS), resulting from a haploinsufficiency of ELN, is caused by improper stress sensing by medial ...
Matthew W. Ellis, Muhammad Riaz, Yan Huang, Christopher W. Anderson, Marie Hoareau, Xin Li, Hangqi Luo, Seoyeon Lee, Jinkyu Park, Jiesi Luo, L. Batty, Qunhua Huang, Colleen A. Lopez, Dieter P Reinhardt, G. Tellides, Y. Qyang   +15 more
semanticscholar   +1 more source

Aortic Root Enlargement and Aortic Valve Replacement for Calcified Supravalvular and Valvular Aortic Stenosis in Homozygous Familial Hypercholesterolemia: A Case Report

World journal for pediatric & congenital heart surgery, 2020
Familial homozygous hypercholesterolemia is a rare disease with diverse clinical presentations ranging from premature ischemic heart disease to aortic root stenosis but rarely presents with anginal symptoms due to supravalvular and valvular aortic ...
U. Chowdhury, A. Chauhan, S. Hasija, J. Jena, L. Sankhyan, Ravi Phulware   +5 more
semanticscholar   +1 more source

Abstract 15361: Comparison of Cardiovascular Outcomes of Supravalvar Aortic Stenosis Patients With Williams Syndrome and Non-williams Supravalvular Aortic Stenosis

Circulation, 2020
Introduction: Cardiovascular outcomes in Williams syndrome (WS) with supravalvar aortic stenosis (SVAS) compared to those with non-Williams SVAS (NW-SVAS) have not been well-described in literature.
D. Shahbah, Justin D Weigand, Benjamin Jacob, Icadal Essandro, Taylor Beecroft, Sara Stephen, Ashley Keyes, Gabrielle N Spurzem, M. Webb, S. Morris   +9 more
semanticscholar   +1 more source

Surgical Repair of Severe Supravalvular Aortic Stenosis with Bicuspid Aortic Valve and Single Coronary Artery in a 5-Year-Old Child

Scholars Journal of Medical Case Reports
Background: Supravalvular aortic stenosis (SVAS) is a rare form of left ventricular outflow tract obstruction in children. Its coexistence with a bicuspid aortic valve (BAV) and a single coronary artery is uncommon and presents significant surgical ...
Dhivan Naidu, Sallehuddin A, Azeman Na
semanticscholar   +1 more source

Supravalvular aortic stenosis

The American Journal of Cardiology, 1983
Supravalvular aortic stenosis has a wide range of clinical and morphologic expression. Since 1961, 25 patients (aged 1 to 49 years) with documented supravalvular aortic stenosis have been evaluated. Seven (28%) had Williams' syndrome, 5 (20%) had a familial form of supravalvular aortic stenosis, and 13 (52%) had a sporadic form.
Greg Flaker, Douglas Teske, James Kilman, Don Hosier, Charles Wooley   +4 more
openaire   +1 more source

[Supravalvular aortic stenosis].

Rozhledy v chirurgii : mesicnik Ceskoslovenske chirurgicke spolecnosti, 1990
The authors describe the case of an inborn supravalvular aortal stenosis in an adult patient who was successfully treated by a plastic operation of the stenotic portion of the ascendent aorta by means of a synthetic patch. At the same time also a plastic operation of an incompetent mitral valve was made.
M, Adamec, P, Firt, J, Pirk, M, Rocek
openaire   +1 more source

Supravalvular Aortic Stenosis in Aortic Dissection

The American Journal of Cardiology, 1998
Supravalvular aortic stenosis is a rare complication of aortic dissection. We report on echocardiographic and magnetic resonance observations in 2 cases of aortic dissection with false lumen thrombosis of the ascending aorta and severe narrowing of the true lumen.
I, Vilacosta, J A, San Román, P, Aragoncillo, J, Ferreirós, R, Méndez, C, Graupner, W, Stoermann, E, Batlle, M, Baquero   +8 more
openaire   +2 more sources