Results 81 to 90 of about 222,722 (307)

Cystic biliary atresia masquerading as a choledochal cyst

Journal of Pediatric Surgery Case Reports, 2021
Cystic biliary atresia is an uncommon form of biliary atresia that is often misdiagnosed as a choledochal cyst. Here we present a case of a neonate who presented with obstructive jaundice and an antenatally-detected abdominal cyst who was found to have ...
Carolyn Reuland, Clint D. Cappiello
doaj  

Long Noncoding RNA H19 Contributes to Cholangiocyte Proliferation and Cholestatic Liver Fibrosis in Biliary Atresia

Hepatology, 2019
Biliary atresia (BA) is a neonatal liver disease featuring cholestasis and severe liver fibrosis (LF). Despite advances in the development of surgical treatment, lacking an early diagnostic marker and intervention of LF invariably leads to death from end‐
Yongtao Xiao, Runping Liu, Xiaojiaoyang Li, E. Gurley, P. Hylemon, Ying Lu, Huiping Zhou, W. Cai   +7 more
semanticscholar   +1 more source

Rectal budesonide: A potential game changer after Kasai hepatoportoenterostomy

Journal of Pediatric Gastroenterology and Nutrition, EarlyView.
Abstract Objectives Intravenous or oral steroid administration in patients with biliary atresia (BA) after Kasai hepatoportoenterostomy (HPE) is commonly practiced, however, the benefits remain controversial. Some studies suggest no positive effects while risking steroid associated side effects.
Stefanie Langreen, Nathalie Pauer, Eva D. Pfister, Norman Junge, Ulrich Baumann, Omid Madadi‐Sanjani, Claus Petersen, Jens Dingemann, Nagoud Schukfeh   +8 more
wiley   +1 more source

Physical development and cognitive performance in a monozygotic twins for biliary atresia: Report of a case and literature reviewing

Journal of Pediatric Surgery Case Reports, 2016
A case of monozygotic twins, one of whom suffered from biliary atresia and the other one was apparently healthy, is described herein. Children with biliary atresia appear to be vulnerable to developmental lags in the physical and cognitive performance ...
Yang Chen, Jianghua Zhan
doaj   +1 more source

Rotavirus Reassortant–Induced Murine Model of Liver Fibrosis Parallels Human Biliary Atresia

Hepatology, 2020
Biliary atresia (BA) is a devastating neonatal cholangiopathy that progresses to fibrosis and end‐stage liver disease by 2 years of age. Portoenterostomy may reestablish biliary drainage, but, despite drainage, virtually all afflicted patients develop ...
S. Mohanty, Inna N. Lobeck, B. Donnelly, Phylicia Dupree, A. Walther, Sarah Mowery, Abigail C. Coots, Alexander J. Bondoc, R. Sheridan, H. Poling, H. Temple, M. McNeal, K. Sestak, Ruchi Bansal, G. Tiao   +14 more
semanticscholar   +1 more source

Paediatric acute liver failure: A prospective, nationwide, population‐based surveillance study in Germany

Journal of Pediatric Gastroenterology and Nutrition, EarlyView.
Abstract Objectives Paediatric acute liver failure (PALF) is a rare but life‐threatening condition, yet comprehensive epidemiological data in Germany are lacking. Our study aimed to systematically analyse incidence, aetiology, and outcome of PALF in Germany.
Dominic Lenz, Muhammad Abdulaziz, Bianca Peters, Matias Wagner, Lea D. Schlieben, Victor M. Corman, Ulrich Baumann, Philip Bufler, Tal Dattner, Rainer Ganschow, Kristin Genzel, Nicole Hammann, Steffen Hartleif, Bianca Hegen, Stephan Henning, André Hoerning, Martin Jankofsky, Norman Junge, Simone Kathemann, Birgit Knoppke, Martina Kohl‐Sobania, Martin Laass, Elke Lainka, Eberhard Lurz, Michael Melter, Hanna Müller, Denisa Pilic, Markus Ries, Lisa Schiefele, Tobias Schwerd, Ekkehard Sturm, Mechtild Wegner, Michael S. Urschitz, Sven F. Garbade, Daniel Wenning, Christian Drosten, Alexander Fichtner, Stefan Kölker, Georg F. Hoffmann, Holger Prokisch, Christian Staufner   +40 more
wiley   +1 more source

Surgical complications in human orthotopic liver transplantation. [PDF]

, 1987
Between March 1, 1980 and December 31, 1984, 393 orthotopic liver transplantations (OLT) were performed in 313 consecutive recipients. Technical complications were responsible for a substantial morbidity (41/393 allograft loss--10.4%) and mortality (26 ...
Gordon, RD, Iwatsuki, S, Lerut, J, Starzl, TE   +3 more
core  

Biliary Atresia: Clinical and Research Challenges for the Twenty‐First Century

Hepatology, 2018
Biliary atresia (BA) is a fibroinflammatory disease of the intrahepatic and extrahepatic biliary tree. Surgical hepatic portoenterostomy (HPE) may restore bile drainage, but progression of the intrahepatic disease results in complications of portal ...
J. Bezerra, R. Wells, C. Mack, S. Karpen, J. Hoofnagle, E. Doo, R. Sokol   +6 more
semanticscholar   +1 more source

Endoscopic remodeling of esophageal stenosis refractory to traditional endoscopic treatment

JPGN Reports, EarlyView.
Abstract Esophageal atresia (EA), with or without tracheoesophageal fistula, is the most common congenital anomaly of the esophagus. Surgical correction is the primary treatment, however, up to 80% of patients experience anastomotic stenosis, with esophageal balloon dilation (EBD) being the first‐line treatment.
María Camila Beltrán‐Ramírez, Jose Fernando Vera‐Chamorro, Ailim Margarita Carias‐Dominguez   +2 more
wiley   +1 more source

Surgery of Biliary Atresia [PDF]

Scandinavian Journal of Surgery, 2011
Biliary atresia (BA) is a progressive fibro-obliterative cholangiopathy of unclear etiology affecting varying degrees of both extra- and intrahepatic biliary tree resulting in obstructive bile flow and cholestasis in neonates. The diagnostic work-up is designed to diagnose or rule out BA without any unnecessary delay.
Mikko P. Pakarinen, Risto Rintala
openaire   +3 more sources