Results 191 to 200 of about 32,760 (223)

Arrhythmogenic Right Ventricular Cardiomyopathy

New England Journal of Medicine, 2017
Abstract Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a heredo-familial heart muscle disease characterized by progressive myocardial atrophy with fibrofatty replacement. It is a rare disease with an estimated prevalence of 1:2000 to 1:5000.
Corrado, Domenico, Link, Mark S., Calkins, Hugh   +2 more
openaire   +7 more sources

Arrhythmogenic right ventricular cardiomyopathy

The Lancet, 2009
Arrhythmogenic right ventricular cardiomyopathy is a rare inherited heart-muscle disease that is a cause of sudden death in young people and athletes. Causative mutations in genes encoding desmosomal proteins have been identified and the disease is nowadays regarded as a genetically determined myocardial dystrophy.
BASSO, CRISTINA, CORRADO, DOMENICO, MARCUS FI, NAVA, ANDREA, THIENE, GAETANO   +4 more
exaly   +7 more sources

Arrhythmogenic Right Ventricular Cardiomyopathy

JACC: Clinical Electrophysiology, 2022
Arrhythmogenic right ventricular cardiomyopathy (ARVC) encompasses a group of conditions characterized by right ventricular fibrofatty infiltration, with a predominant arrhythmic presentation. First described in the late 1970s and early 1980s, it is now frequently recognized to have biventricular involvement.
Andrew D, Krahn, Arthur A M, Wilde, Hugh, Calkins, Andre, La Gerche, Julia, Cadrin-Tourigny, Jason D, Roberts, Hui-Chen, Han   +6 more
openaire   +4 more sources

Pathobiology of Arrhythmogenic Cardiomyopathy

Cardiac Electrophysiology Clinics, 2011
This article discusses recent advances in the pathology and pathogenesis of arrhythmogenic cardiomyopathy (AC) that have led to the current perspective of a genetically determined cardiomyopathy. AC was initially believed to be a developmental defect of the right ventricular (RV) myocardium, thus justifying the original designation of dysplasia.
BASSO, CRISTINA, PILICHOU, KALLIOPI, carturan E, Rizzo S, Bauce B, THIENE, GAETANO   +5 more
openaire   +3 more sources

Arrhythmogenic cardiomyopathy

Annual Review of Medicine, 2010
Arrhythmogenic right ventricular cardiomyopathy (ARVC) has a prevalence of at least 1 in 1000, is a leading cause of sudden cardiac death in people aged ≤35 years, and accounts for up to 10% of deaths from undiagnosed cardiac disease in the <65 age group.
Sen-Chowdhry, Srijita, Morgan, Robert, Chambers, John C, McKenna, William J   +3 more
openaire   +1 more source

[Early-onset arrhythmogenic cardiomyopathy].

Giornale italiano di cardiologia (2006), 2023
Caso di cardiomiopatia aritmogena destra con esordio in eta ...
De Raffele, Martina, Passarini, Giulia
openaire   +2 more sources

Arrhythmogenic Right Ventricular Cardiomyopathy

Heart Failure Clinics, 2010
Arrhythmogenic right ventricular cardiomyopathy (ARVC) originally emerged as a pathologic diagnosis based on distinctive autopsy findings in cases of premature sudden death. Subsequently these characteristic pathologic features were associated with ventricular tachycardia of right ventricular origin and syncope.
Patrick T, Ellinor, Calum A, MacRae, Ludwig, Thierfelder   +2 more
openaire   +5 more sources

Arrhythmogenic Cardiomyopathy

Heart Failure Clinics, 2023
Sohaib Ahmad Basharat, Ingrid Hsiung, Jalaj Garg, Amro Alsaid   +3 more
openaire   +2 more sources

Pathophysiology of arrhythmogenic cardiomyopathy

Nature Reviews Cardiology, 2011
Arrhythmogenic cardiomyopathy (AC) is a clinically and genetically heterogeneous disorder of heart muscle that is associated with ventricular arrhythmias and risk of sudden cardiac death, particularly in the young and athletes. Mutations in five genes that encode major components of the desmosomes, namely junction plakoglobin, desmoplakin, plakophilin ...
BASSO, CRISTINA, BAUCE, BARBARA, CORRADO, DOMENICO, THIENE, GAETANO   +3 more
openaire   +2 more sources