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American College of Rheumatology Guidance Statement for Diagnosis and Management of VEXAS Developed by the International VEXAS Working Group Expert Panel
Arthritis &Rheumatology, EarlyView.Objective
Vacuoles E1 enzyme X‐linked autoinflammatory somatic syndrome (VEXAS) is a recently identified rare genetic disorder associated with somatic mutations in the UBA1 gene. VEXAS presents with a combination of inflammatory and hematologic manifestations, leading to increased morbidity and mortality.Arsene Mekinian, Sophie Georgin‐Lavialle, Marcela A. Ferrada, Sinisa Savic, Matthew J. Koster, Olivier Kosmider, Thibault Comont, Mael Heilblig, Juan I. Arostegui, Annmarie Bosco, Rim Bourguiba, Katherine R. Calvo, Catherine Cargo, Chiara Cattaneo, François Chasset, Henrique Coelho, Corrado Campochiaro, Francesca Crisafulli, Stephanie Ducharme‐Benard, Raquel Faria, Franco Franceschini, Micol Frassi, Emma M. Groarke, Carmelo Gurnari, Yervand Hakobyan, Yvan Jamilloux, Ciprian Jurcut, Yohei Kirino, Austin Kulasekararaj, Hiroyoshi Kunimoto, Lauren M. Madigan, Heřman F. Mann, Chiara Marvisi, Marcin Milchert, Sara Morais, Katja Sockel, Francesco Muratore, Hideaki Nakajima, Mrinal M. Patnaik, Luísa Regadas, Marie Robin, Abraham Rutgers, Carlo Salvarani, Anthony M. Sammel, Joerg Seebach, Pierre Sujobert, Alessandro Tomelleri, Geoffrey Urbanski, Frédéric Vandergheynst, Romana Vieira, David S. Viswanatha, Ewa Więsik‐Szewczyk, Elisa Diral, Benjamin Terrier, Bhavisha A. Patel, Pierre Fenaux, Peter C. Grayson, David B. Beck, on behalf of the International VEXAS working group, and with endorsement of EuroBloodNet, the European Reference Network in Rare Hematological Diseases, Heřman Mann, Benjamin Terrier, François Chasset, Sophie Georgin Lavialle, Alessandro Tomelleri, Campochiaro Corrado, Carlo Salvarani, Francesca Crisafulli, Franco Franceschini, Micol Frassi, Yohei Kirino, Ewa Więsik‐Szewczyk, Marcin Milchert, Raquel Faria, Ciprian Jurcut, Joerg Seebach, Sinisa Savic, David Beck, Lauren Madigan, Matthew Koster, Patnaik Mrinal, Olivier Kosmider, Pierre Sujobert, Juan I. Arostegui, Catherine Cargo, David Viswanatha, Yervand Hagopian, Mael Heilblig, Pierre Fenaux, Thibault Comont, Bruno Alessandro, Chiara Cattaneo, Elisa Diral, Sara Morais, Austin Kulasekarara, Emma Groarke, Katherine Calvo, Patel Bhavisha, Anthony Sammel, Arsene Mekinian, Benjamin Terrier, Marie Robin, Sophie Georgin Lavialle, Katja Sockel, Yvan Jamilloux, Carmelo Gurnari, Henrique Coelho, Romana Vieira, Rim Bourguiba, Marcela Ferrada, Peter Grayson +111 morewiley +1 more sourceElectrocardiogram Features in Non-Cardiac Diseases: From Mechanisms to Practical Aspects
Journal of Multidisciplinary HealthcareAlexandr Ceasovschih,1,2,* Victorița Șorodoc,1,2 Serghei Covantsev,3,* Anastasia Balta,1,2,* Jamol Uzokov,4,* Sergio E Kaiser,5 Abdallah Almaghraby,6 Cătălina Lionte,1,2 Cristian Stătescu,1,7 Radu A Sascău,1,7 ...Ceasovschih A, Șorodoc V, Covantsev S, Balta A, Uzokov J, Kaiser SE, Almaghraby A, Lionte C, Stătescu C, Sascău RA, Onofrei V, Haliga RE, Stoica A, Bologa C, Ailoaei Ș, Şener YZ, Kounis NG, Șorodoc L +17 moredoaj 2024 Clinical practice guidelines for Acute coronary syndrome without ST segment elevation electrocardiogram
