Results 1 to 10 of about 313 (112)

A Swiss database and biobank to better understand and manage congenital lung anomalies [PDF]

open access: yesSwiss Medical Weekly, 2019
Congenital lung anomalies are a group of rare malformations, often diagnosed during the prenatal period. Guidelines on how to manage these patients are currently under debate, especially with regard to prophylactic surgery in asymptomatic patients, or ...
Isabelle Vidal   +8 more
doaj   +6 more sources

Congenital anomaly of the lung

open access: yesLung India, 2014
Sandeep Rana   +4 more
doaj   +3 more sources

Agenesis of the Lung: A Rare Congenital Anomaly of the Lung

open access: yesActa Medica Iranica, 2013
Pulmonary agenesis is a very rare condition and many of them are associated with a variety of cardiac and non-cardiac malformations. We report an eight-month old girl with chronic lung infection due to right sided pulmonary agenesis without any ...
Arun De
doaj   +4 more sources

Lobar agenesis of the lung in a newborn: A rare case report

open access: yesIndian Journal of Respiratory Care, 2021
Lobar agenesis (LA) of the lung is a very uncommon congenital anomaly. Typically, the presentation is with respiratory symptoms, but the onset is highly variable.
Pradyumna Pan, Ritika Pan
doaj   +1 more source

Two rare cases of horseshoe lung with scimitar syndrome in Vietnam

open access: yesRespiratory Medicine Case Reports, 2021
Horseshoe lung is a rare, congenital, pulmonary anomaly in which the caudal and basal segments of the left and right lungs are joined together. Most cases of horseshoe lung are associated with scimitar syndrome.
Le Thuong Vu   +5 more
doaj   +1 more source

Congenital isolated unilateral hypoplasia of the left pulmonary artery: A rare incidental anomaly in an elderly female

open access: yesLung India, 2021
Congenital isolated unilateral hypoplasia of the pulmonary artery (CIUPAH) can have late presentation in the adulthood, mostly diagnosed incidentally, as in our case.
Pankaj Jariwala   +2 more
doaj   +1 more source

Associated Anomalies in Congenital Lung Abnormalities: A 20-Year Experience [PDF]

open access: yesNeonatology, 2020
<b><i>Introduction:</i></b> A congenital lung abnormality (CLA) is often found in conjunction with other abnormalities but screening guidelines for newborns with CLA have not yet been reported. We aimed to assess the incidence of associated anomalies in CLA patients born or followed up at our centre and the need for additional ...
Sergei M. Hermelijn   +6 more
openaire   +3 more sources

Left Pulmonary Agenesis with Right Lung Bronchiectasis in an Adult [PDF]

open access: yesJournal of Clinical and Diagnostic Research, 2016
Pulmonary agenesis is a rare congenital anomaly characterized by the absence of pulmonary parenchyma and vasculature. Bilateral pulmonary agenesis is incompatible with extrauterine life.
Prabhat Kumar   +4 more
doaj   +1 more source

Unilateral Pulmonary Hypoplasia in a Child

open access: yesJournal of Nepal Medical Association, 2015
Pulmonary hypoplasia is an uncommon congenital anomaly. A case reported in a six year old male child from Bangladesh who presented with chronic dry cough, episodic fever and occasional haemoptysis causing confusion with tuberculosis. X-ray suggested lung
Gaurab Dewan
doaj   +3 more sources

Unilateral lung agenesis – rare congenital malformation diagnosed in infants [PDF]

open access: yesRomanian Journal of Pediatrics
Pulmonary agenesis is a congenital anomaly defined by the complete absence of lung parenchyma, as well as bronchial and vascular structures. Right lung agenesis is less frequent compared to left lung agenesis, and usually has a worse prognosis being ...
Ala David   +5 more
doaj   +1 more source

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