Results 131 to 140 of about 7,669 (173)

Three cases of Creutzfeldt–Jakob disease presenting with a predominant dysexecutive syndrome

Journal of Neurology, 2022
Creutzfeldt-Jakob disease (CJD) is a rare, uniformly fatal prion disease. Although CJD commonly presents with rapidly progressive dementia, ataxia, and myoclonus, substantial clinicopathological heterogeneity is observed in clinical practice. Unusual and predominantly cognitive clinical manifestations of CJD mimicking common dementia syndromes are ...
Nick Corriveau-Lecavalier, Wentao Li, Vijay K. Ramanan, Daniel A. Drubach, Gregory S. Day, David T. Jones   +5 more
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Sjögren syndrome presenting with encephalopathy mimicking Creutzfeldt–Jakob disease

Journal of the Neurological Sciences, 2013
A 61-year-old man developed subacute progressive dementia, general fatigue, a tonic-clonic seizure, and a decreased level of consciousness. He had a past history of chronic hepatitis type C and was diagnosed as having hepatic encephalopathy due to hyperammonemia.
Koushun, Matsuo, Makoto, Saburi, Hiroki, Ishikawa, Kou, Tei, Youhei, Hosokawa, Chihiro, Fujii, Toshiki, Mizuno, Masanori, Nakagawa   +7 more
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Presentation of Creutzfeldt–Jakob disease as acute corticobasal degeneration syndrome

Movement Disorders, 2004
AbstractWe provide a brief report with videotape documentation of a possible case of Creutzfeldt–Jakob disease.
Galit, Kleiner-Fisman, Catherine, Bergeron, Anthony E, Lang   +2 more
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Transmission of Creutzfeldt–Jakob disease with scrapie-like syndromes to mice

Nature, 1978
THE transmission of Creutzfeldt–Jakob disease of man, one of the subacute spongiform virus encephalopathies1, to guinea pigs2,3 and to hamsters4 has been reported from this laboratory; Brownell et al. have also claimed transmission of Creutzfeldt–Jakob disease to mice5,6.
E E, Manuelidis, E J, Gorgacz, L, Manuelidis   +2 more
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Creutzfeldt-Jakob disease presenting as Wernicke-Korsakoff syndrome

Journal of the Neurological Sciences, 1992
A 47-year-old man began to suffer from progressive truncal ataxia and mental alterations typical of Wernicke-Korsakoff syndrome. He showed confusional state, hallucinations, delirium of jealousy and a serious impairment of recent memory. The symptomatology lasted 13 months, but only in the last weeks was it complicated by myoclonias.
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[A note on the epidemiology of Creutzfeldt-Jakob syndrome].

Revue neurologique, 1998
The annual incidence of sporadic Jakob-Creuzfeldt disease has been stable for the last 30 years. The new variant affecting young adults which appeared in the United Kingdom (20 cases) and France (1 case) in 1994 is due to the same infectious agent which causes bovine spongiform encephalopathy.
A, Alpérovitch, N, Delasnerie-Lauprêtre, J P, Brandel   +2 more
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Characterising the uncommon corticobasal syndrome presentation of sporadic Creutzfeldt-Jakob disease

Parkinsonism & Related Disorders, 2013
Corticobasal syndrome (CBS), which encompasses cortical sensory loss, alien limb, bradykinesia, rigidity, limb apraxia and dystonia, is the classic presentation of corticobasal degeneration (CBD). It may occur in other neurodegenerative disorders including sporadic Creutzfeldt-Jakob disease (sCJD).
Lee, W, Simpson, M, Ling, H, Mclean, C, Collins, S, Williams, DR   +5 more
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Mutations in familial Creutzfeldt-Jakob disease and Gerstmann-Sträussler-Scheinker's syndrome

Experimental Neurology, 1989
A host protein encoded by the gene specifying the scrapie amyloid precursor affects pathogenesis of the transmissible spongiform encephalopathies: Creutzfeldt-Jakob disease (CJD), Gerstmann-Sträussler-Scheinker's syndrome (GSS), and kuru in man, and scrapie in animals.
D, Goldgaber, L G, Goldfarb, P, Brown, D M, Asher, W T, Brown, S, Lin, J W, Teener, S M, Feinstone, R, Rubenstein, R J, Kascsak   +9 more
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MV2 subtype of sporadic Creutzfeldt‐Jakob disease presenting as corticobasal syndrome

Movement Disorders, 2007
Clinicopathologic correlative studies have shown that the corticobasal syndrome (CBS) is associated with various pathologies, including PSP, AD or sporadic Creutzfeldt-Jakob disease (sCJD), in addition to corticobasal degeneration (CBD. sCJD is generally distinguished from CBD by the much shorter duration of illness and the finding of either a 14-3-3 ...
Anna Magherini, Roberta Pentore, Giuliana Galassi, Carlo M. Stucchi, CAPELLARI, SABINA, PARCHI, PIERO   +5 more
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Balint's syndrome revealing Creutzfeldt-Jakob disease

Revue Neurologique, 2022
M, Escalere, C, Joly, J, Palisson, C, Budowski, M, Mongin, B, Degos   +5 more
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