Results 51 to 60 of about 154,985 (267)
Early Clinical, Imaging, and Pathological Characteristics of SRPK3/TTN‐Digenic Myopathy
ABSTRACT Objective SRPK3/TTN‐digenic myopathy was recently established as a skeletal muscle myopathy caused by digenic inheritance. This study characterizes the early clinical presentation of SRPK3/TTN‐digenic myopathy in one previously reported and seven newly identified pediatric patients.
Rotem Orbach +23 more
wiley +1 more source
Union Is Strength In Lossy Image Compression
{"references": ["J.-L. Starck, and P. Querre, \"Multispectral Data Restoration by the\nWavelet-Karhunen-Lo\u00e8ve Transform,\" Preprint submitted to Elsevier\nPreprint, 2000, pp. 1-29.", "D. L. Donoho, and I. M. Johnstone, \"Adapting to unknown smoothness\nvia wavelet shrinkage,\" Journal of the American Statistical Assoc., vol.\n90, no. 432, pp. 1200-
openaire +3 more sources
Wetting effects and strength degradation of swelling shale evaluated from multistage triaxial test
The multistage triaxial compression test was mainly utilized in this research to investigate the degradation in the strength of swelling shale under different wetting conditions.
Hayder Mohammed Salim Al-Maamori +2 more
doaj +1 more source
Peripheral Neutrophil Activation and Extracellular Trap Formation in Amyotrophic Lateral Sclerosis
Markers of neutrophil activation are increased in plasma during ALS, and markers of NET formation associate with ALS survival. ABSTRACT Objectives Peripheral neutrophil levels in amyotrophic lateral sclerosis (ALS) inversely correlate with survival, suggesting a role for neutrophils in disease progression.
Lillia A. Baird +9 more
wiley +1 more source
ABSTRACT Objective Facioscapulohumeral muscular dystrophy (FSHD) is one of the most debilitating and common muscular dystrophies. Despite its severity, no approved therapy exists for FSHD patients. However, several therapeutic candidates are currently under development, and some have recently entered clinical trials, marking the need for reliable ...
Mustafa Bilal Bayazit +11 more
wiley +1 more source
The Strength of Compressed Tablets
Abstract Examination of the fracture of tablets in a strength test has revealed two types of failure. Where the interparticulate bond is strong, fracture occurs across the grains and the strength of tablet is a simple function of the particle size.
E Shotton, D Ganderton
openaire +1 more source
Bi‐ and Mono‐Allelic RFC1 Expansion in a North American Cohort With Idiopathic Axonal Neuropathy
ABSTRACT Objective RFC1 biallelic repeat expansion is increasingly recognized as a cause of chronic idiopathic axonal polyneuropathy (CIAP), but it remains challenging to know who to test. This study aims to determine the prevalence of biallelic and monoallelic RFC1 expansions and their corresponding neuropathy phenotypes in CIAP patients and identify ...
Amro M. Stino +25 more
wiley +1 more source
Discordance Between Patient and Physician Global Assessments in Early Systemic Sclerosis
Objective This study aims to identify factors associated with patient global assessment (PtGA) and physician global assessment (PhGA) and discordance between them in systemic sclerosis (SSc). Methods Data from adults with early SSc (<5 years) from the Collaborative National Quality and Efficacy Registry were included.
Ellen Romich +35 more
wiley +1 more source
Mechanical behavior of sandy facies of Opalinus Clay under different load conditions
The mechanical behavior of sandy facies of Opalinus Clay at the Mont Terri underground rock laboratory (URL) in Switzerland was investigated with drained and undrained triaxial compression and extension, cyclic compression, and creep tests.
Chun-Liang Zhang, Ben Laurich
doaj +1 more source
Immunosuppressive Drug Use in Limited Systemic Sclerosis: An International Survey
Objective Current guidelines recommend immunosuppressive treatment for diffuse cutaneous systemic sclerosis but are less clear on their use in limited cutaneous systemic sclerosis (lcSSc) in the absence of internal organ complications. We conducted an international survey to understand current immunosuppressive drug prescribing patterns in lcSSc ...
Sabrina Hoa +3 more
wiley +1 more source

