Results 21 to 30 of about 276,553 (236)
Characterizing the Healthcare Utilization and Costs of Hereditary Hemorrhagic Telangiectasia
American Journal of Hematology, EarlyView.ABSTRACT Hereditary hemorrhagic telangiectasia (HHT) is the second‐most common inherited bleeding disorder worldwide, afflicting one in 4000–5000 people, and is the most morbid inherited bleeding disorder of women. HHT causes recurrent severe epistaxis, chronic gastrointestinal bleeding, heavy menstrual bleeding, and arteriovenous malformations in the ...
Hanny Al‐Samkari +5 more
wiley +1 more source
Arteriovenous Malformation of the Oral Cavity
Case Reports in Dentistry, 2014 Vascular anomalies are a heterogeneous group of congenital blood vessel disorders more typically referred to as birthmarks. Subcategorized into vascular tumors and malformations, each anomaly is characterized by specific morphology, pathophysiology ...
S. Manjunath +7 more
semanticscholar +1 more source
American Journal of Hematology, EarlyView.ABSTRACTHereditary hemorrhagic telangiectasia (HHT, Osler‐Weber‐Rendu disease) is the second most common inherited bleeding disorder worldwide, affecting approximately 1 in 5000 people. Development of disease‐modifying and efficacious hemostatic agents to treat HHT has finally begun after decades without such medical therapies.
Hanny Al‐Samkari +22 more
wiley +1 more source
Arteriovenous Malformations of the Brain
Pediatric Neurology Briefs, 1987 Twenty-three children with A-V malformations have been treated by neurosurgeons at the Childrens Hospital of Eastern Ontario, Ottawa, Ontario.
Ruth E. Vaiden, William R. White
openaire +6 more sources
Human Mutation, 2013 Capillary malformation–arteriovenous malformation (CM–AVM) is an autosomal‐dominant disorder, caused by heterozygous RASA1 mutations, and manifesting multifocal CMs and high risk for fast‐flow lesions.
N. Revencu +51 more
semanticscholar +1 more source
American Journal of Medical Genetics Part A, EarlyView.ABSTRACT Some vascular anomalies, such as hamartomas associated with PTEN hamartoma tumor syndrome (PHTS) and fibroadipose vascular anomaly (FAVA, often due to PI3KCA variants), share similar clinical, radiological, and histopathological presentations that challenge clinicians to provide an accurate diagnosis.
Luciana Daniela Garlisi Torales +10 more
wiley +1 more source
International Forum of Allergy &Rhinology, EarlyView.ABSTRACT Background Given the association between spontaneous cerebrospinal fluid (sCSF) leak and idiopathic intracranial hypertension (IIH), and the association of IIH and venous sinus stenosis (VSS), we sought to determine the prevalence of VSS in sCSF leak and the role of venous sinus stenting for sCSF leak.
Jenny B. Xiao +6 more
wiley +1 more source
Vascular Anomalies, 2014 214 Purpose: We demonstrate the successful single session endovascular embolization for the parenchymal AVM of the temporal lobe through a small feeder of MMA by using liquid embolic materials and detachable delivery catheter.
A. K. Greene, Patricia E. Burrows
semanticscholar +1 more source
ESC Heart Failure, EarlyView.Temporary RVAD support following HM3 LVAD is associated with high morbidity and mortality. Temporary RVAD support occurs most frequently in INTERMACS 1 or 2 patients and those who require pre‐operative VA‐ECMO. In addition to higher post‐operative mortality, a significantly higher risk of both dialysis and stroke at 1 year post‐implant was observed in ...
Vinh Q. Chau +12 more
wiley +1 more source
European Journal of Heart Failure, EarlyView.Aims Bone morphogenetic protein 10 (BMP10), activin receptor‐like kinase 1 (ALK1) and endoglin form a single transforming growth factor‐β family signalling complex that is the principal driver of cardiac and vascular morphogenesis and maturation during hypoxic embryonic development. These proteins are down‐regulated with the onset of normoxia at birth,
Milton Packer +14 more
wiley +1 more source