Российский кардиологический журналRussian Society of Cardiology (RSC)With the participation of: the Association of Cardiovascular Surgeons, the Russian Society of Emergency Medical Care, the Russian Association of Ultrasound Diagnostics Specialists in Medicine (RASUDM)Approved by the ...O. V. Averkov, G. K. Harutyunyan, D. V. Duplyakov, E. V. Konstantinova, N. N. Nikulina, R. M. Shakhnovich, I. S. Yavelov, A. N. Yakovlev, S. A. Abugov, B. G. Alekyan, D. M. Aronov, M. V. Arkhipov, O. L. Barbarash, S. A. Boytsov, M. G. Bubnova, T. V. Vavilova, E. Yu. Vasilyeva, A. S. Galyavich, V. I. Ganyukov, S. R. Gilyarevsky, E. P. Golubev, E. Z. Golukhova, D. A. Zateyshchikov, Yu. A. Karpov, E. D. Kosmacheva, Yu. M. Lopatin, V. A. Markov, E. V. Merkulov, N. A. Novikova, E P. Panchenko, D. V. Pevzner, N. V. Pogosova, D. M. Prasol, A. V. Protopopov, D. V. Skrypnik, R. S. Tarasov, S. N. Tereshchenko, S. A. Ustyugov, A. V. Khripun, E. A. Tsebrovskaya, S. V. Shalaev, E. V. Shlyakhto, A. V. Shpektor, S. S. Yakushin +43 moredoaj +1 more sourceInclisiran: A New Strategy for LDL-C Lowering and Prevention of Atherosclerotic Cardiovascular Disease
Vascular Health and Risk Management, 2023 Michael S Albosta,1 Jelani K Grant,2 Pam Taub,3 Roger S Blumenthal,2 Seth S Martin,2 Erin D Michos2 1Internal Medicine Department, University of Miami Miller School of Medicine/ Jackson Memorial Hospital, Miami, FL, USA; 2Ciccarone Center for the ...Albosta MS, Grant JK, Taub P, Blumenthal RS, Martin SS, Michos ED +5 moredoaj Step by step daily management of short-term mechanical circulatory support for cardiogenic shock in adults in the intensive cardiac care unit: a clinical consensus statement of the Association for Acute CardioVascular Care of the European Society of Cardiology SC, the European Society of Intensive Care Medicine, the European branch of the Extracorporeal Life Support Organization, and the European Association for Cardio-Thoracic Surgery [PDF]
, 2023 Jacob Eifer Møller, Alessandro Sionís, Nadia Aïssaoui, Albert Ariza, Jan Bělohlávek, Daniel De Backer, Gloria Färber, Can Gollmann‐Tepeköylü, Alexandre Mebazaa, Susanna Price, Justyna Swol, Hölger Thiele, Christian Hassager +12 moreopenalex +1 more source2024 Clinical practice guidelines for Acute myocardial infarction with ST segment elevation electrocardiogram
Российский кардиологический журналRussian Society of Cardiology (RSC)With the participation of: the Association of Cardiovascular Surgeons, the Russian Society of Emergency Medical Care, the Russian Association of Ultrasound Diagnostics Specialists in Medicine (RASUDM)Approved by the ...O. V. Averkov, G. K. Harutyunyan, D. V. Duplyakov, E. V. Konstantinova, N. N. Konstantinova, R. M. Shakhnovich, I. S. Yavelov, A. N. Yakovlev, S. A. Abugov, B. G. Alekyan, D. M. Aronov, M. V. Arkhipov, O. L. Barbarash, S. A. Boytsov, M. G. Bubnova, T. N. Vavilova, E. Yu. Vasilyeva, A. S. Galyavich, V. I. Ganyukov, S. R. Gilyarevsky, E. P. Golubev, E. Z. Golukhova, D. A. Zateyshchikov, Yu. A. Karpov, E. D. Kosmacheva, Yu. M. Lopatin, V. A. Markov, E. V. Merkulov, N. A. Novikova, E. P. Panchenko, D. V. Pevzner, N. V. Pogosova, D. M. Prasol, A. V. Protopopov, D. V. Skrypnik, R. S. Tarasov, S. N. Tereshchenko, S. A. Ustyugov, A. V. Khripun, E. A. Tsebrovskaya, S. V Shalaev, E. V. Shlyakhto, A. V Shpektor, S. S. Yakushin +43 moredoaj +1 more sourceFostamatinib and the risk of acute aortic dissection in immune thrombocytopenia
British Journal of Clinical Pharmacology, EarlyView.Immune thrombocytopenia (ITP) is a rare autoimmune disorder characterized by platelet destruction. While most patients respond to first‐ or second‐line therapies, a small subset is multirefractory. Fostamatinib, an oral spleen tyrosine kinase (SYK) inhibitor, is a therapeutic option in these cases.Paul Dalmas, Alexis Theron, Rita Badaoui, Stéphane Zaffran, Rayid Mchinda, Joelle Micallef, Nicolas Schleinitz, Mikael Ebbo +7 morewiley +1 more source