Results 201 to 210 of about 23,188 (240)
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Circulation, 1995
The last 12 months could be viewed as the annus mirabilis for the molecular delineation of ventricular arrhythmia substrates, analogous to the celebration of the molecular determinants of gating and selectivity of potassium channels in a previous year.1 In 1991, the first genetic locus (LQT1) for the congenital long QT syndromes was identified on ...
Andrew A. Grace, Kenneth R. Chien
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The last 12 months could be viewed as the annus mirabilis for the molecular delineation of ventricular arrhythmia substrates, analogous to the celebration of the molecular determinants of gating and selectivity of potassium channels in a previous year.1 In 1991, the first genetic locus (LQT1) for the congenital long QT syndromes was identified on ...
Andrew A. Grace, Kenneth R. Chien
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Advances in congenital long QT syndrome
Current Opinion in Pediatrics, 2006Dramatic advances have been made in understanding of both the genetics and the phenotypic expression of congenital long QT syndrome. This paper reviews recent clinically relevant literature.Long QT syndrome is one of the leading causes of sudden cardiac death.
Kathryn K, Collins, George F, Van Hare
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Epinephrine QT stress testing in congenital long QT syndrome
Journal of Electrocardiology, 2006Epinephrine QT stress testing is an effective diagnostic tool to unmask concealed Long QT Syndrome (LQTS), particularly type 1 LQTS (LQT1). Unique responses have also been observed in patients with LQT2 and LQT3, making this test invaluable in the diagnostic work-up of LQTS. This article reviews the epinephrine QT stress test, explains the pathological
Himeshkumar, Vyas, Michael J, Ackerman
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Fetal Presentation of Congenital Long QT Syndrome
Pediatric Cardiology, 1999Thirty-two-week prenatal ultrasound revealed a fetal heart rate of 100 bpm with decreased variability on the heart rate tracing. Echocardiogram documented normal anatomy and sinus bradycardia. Newborn electrocardiogram revealed sinus rhythm at 100 bpm with a QTc of 0.657.
M T, Donofrio +3 more
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[Congenital long QT syndrome].
Archives de pediatrie : organe officiel de la Societe francaise de pediatrie, 2001Long QT syndrome (LQTS) is a clinically and genetically heterogenous syndrome characterized by a lengthening of the QT interval on the surface ECG and a propensity to severe ventricular arrhythmias such as torsades de pointes and ventricular fibrillation, leading eventually to syncope and sudden death.
J M, Lupoglazoff +4 more
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[Congenital long QT syndrome].
Presse medicale (Paris, France : 1983), 1998SEVERAL FORMS: Congenital long QT syndrome is a clinically (with and without deafness) and genetically (recessive or dominant autosomal inheritance) heterogeneous entity characterized by a long QT interval on the ECG associated with the risk of severe ventricular arrhythmia (torsade de pointes, ventricular fibrillation) and subsequent syncope or sudden
Lupoglazoff, J +5 more
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Anesthesia eJournal
Context: Congenital long QT syndrome (cLQTS) is the most common genetic cardiac ion channelopathy in the US. Patients with cLQTS are at risk for ventricular tachycardia (VT) in the “torsades de pointes” (TdP) pattern from physical and emotional stress, including during the perioperative period.
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Context: Congenital long QT syndrome (cLQTS) is the most common genetic cardiac ion channelopathy in the US. Patients with cLQTS are at risk for ventricular tachycardia (VT) in the “torsades de pointes” (TdP) pattern from physical and emotional stress, including during the perioperative period.
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[Congenital long QT syndromes].
Archives des maladies du coeur et des vaisseaux, 1997Molecular genetic studies have transformed our understanding of the congenital long QT syndromes. Previously, the phenotypes of the Jervell and Lange-Nielsen and Romano-Ward syndromes were characterised by prolongation of the QTc interval greater than 0.44 seconds on the ECG and by syncope or sudden death favorised by stress, the two syndromes being ...
H, Le Marec, J J, Schott
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Arrhythmic risk in congenital long QT syndrome
Journal of Electrocardiology, 2011One of the most important and challenging aspects of caring for patients with congenital long QT syndrome (LQTS) is assessing an individual's risk of sudden cardiac death (SCD) because of torsades de pointes. Current risk assessment integrates clinical and genetic features known to be associated with SCD, but more accurate methods of risk assessment ...
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[Congenital long QT-interval syndrome].
Anales espanoles de pediatria, 1989Authors report one pediatric patient with prolonged QT-interval syndrome. Importance of this syndrome is based on the possibility of syncopal episodes, due to serious arrhythmias, and sudden death. Therapeutics protocols and prophylactic treatment's indications.
M I, Chamorro Romero +6 more
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