Results 41 to 50 of about 11,231 (193)

Pericarditis constrictiva calcificada: una presentación inicial infrecuente de la esclerodermia

Cirugía Cardiovascular, 2017
Resumen: Aunque la afectación pericárdica ha sido demostrada de forma habitual en autopsias de pacientes afectos de esclerodermia, esta afectación pericárdica rara vez es sintomática.
Daniel Hernández-Vaquero, Rubén Álvarez-Cabo, Rocío Díaz, Carlos Morales, Francisco Callejo, Jacobo Silva   +5 more
doaj   +1 more source

Tuberculous constrictive pericarditis [PDF]

BMJ Case Reports, 2019
A previously healthy 53-year-old Brazilian man presented with a 3-month history of anasarca, dyspnoea on minimal exertion, orthopnoea, paroxysmal nocturnal dyspnoea, low-grade fever and an unintentional 12 kg weight loss. No prior medical condition was related.
Neiberg de Alcantara Lima, Danielli Oliveira da Costa Lino, Naiana Medeiros Coelho, Thomas Melgar   +3 more
openaire   +2 more sources

Development of a Disease Activity Index for the Assessment of VEXAS Syndrome (VEXAS‐DAI)

Arthritis Care &Research, EarlyView.
Objective Vacuoles, E1 enzyme, X‐linked, autoinflammatory, somatic syndrome (VEXAS) syndrome is characterized by a complex spectrum of inflammatory and hematologic manifestations. Clinical research to identify effective therapies is urgently needed but is hindered by the lack of validated outcome measures.
Kevin Byram, Heřman Mann, Danielle Hammond, Onima Chowdhury, Sinisa Savic, Yohei Kirino, Carmelo Gurnari, Maël Heiblig, Thibault Comont, Arsène Mekinian, Mrinal M. Patnaik, Lachelle D. Weeks, Gary Ho, Adam Al‐Hakim, Scott Goldberg, Marcela A. Ferrada, Sophie Georgin‐Lavialle, Peter C. Grayson, Emma M. Groarke, Bhavisha Patel, Megan Sullivan, Sarah A. Buckley, Bryan G. Harder, Raman Garcha, David B. Beck, Matthew J. Koster   +25 more
wiley   +1 more source

Ventricular coupling in constrictive pericarditis.

, 1986
Because of the close anatomic association, the volume or pressure in one ventricle can directly influence the volume and pressure in the other ventricle.
M K Dowd, S J Van Buren, R Bartlett, M A Kutcher, W P Santamore   +4 more
core   +1 more source

Delayed Diagnosis of Constrictive Pericarditis Resulting in Recurrent Heart Failure: A Case Report

Clinical Medicine Insights: Case Reports
Constrictive pericarditis can lead to compromised diastolic ventricular filling due to pericardial inflammation and fibrosis. A diagnosis of constrictive pericarditis was established by identifying structural and hemodynamic features through ...
Chunliang Wang, Yuzhu Fan, Guiting Liang, Yu Chen, Tian Tu, Juan Du   +5 more
doaj   +1 more source

Severe ADEM‐Like Neuroinflammatory Disease and Cerebrovascular Fragility With Recurrent Pseudoaneurysms and Moyamoya in a Familial Germline CBL Mutation: Expanding the Clinical Phenotype

American Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Heterozygous germline variants in CBL disrupt its function as a negative regulator of the Ras/MAPK pathway, classically predisposing to Juvenile myelomonocytic leukemia (JMML) and moyamoya. We describe two affected siblings carrying a paternally inherited CBL variant (c.1210 T> C, p.
Michal Bar‐Hakim, Anat Abramovich, Sara Via‐Dorembus, Gali Heimer, Bruria Ben‐Zeev, Etai Adam, Assaf A. Barg, Jonathan Roth, Basheer Sheick‐Yousif, Rony Beeri Berkowiz, Michal Feldon, Haim Bassan, Moran Hausman‐Kedem   +12 more
wiley   +1 more source

Exome Sequencing Uncovers Phenotypic and Genotypic Heterogeneity in 196 Indian Families Evaluated for Autoinflammatory Disorders

American Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Autoinflammatory disorders (AIDs) are a clinically heterogeneous group of inborn errors of immunity primarily caused by dysregulation in the innate immune system. Clinical diagnosis is often challenging due to clinical heterogeneity and the overlapping phenotypes with other inborn errors of immunity and monogenic conditions that mimic AIDs ...
Vaishnavi Ashok Badiger, Periyasamy Radhakrishnan, Suma Balan, Anand P. Rao, Prajna Udupa, Karthik Vijay Nair, Bhagesh Hunakunti, Adarsh Pooradan Prasannakumar, Sanket Limaye, Huzail Gani Shaikh, Rohit Naik, Mahesh Janarthanan, Sudharshan Sridharan, Vishal Sondhi, Sheela Nampoothiri, Hitesh Shah, Sabrinath Mahadevan, Mahabaleshwar Mamadapur, Devang Pandya, Katta Mohan Girisha, Abhay Shivpuri, Amita Moirangthem, Jyothi Raghuram, Gandham Sri Lakshmi Bhavani, Sachin Jeevanagi, Girish Subramaniam, Amita Aggarwal, Anju Shukla, Dhanya Lakshmi Narayanan   +28 more
wiley   +1 more source

Chronic constrictive pericarditis: an “Egg-Shell” calcification [PDF]

, 2019
Chronic constrictive pericarditis is a condition marked by scarred and inelastic pericardium with excessive fibrous tissue and calcium. Here, we report a case of Egg-Shell like calcification in a 30-year-old young adult diagnosed with chronic ...
Patel, Ramesh, Gohel, Rohit
core   +1 more source

A failing right heart in an eggshell: A case report of idiopathic constrictive pericarditis

Clinical Case Reports
key Clinical Message Constrictive Pericarditis is a rare fibrotic conversion of the pericardium that results in non‐specific clinical symptoms such as hepatomegaly, ascites, pleural effusions, and lower extremity edema.
Nivedha Balaji, Sheriff N. Dodoo, Alex Adams, Priyadarshini Dixit, Giancarlo Acosta, Jaime Burkle   +5 more
doaj   +1 more source

Pericardial mesothelioma presenting as chronic constrictive pericarditis. A series of three cases from a single institution

Indian Journal of Pathology and Microbiology, 2018
Pericardial mesotheliomas are rare tumors which often present with features of constrictive pericarditis. We present clinical, imaging, histological, and immunohistochemical findings of three cases presenting with chronic constrictive pericarditis.
Monalisa Hui, K R Harshavardhana, Shantveer G Uppin   +2 more
doaj   +1 more source