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JACC: Clinical Electrophysiology, 2022
Congenital long QT syndrome (LQTS) encompasses a group of heritable conditions that are associated with cardiac repolarization dysfunction. Since its initial description in 1957, our understanding of LQTS has increased dramatically. TheĀ prevalence of LQTS is estimated to be ā¼1:2,000, with a slight female predominance.
Andrew D, Krahn +6 more
openaire +4 more sources
Congenital long QT syndrome (LQTS) encompasses a group of heritable conditions that are associated with cardiac repolarization dysfunction. Since its initial description in 1957, our understanding of LQTS has increased dramatically. TheĀ prevalence of LQTS is estimated to be ā¼1:2,000, with a slight female predominance.
Andrew D, Krahn +6 more
openaire +4 more sources
Cardiac Electrophysiology Review, 1997
Many important advances have been made in the last several years regarding the molecular genetics and physiology of the congenital long QT syndrome. These findings have significantly changed our perceptions of the clinical manifestations of this disorder, and added new diagnostic and therapeutic strategies.
G Michael, Vincent +2 more
+6 more sources
Many important advances have been made in the last several years regarding the molecular genetics and physiology of the congenital long QT syndrome. These findings have significantly changed our perceptions of the clinical manifestations of this disorder, and added new diagnostic and therapeutic strategies.
G Michael, Vincent +2 more
+6 more sources
AACN Advanced Critical Care, 2010
The congenital long QT syndrome (LQTS) is considered to be one of the hereditary cardiac arrhythmia syndromes, nowadays also known as cardiac channelopathies. The syndrome is characterized by prolongation of the heart rate corrected QT-interval (QTc) on the 12-lead electrocardiogram (ECG).
Hubert F. Baars +1 more
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The congenital long QT syndrome (LQTS) is considered to be one of the hereditary cardiac arrhythmia syndromes, nowadays also known as cardiac channelopathies. The syndrome is characterized by prolongation of the heart rate corrected QT-interval (QTc) on the 12-lead electrocardiogram (ECG).
Hubert F. Baars +1 more
openaire +3 more sources
The congenital long QT syndrome
The Indian Journal of Pediatrics, 2002The long QT syndrome (LQTS) is a disorder of the electrical system of the heart, due to dysfunction of the ion channels and involving the repolarisation process. The inherited form occurs when there is a mutation in one of the genes which encode the making of a channel.
Preeti, Shanbag +4 more
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Advances in congenital long QT syndrome
Current Opinion in Pediatrics, 2006Dramatic advances have been made in understanding of both the genetics and the phenotypic expression of congenital long QT syndrome. This paper reviews recent clinically relevant literature.Long QT syndrome is one of the leading causes of sudden cardiac death.
Kathryn K, Collins, George F, Van Hare
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Circulation, 1995
The last 12 months could be viewed as the annus mirabilis for the molecular delineation of ventricular arrhythmia substrates, analogous to the celebration of the molecular determinants of gating and selectivity of potassium channels in a previous year.1 In 1991, the first genetic locus (LQT1) for the congenital long QT syndromes was identified on ...
Andrew A. Grace, Kenneth R. Chien
openaire +1 more source
The last 12 months could be viewed as the annus mirabilis for the molecular delineation of ventricular arrhythmia substrates, analogous to the celebration of the molecular determinants of gating and selectivity of potassium channels in a previous year.1 In 1991, the first genetic locus (LQT1) for the congenital long QT syndromes was identified on ...
Andrew A. Grace, Kenneth R. Chien
openaire +1 more source
[Congenital long QT syndromes].
Archives des maladies du coeur et des vaisseaux, 1997Molecular genetic studies have transformed our understanding of the congenital long QT syndromes. Previously, the phenotypes of the Jervell and Lange-Nielsen and Romano-Ward syndromes were characterised by prolongation of the QTc interval greater than 0.44 seconds on the ECG and by syncope or sudden death favorised by stress, the two syndromes being ...
H, Le Marec, J J, Schott
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The molecular genetics of the congenital long QT syndromes
Current Opinion in Cardiology, 1996During the past half decade, significant insight into the clinical electrocardiographic, and genetic features of the congenital long QT syndromes has emerged. Based on this foundation, recent linkage analysis studies have demonstrated the genetic heterogeneity of the Romano-Ward long QT syndrome and led to the discovery of two of the four (or more ...
M W, Russell, M, Dick
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