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The Outcome of a Centralization Program in Biliary Atresia
Annals of SurgeryObjective: Biliary atresia is a rare disease and reported outcomes of surgical management, typically a Kasai portoenterostomy (KPE), vary considerably across the world. Centralization has been proposed to improve this.
Mark Davenport +5 more
semanticscholar +1 more source
Clinics and Research in Hepatology and Gastroenterology, 2012
Biliary atresia is an obliterative cholangiopathy with progressive hepatobiliary disease, starting from the perinatal period. With a frequency of 1/15-18,000 live births, biliary atresia is the commonest cause of life-threatening liver disease in infants, and fatal if untreated.
Ulrich, Baumann, Benno, Ure
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Biliary atresia is an obliterative cholangiopathy with progressive hepatobiliary disease, starting from the perinatal period. With a frequency of 1/15-18,000 live births, biliary atresia is the commonest cause of life-threatening liver disease in infants, and fatal if untreated.
Ulrich, Baumann, Benno, Ure
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Biliary atresia and biliary cysts
Baillière's Clinical Gastroenterology, 1997The authors present a review of the classification, aetiology, presentation, treatment and long-term outcome of children and adults with biliary atresia and choledochal cyst disease. Biliary atresia should be suspected in any infant with jaundice beyond the second week of life.
P A, Lipsett, D L, Segev, P M, Colombani
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Etiopathogenesis of Biliary Atresia
Seminars in Liver Disease, 2001Biliary atresia, a progressive sclerosis of the extrahepatic biliary tree that occurs only within the first 3 months of life, is one of the most common causes of neonatal cholestasis and accounts for over half of children who undergo liver transplantation.
R J, Sokol, C, Mack
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Current Opinion in Gastroenterology, 2019
Biliary atresia is a poorly understood deadly disease. Genetic predisposition factors are suspected albeit not firmly established. This review summarizes recent evidence of genetic alterations in biliary atresia.Whole-genome association studies in biliary atresia patients identified four distinct predisposition loci with four different genes ...
Muriel, Girard, Ganna, Panasyuk
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Biliary atresia is a poorly understood deadly disease. Genetic predisposition factors are suspected albeit not firmly established. This review summarizes recent evidence of genetic alterations in biliary atresia.Whole-genome association studies in biliary atresia patients identified four distinct predisposition loci with four different genes ...
Muriel, Girard, Ganna, Panasyuk
openaire +2 more sources
Pediatrics, 1975
It is difficult for me to find fault with Dr. Lilly's presentation, especially since he refers to me as a fair-minded, clear-thinking man! Dr. Thaler and I concluded in 1968 that the chance of encountering a patient with operable atresia of the extrahepatic biliary ducts was so small that our primary obligation was to protect the infant ...
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It is difficult for me to find fault with Dr. Lilly's presentation, especially since he refers to me as a fair-minded, clear-thinking man! Dr. Thaler and I concluded in 1968 that the chance of encountering a patient with operable atresia of the extrahepatic biliary ducts was so small that our primary obligation was to protect the infant ...
openaire +2 more sources
Biliary atresia in the newborn
Journal of Pediatric Surgery, 1986A prenatal sonographic diagnosis of extrahepatic biliary atresia was made and, 76 hours after birth, operatively confirmed. A standard Kasai operation was performed, with the exception of the use of an ancillary appendiceal conduit to provide biliary drainage of an independent bile duct draining the right anterior hepatic segment.
S K, Greenholz +3 more
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Cardiac-associated biliary atresia (CABA): a prognostic subgroup
Archives of Disease in Childhood, 2020Objectives To describe the range of concurrent cardiac malformations in biliary atresia (BA) while providing a functional framework of risk. Methods Demographic and variables were collected from a prospectively maintained single-centre database.
B. Aldeiri +5 more
semanticscholar +1 more source
Serum MMP-7 in the Diagnosis of Biliary Atresia
Pediatrics, 2019BA is a serious disorder with difficulty in accurate noninvasive diagnosis. This study validated the promising diagnostic accuracy of MMP-7 for BA.
Jingying Jiang +7 more
semanticscholar +1 more source