Results 41 to 50 of about 3,775 (165)
Pediatric Discovery, Volume 3, Issue 4, December 2025.The clinical manifestation of DOLV was atypical. TTE has a relatively high diagnostic accuracy for DOLV in pediatric, which is very valuable for its early detection. ABSTRACT Double outlet left ventricle (DOLV) is a rare congenital cardiac anomaly in which both great arteries originate entirely or predominantly from the morphologic left ventricle.
Xu Zhu +6 more
wiley +1 more source
Role of Catheter Ablation in Arrhythmogenic Right Ventricular Dysplasia
Indian Pacing and Electrophysiology Journal, 2005 Arrhythmogenic right ventricular dysplasia/cardiomyopathy is a disorder characterized by frequent ventricular tachycardia originating from the right ventricle and fibro-fatty replacement of right ventricular myocardium. Though the disorder was originally
Guy Fontaine, Johnson Francis
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Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia: Mechanisms and Management
Research Reports in Clinical Cardiology, 2020 Ahmed AlTurki,1 Bader Alotaibi,1 Jacqueline Joza,1 Riccardo Proietti2 1Division of Cardiology, McGill University Health Center, Montreal, QC, Canada; 2Department of Cardiac, Thoracic, Vascular Sciences, and Public Health, University of Padua, Padua ...
AlTurki A +3 more
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Clinical Cardiology, Volume 48, Issue 11, November 2025.Despite high acute success, catheter ablation for electrical storm is associated with substantial recurrence and mortality. This study emphasizes the complex substrate and high‐risk profile of this population, underscoring the need for careful long‐term management.
Cem Çöteli +4 more
wiley +1 more source
Arrhythmogenic right ventricular dysplasia: A case report
CorSalud, 2015 Arrhythmogenic right ventricular dysplasia is a heart muscle disease that predominantly affects the right ventricle, bringing about the replacement of normal myocardium with fatty or fibrofatty tissue and causing sudden death in young individuals ...
Tessa Negrín Valdés +4 more
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New insights into applications of base editor in hereditary disorders
Interdisciplinary Medicine, Volume 3, Issue 6, November 2025.Abstract Hereditary disorders are a group of diseases caused by genetic mutations or chromosomal variations. Although the incidence of each genetic disorder is relatively low, patients affected by the disease generally experience a range of severe symptoms, including blindness, disability, and even premature death. In addition, the available treatments
Maoping Cai +8 more
wiley +1 more source
Atrial Fibroblasts‐Derived Extracellular Vesicles Exacerbate Atrial Arrhythmogenesis
Advanced Science, Volume 12, Issue 37, October 6, 2025.Exosome miR‐224‐5p derived from angiotensin II‐treated atrial fibroblasts creates a substrate for AF by promoting atrial electrical remodeling. Increased exosome miR‐224‐5p enhances AF susceptibility by inhibiting CACNA1c expression and decreasing ICa current of atrial cardiomyocytes.
Yue Yuan +13 more
wiley +1 more source
Indian Journal of Radiology and Imaging, 2006 Arrhythmogenic right ventricular dysplasia (ARVD) is characterized by progressive fibro fatty replacement of the right ventricular myocardium which constitutes a substrate for electrical instability and a focus of ventricular arrhythmias.
K Arda +4 more
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Genome Sequencing Uncovers Additional Findings in Phelan‐McDermid Syndrome
American Journal of Medical Genetics Part B: Neuropsychiatric Genetics, Volume 198, Issue 7, Page 126-134, October 2025.ABSTRACT Phelan‐McDermid syndrome (PMS) is a genetic condition caused by deletions of chromosome 22q13.3 or pathogenic variants in the SHANK3 gene. Neurologic features typically include intellectual disability, autism spectrum disorder, hypotonia, and absent speech, though there is considerable variability even among individuals with the same molecular
Rachel Gore Moses +21 more
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A case of arrhythmogenic right ventricular cardiomyopathy with biventricular involvement
Monaldi Archives for Chest Disease, 2019 We reported a case of a young adult male aged 18 years admitted in our institution for syncope during a basketball match. No previous symptoms were reported.
Filippo Brandimarte +5 more
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