Results 241 to 250 of about 81,604 (317)

WS1.2 Vardenafil promotes relocalization of F508del-CFTR in human and mouse airways

, 2014
Marie D’hooghe, Sabrina Noël, Caroline Bouzin, Gaëtane Behets-Wydemans, Teresinha Leal   +4 more
openalex   +1 more source

Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR. [PDF]

Front Pharmacol
Pranke I, Capurro V, Chevalier B, Pesce E, Tomati V, Pastorino C, Kelly-Aubert M, Hatton A, Dreano E, Lena M, Bocciardi R, Zara F, Pantano S, Terlizzi V, Lucanto C, Costa S, Claut L, Daccò V, Poli P, Maschio M, Fabrizzi B, Caporelli N, Cipolli M, Volpi S, Chedevergne F, Cosson L, Macey J, Ramel S, Weiss L, Grenet D, Le Clainche-Viala L, Douvry B, Ravoninjatovo B, Audousset C, Tatopoulos A, Richaud-Thiriez B, Baravalle M, Thouvenin G, Labbé G, Mittaine M, Reix P, Durieu I, Mankikian J, Bui S, Nguyen-Khoa T, Khoukh K, Martin C, Da Silva J, De Carli P, Castellani C, Cresta F, Galietta L, Guillemaut A, Girodon E, Remus N, Bulcaen M, Ensinck M, Zajac M, Carlon M, LeBihan J, Burgel PR, Sermet-Gaudelus I, Hinzpeter A, Pedemonte N.   +63 more
europepmc   +1 more source

Systematic review of nasal endoscopy scores in cystic fibrosis patients treated with CFTR modulators [PDF]

R. Gallardo, Bruna Santos Silva, L.S.S. Salgado, José Dirceu Ribeiro, Eulália Sakano   +4 more
openalex   +1 more source

Functional CFTR may be required for Prevotella melaninogenica regulation of epithelial cell defense against Staphylococcus aureus. [PDF]

J Cyst Fibros
Goryachok M, Fairbanks-Mahnke A, Fulte S, Tamkin E, McCarty A, Larson ED, Planet PJ, Clark SE.   +7 more
europepmc   +1 more source

Transforming Care Models in Cystic Fibrosis: A Review. [PDF]

Healthcare (Basel)
Diener BL, Berdella M, DeCelie-Germana J, Stables-Carney T, Kier C.   +4 more
europepmc   +1 more source

Cystic Fibrosis and CFTR Modulators: The Impact on Bone Density, Muscle Mass and Strength in Children and Young Adolescents. [PDF]

Children (Basel)
Iordanidou K, Karakousis ND, Hatziagorou E, Chrysochoou EA, Galogavrou M, Sopiadou A, Papagianni M.   +6 more
europepmc   +1 more source

Role of S1PR1 in Modulating Airway Epithelial Responses to <i>Pseudomonas aeruginosa</i> in Cystic Fibrosis. [PDF]

Pathogens
Cigana C, Caslini C, Migliara A, Alcala'-Franco B, Veschetti L, Lorè NI, Lombardo A, Bragonzi A.   +7 more
europepmc   +1 more source

CFTR corrector C17 rescues defective SERCA1 in bovine pseudomyotonia: a potential therapy for Brody myopathy. [PDF]

Hum Mol Genet
Akyürek EE, Jacinto JGP, Iori S, Bianchini E, Bolcato M, Costa R, Giantin M, Carotti M, Dacasto M, Cenacchi G, Sandonà D, Gentile A, Sacchetto R.   +12 more
europepmc   +1 more source

Case Report: Pitfalls in CF screening - targeted variant analysis can cause misleading results and therapy recommendations. [PDF]

Front Genet
Karnstedt M, Ahting S, Behrendt S, Hove MV, Hentschel J.   +4 more
europepmc   +1 more source

Implications for cystic fibrosis therapy: Potentiator icenticaftor is superior to ivacaftor in improving function and maintaining stability of F508del CFTR. [PDF]

Sci Prog
Cholon DM, Aleksandrov LA, Quinney NL, Boyles SE, Jensen TJ, Aleksandrov AA, Gentzsch M.   +6 more
europepmc   +1 more source