Results 11 to 20 of about 6,300 (176)

Genetic predisposition to porto‐sinusoidal vascular disorder: A functional genomic‐based, multigenerational family study

Hepatology, EarlyView., 2022
A deleterious variant of FCHSD1 results in mTOR pathway overactivation and may cause porto‐sinusoidal vascular disorder (PSVD). The pedigree of the family demonstrated an autosomal dominant disease with variable expressivity. Whole‐genome sequencing and Sanger sequencing both validated the existence of the FCHSD1 variant and the heterozygosity of c ...
Jingxuan Shan, André Megarbane, Aziz Chouchane, Deepak Karthik, Ramzi Temanni, Atilio Reyes Romero, Huiying Hua, Chun Pan, Xixi Chen, Murugan Subramanian, Chadi Saad, Hamdi Mbarek, Cybel Mehawej, Eliane Chouery, Sirin W. Abuaqel, Alexander Dömling, Sami Remadi, Cesar Yaghi, Pu Li, Lotfi Chouchane   +19 more
wiley   +1 more source

Liver transplantation for Budd-Chiari syndrome: A challenging but handable procedure

Asian Journal of Surgery, 2022
Backround: Establishing venous outflow in liver transplantation for patients with Budd-Chiari syndrome is crucial and requires various surgical techniques.
Hikmet Aktas, Ali Ozer, Tonguc Utku Yilmaz, Selim Keceoglu, Meltem Guner Can, Remzi Emiroglu   +5 more
doaj   +1 more source

P- 30 CLINICAL FEATURES, TREATMENT, AND SURVIVAL OF PATIENTS WITH BUDD-CHIARI SYNDROME IN A HEPATOLOGY COLOMBIAN CENTER

Annals of Hepatology, 2023
Introduction and Objectives: Budd-Chiari syndrome is defined as the obstruction of the hepatic venous flow. In Colombia, there is limited evidence regarding the characterization of these patients.
Ximena Morales, Daniel Rojas, Felipe Durán-Torres, Carolina Salinas, Leonardo Pérez, Andrés Murillo, Enrique Ponce, Jorge Ceballos, Martín Garzón, Geovanny Hernández-Cely, Cristina Torres, Adriana Varón, Andrés Murcia, Gilberto Mejía, José Gabriel Caviedes, Juan Manuel Pérez, Oscar Beltrán   +16 more
doaj   +1 more source

A rare case of constrictive pericarditis with Budd–Chiari syndrome due to right atrial thrombosis

SAGE Open Medical Case Reports, 2021
Patients living with HIV (PLWH) with previous pulmonary tuberculosis, presenting with disproportionate ascites to peripheral congestion, should alert the clinician to consider constrictive pericarditis and Budd–Chiari syndrome (BCS).
Somasundram Pillay, Nokwazi Moffat
doaj   +1 more source

Experts consensus on Chinese nomenclature of Budd-Chiari syndrome

Journal of Interventional Medicine, 2021
In China, Budd-Chiari syndrome has been transliterated into six names according to the pronunciation of the letters. To standardize and unify the Chinese names of the disease, multi-disciplinary experts suggest translating Budd-Chiari syndrome into ...
Maoheng Zu, Ke Xu, Bian Ce, Cao Jianmin, Cheng Yongde, Cui Jinguo, Dang Xiaowei, Dong Jiahong, Gao Yong, Gu Jianping, Gu Yuming, Guo Chenghao, Han Xinwei, Li Linsun, Li Yanhao, Li Zhen, Liu Zuoqin, Mu Wei, Ni Caifang, Wang Zhonggao, Wang Maoqiang, Xiang Hua, Xu Hao, Xu kai, Xu Ke, Yan Zhiping, Zhang Lin, Zhang Qingqiao, Zhang Xiaoming, Zu Maoheng   +29 more
doaj   +1 more source

Budd-Chiari syndrome

Clinics and Research in Hepatology and Gastroenterology, 2020
International ...
Coilly, Audrey, Potier, Pascal, Broué, Pierre, Kounis, Ilias, Valla, Dominique, Hillaire, Sophie, Lambert, Vincent, Dutheil, Danielle, Hernández-Gea, Virginia, Plessier, Aurélie, Vilgrain, Valérie, Bureau, Christophe   +11 more
openaire   +3 more sources

BUDD-CHIARI SYNDROME IN PATIENTS WITH ULCERATIVE COLITIS: A SYSTEMATIC LITERATURE REVIEW

Hematology, Transfusion and Cell Therapy, 2021
Objective: Budd-Chiari syndrome (BCS) is characterized by hepatic venous outflow obstruction that can lead to hepatic congestion, portal hypertension, ascites, esophageal varices, and liver failure.
TL Correa, MSTC Guelli
doaj   +1 more source

Budd-Chiari syndrome

Annals of Hepatology, 2005
Manuscript received and accepted: July 18, 2005. A 29 years old man with Budd-Chiari syndrome. Budd-Chiari syndrome is defined as hepatic venous outflow obstruction at any level from the small hepatic veins to the junction of the inferior vena cava and the right atrium, regardless of the cause of obstruction.
Nahum Méndez-Sánchez, Norberto C. Chávez-Tapia, Eric López-Méndez, Misael Uribe   +3 more
openaire   +5 more sources

Budd-Chiari syndrome [PDF]

Journal of British Surgery, 1995
Abstract Budd-Chiari syndrome is the generic term for different forms of hepatic venous outflow obstruction resulting in a clinical picture of portal hypertension and hepatomegaly. Three levels of venous outflow obstruction may be recognized, affecting respectively the small intrahepatic venules, the large hepatic veins and the inferior ...
openaire   +2 more sources

The Budd-Chiari Syndrome in Pregnancy [PDF]

Obstetrical & Gynecological Survey, 1978
Summary A case of Budd-Chiari syndrome in a young woman, which started probably in the last trimester of pregnancy, is described. The diagnosis was made clinically and was confirmed by inferior venacavography and on exploratory laparotomy. The possible connection of the syndrome with the pregnancy is discussed.
M, Tiliacos, D, Tsantoulas, A, Tsoulias, E, Kokka, E, Eudaimon, S, Aphentoglou, C, Metzantonakis   +6 more
openaire   +2 more sources