Glucose inhibits cardiac muscle maturation through nucleotide biosynthesis. [PDF]
The heart switches its energy substrate from glucose to fatty acids at birth, and maternal hyperglycemia is associated with congenital heart disease. However, little is known about how blood glucose impacts heart formation.
Braas, Daniel +21 more
core +2 more sources
The use of Macitentan in Fontan circulation: a case report
Background The Fontan circulation, a result of a palliative procedure in patients with single systemic ventricles, is defined by chronically elevated pulmonary vascular resistance.
Polyvios Demetriades +4 more
doaj +1 more source
The views of parents concerning the planning of services for rehabilitation of families of children with congenital cardiac disease [PDF]
Background and purpose: Although much previous research has focused on the medical aspects of congenital cardiac disease, there is a growing body of research which suggests that families may need help and support with the wider issues associated with the
Kendall, L +3 more
core +1 more source
Cardiac index in adults with repaired tetralogy of Fallot: Are we missing the forest for the trees?
Background: Many cardiac parameters have been associated with poor outcomes in patients with repaired tetralogy of Fallot (TOF) and significant residual pulmonary regurgitation (PR).
Maria Fadous +7 more
doaj +1 more source
Frequency of the Congenital Transmission of Trypanosoma cruzi: A Systematic Review and Meta-Analysis [PDF]
BACKGROUND: Chagas disease is caused by the parasite Trypanosoma cruzi and is endemic in much of Latin America. With increased globalisation and immigration, it is a risk in any country, partly through congenital transmission. The frequency of congenital
Buekens, Pierre +4 more
core +1 more source
Hypoalbuminaemia predicts outcome in adult patients with congenital heart disease [PDF]
Background In patients with acquired heart failure, hypoalbuminaemia is associated with increased risk of death. The prevalence of hypoproteinaemia and hypoalbuminaemia and their relation to outcome in adult patients with congenital heart disease (ACHD ...
Alonso-Gonzalez, R +11 more
core +1 more source
Objective: The number of patients with congenitally corrected transposition of the great arteries (ccTGA) surviving to old age is increasing. This study therefore sought to characterize 'geriatric' systemic right ventricle (sRV) in terms of clinical ...
Ewa Kowalik +6 more
doaj +1 more source
Background Accurate measurements of left ventricular (LV) volumes and function are important in the management of patients with various cardiac abnormalities.
Heba Kamel +3 more
doaj +1 more source
Image to Fit the Clinical Picture: Point-of-care Ultrasound Assessment of Ebstein’s Anomaly in Peru [PDF]
Ebstein’s anomaly is a congenital heart defect that when left untreated can lead to unique physical exam and ultrasound findings. This case describes a patient who presented with dyspnea and was found to have cyanosis, clubbing, and dilation of right ...
Dreyfuss, Andrea +2 more
core
Application of the Boston Technical Performance Score to intraoperative echocardiography
Background: The Technical Performance Score (TPS) developed by Boston Children’s Hospital showed surgical outcomes correlate with adequacy of technical repair when implemented on pre-discharge echocardiograms.
Hannah R Bellsham-Revell +11 more
doaj +1 more source

