Results 1 to 10 of about 347,198 (324)

Restrictive cardiomyopathy: definition and diagnosis [PDF]

European Heart Journal, 2022
Restrictive cardiomyopathy (RCM) is a heterogeneous group of diseases characterized by restrictive left ventricular pathophysiology, i.e. a rapid rise in ventricular pressure with only small increases in filling volume due to increased myocardial ...
Claudio Rapezzi, Alberto Aimo, Andrea Barison   +2 more
exaly   +3 more sources

Genetic Insights into Primary Restrictive Cardiomyopathy

Journal of Clinical Medicine, 2022
Restrictive cardiomyopathy is a rare cardiac disease causing severe diastolic dysfunction, ventricular stiffness and dilated atria. In consequence, it induces heart failure often with preserved ejection fraction and is associated with a high mortality ...
Andreas Brodehl, Brenda Gerull, Brodehl Andreas   +2 more
exaly   +4 more sources

Restrictive Cardiomyopathy in a Child

Pediatrics and Neonatology, 2008
Restrictive cardiomyopathy in young children is rare and carries a poor prognosis. We report an 18-month-old girl with poor feeding and abdominal distension. Except for hepatomegaly, no other gastrointestinal abnormalities were found. She had normalsized
Shan-Miao Lin, Haw-Kwei Hwang, Ming-Ren Chen   +2 more
doaj   +4 more sources

Restrictive cardiomyopathy: from genetics and clinical overview to animal modeling

Reviews in Cardiovascular Medicine, 2022
Restrictive cardiomyopathy (RCM), a potentially devastating heart muscle disorder, is characterized by diastolic dysfunction due to abnormal muscle relaxation and myocardial stiffness resulting in restrictive filling of the ventricles.
Michelle Chintanaphol, Buyan-Ochir Orgil, Neely R. Alberson, Jeffrey A. Towbin, Enkhsaikhan Purevjav   +4 more
doaj   +2 more sources

Left Bundle Pacing for Left Bundle Branch Block and Intermittent Third-Degree Atrioventricular Block in a MYH7 Mutation-Related Hypertrophic Cardiomyopathy With Restrictive Phenotype in a Child

Frontiers in Pediatrics, 2020
Hypertrophic cardiomyopathy (HCM) is a group of myocardial diseases defined by cardiac hypertrophy which cannot be explained by secondary causes with a non-dilated left ventricle and preserved or increased ejection fraction.
Luyan Zhang, Xueying Cheng, Jinlong Chen, Ming Zhou, Tianwei Qian, Zhongman Zhang, Jie Yin, Han Zhang, Genyin Dai, Yuming Qin, Shiwei Yang   +10 more
doaj   +2 more sources

Prognosis of pediatric restrictive cardiomyopathy: more severe in sarcomeric variants [PDF]

Frontiers in Genetics
Restrictive cardiomyopathy (RCM) is the most severe type of cardiomyopathy in children with a very poor prognosis. RCM is often diagnosed between 6 and 10 years old and is predominantly of genetic origin. We conducted a retrospective study of 53 patients.
Catherine Gardin, Pierre-Emmanuel Michels, Elena Panaioli, Elise Daire, Flavie Ader, Flavie Ader, Flavie Ader, Sophie Malekzadeh-Milani, Damien Bonnet, Diala Khraiche   +9 more
doaj   +2 more sources

Engineered cardiac tissue model of restrictive cardiomyopathy for drug discovery

Cell Reports Medicine, 2023
Summary Restrictive cardiomyopathy (RCM) is defined as increased myocardial stiffness and impaired diastolic relaxation leading to elevated ventricular filling pressures. Human variants in filamin C (FLNC) are linked to a variety of cardiomyopathies, and
Bryan Z. Wang, Trevor R. Nash, Xiaokan Zhang, J. Rao, L. Abriola, Youngbin Kim, Sergey Zakharov, Michael Kim, Lori J. Luo, Margreet Morsink, Bohao Liu, Roberta I. Lock, Sharon Fleischer, M. Tamargo, Michael S Bohnen, C. Welch, Wendy K. Chung, S. Marx, Y. Surovtseva, G. Vunjak‐Novakovic, B. Fine   +20 more
semanticscholar   +1 more source

Multimodality Imaging Clues for Restrictive Cardiomyopathy

Journal of the Indian Academy of Echocardiography & Cardiovascular Imaging, 2022
Restrictive cardiomyopathy is an entity that can be mistaken for several mimicking conditions, including hypertrophic cardiomyopathy. These patients present with heart failure, which is essentially due to left ventricular diastolic dysfunction, with ...
Srilakshmi M Adhyapak, Grace A Thomas, Anuraag Gupta, Jabraan U Shaikh, Tivlin Jose, Harshith Kramadhari, Kiron Varghese   +6 more
doaj   +1 more source

Echocardiography-Based Deep Learning Model to Differentiate Constrictive Pericarditis and Restrictive Cardiomyopathy.

JACC Cardiovascular Imaging, 2023
BACKGROUND Constrictive pericarditis (CP) is an uncommon but reversible cause of diastolic heart failure if appropriately identified and treated. However, its diagnosis remains a challenge for clinicians.
C. Chao, J. Jeong, R. Arsanjani, Kihong Kim, Yi-Lin Tsai, Wen-Chung Yu, J. Farina, A. Mahmoud, C. Ayoub, Martha Grogan, Garvan C. Kane, Imon Banerjee, Jae K. Oh   +12 more
semanticscholar   +1 more source

Pediatric Restrictive Cardiomyopathies [PDF]

Frontiers in Pediatrics, 2022
Restrictive cardiomyopathy (RCM) is the least frequent phenotype among pediatric heart muscle diseases, representing only 2.5–3% of all cardiomyopathies diagnosed during childhood. Pediatric RCM has a poor prognosis, high incidence of pulmonary hypertension (PH), thromboembolic events, and sudden death, is less amenable to medical or surgical treatment
Raffaello Ditaranto, Angelo Giuseppe Caponetti, Valentina Ferrara, Vanda Parisi, Matteo Minnucci, Chiara Chiti, Riccardo Baldassarre, Federico Di Nicola, Simone Bonetti, Tammam Hasan, Luciano Potena, Nazzareno Galiè, Luca Ragni, Elena Biagini   +13 more
openaire   +3 more sources