Results 101 to 110 of about 29,117 (272)
ABSTRACT Pseudoxanthoma elasticum (PXE) is a rare autosomal recessive disorder caused by pathogenic variants in ABCC6, leading to progressive calcification of elastic fibers. Although PXE typically presents in adolescence with dermatologic or ocular manifestations, early vascular involvement, including pediatric hypertension, is increasingly recognized.
Hana Flogelova +8 more
wiley +1 more source
In systemic sclerosis skin perfusion of hands is reduced and may predict the occurrence of new digital ulcers [PDF]
Systemic sclerosis (SSc) patients are at high risk for the development of ischemic digital ulcers (DUs). The aim of this study was to assess in SSc patients a correlation between skin perfusion evaluated by LDPI and DUs and to evaluate the prognostic ...
Barbano, Biagio +6 more
core +1 more source
Objective Juvenile dermatomyositis (JDM) is a rare childhood inflammatory myopathy, whereas spondyloarthritis (SpA) is an inflammatory arthropathy characterized by enthesitis and peripheral or axial involvement. We describe a series of patients diagnosed with JDM in childhood who later fulfilled classification criteria for SpA, a sequential phenotype ...
Austen Grooms +3 more
wiley +1 more source
Comparison of the Utility and Validity of Three Scoring Tools to Measure Skin Involvement in Patients With Juvenile Dermatomyositis [PDF]
OBJECTIVE: To compare the abbreviated Cutaneous Assessment Tool (CAT), Disease Activity Score (DAS), and Myositis Intention to Treat Activity Index (MITAX) and correlate them with the physician's 10-cm skin visual analog scale (VAS) in order to define ...
Almeida, B +9 more
core +1 more source
Pioneers in Dermatology and Venereology: An interview with Professor Eli Sprecher
Journal of the European Academy of Dermatology and Venereology, Volume 40, Issue 5, Page 732-735, May 2026.
Eli Sprecher
wiley +1 more source
Concurrent Psoriasis and Dermatomyositis: Retrospective Analysis and Literature Review
ABSTRACT Background Psoriasis (PsO) and dermatomyositis (DM) are both autoimmune‐mediated, inflammatory conditions. The concurrence of PsO and DM is rare, and literature on their relationship remains limited. Additionally, cutaneous DM can be challenging to clinically diagnosis, often presenting with psoriasiform clinical features.
Emily R. Gordon +5 more
wiley +1 more source
Calcinosis cutis universalis - a rare manifestation of systemic lupus erthymatosus
Calcinosis cutis (or skin and subcutaneous calcification) is a feature of a variety of rheumatic conditions, most commonly dermatomyositis and scleroderma, but is rarely reported in systemic lupus erythematosus (SLE ). When calcinosis cutis does occur in
farhana ebrahim suleman +1 more
doaj +1 more source
A proposed role for sepsis in the pathogenesis of myocardial calcification [PDF]
Myocardial calcification is a rare and life-threatening condition that is a recognised complication of ischaemic heart disease, cardiac surgery, rheumatic fever and myocarditis.
AROMATARIO, MARIAROSARIA +7 more
core +1 more source
INTRODUCTION Objective outcome measures are needed to facilitate clinical trials of much needed treatments for calcinosis in systemic sclerosis (SSc).
M. Hughes +8 more
semanticscholar +1 more source

