Results 31 to 40 of about 2,648 (158)

A rare case of polyarteritis nodosa associated with nontuberculous mycobacterial infection

Clinical Case Reports, 2019
Clinicians should be aware that cutaneous PAN can present with significant extracutaneous and constitutional symptoms which make it hard to differentiate from systemic PAN. The condition can also rarely be associated with NTM infections.
ShengYang Bertrand Lian, Yee Leng Teoh, Yong‐Kwang Tay   +2 more
doaj   +1 more source

Poliarterite nodosa cutânea: relato de caso Cutaneous polyarteritis nodosa: case report

Anais Brasileiros de Dermatologia, 2006
Poliarterite nodosa cutânea é vasculite que acomete vasos de médio calibre na derme profunda e panículo adiposo. É caracterizada por nódulos dolorosos que podem ulcerar, antecedidos, acompanhados ou seguidos de livedo reticular, sendo seu diagnóstico ...
Izelda Maria Carvalho Costa, Lucas Souza-Carmo Nogueira   +1 more
doaj   +1 more source

Recent topics related to etiology and clinical manifestations of cutaneous arteritis

Frontiers in Medicine, 2022
Cutaneous polyarteritis nodosa (cPAN) was first reported by Lindberg in 1931. It has been recognized as a skin-limited vasculitis whose cutaneous histopathological features are indistinguishable from those of PAN.
Takaharu Ikeda
doaj   +1 more source

Inborn errors of immunity in children with neuroinflammation

Developmental Medicine &Child Neurology, EarlyView.
Abstract Inborn errors of immunity (IEIs), an expanding group of monogenic disorders with diverse clinical manifestations, are increasingly recognized to include neuroinflammatory disease. Examples of diseases included under this umbrella are Aicardi–Goutières syndrome, deficiency of adenosine deaminase 2, familial haemophagocytic lymphohistiocytosis ...
Eppie M Yiu, Dilan Dissanayake, Jessie Cunningham, Helen Branson, Ori Scott, E Ann Yeh   +5 more
wiley   +1 more source

Focal vascular occlusion: A link between livedoid vasculopathy and cutaneous arteritis?

JEADV Clinical Practice, 2023
Background Livedoid vasculopathy (LV) and cutaneous arteritis (CA) are rare cutaneous diseases. A consideration of these two conditions as different entities is debatable, because thrombosis and inflammation are closely related in their pathogenesis ...
Géza R. Nagy, Klára Veres, Nóra Belső, István Balázs Németh, Erika Varga, Irma Korom, Lajos Kemény, Zsuzsanna Bata‐Csörgő   +7 more
doaj   +1 more source

When to consider an inborn error of immunity: clues for physicians

Internal Medicine Journal, EarlyView.
Abstract The term inborn errors of immunity (IEIs) refers to the rapidly expanding group of genetic disorders causing dysregulation of the immune system. With improved genetic testing in recent years, the number of defined IEIs and their range of phenotypic presentations has grown vastly, with more than 550 IEIs now described.
Meera Thangarajah, Lucinda J. Berglund
wiley   +1 more source

Rare Gain‐of‐Function Variants in IDH1 and IDH2 Confer Increased Risk of Immune‐Mediated Rheumatic Diseases

ACR Open Rheumatology, Volume 8, Issue 4, April 2026.
Objective Gain‐of‐function variants in IDH1 and IDH2 are enriched among individuals with coexisting myeloid neoplasms and autoimmune diseases. However, the association between IDH1/IDH2 variants and rheumatic diseases independent of hematologic neoplasms remains unclear. We investigated the association between rare gain‐of‐function and loss‐of‐function
Mahmut S. Kaymakci, Mehmet Hocaoğlu, Kenneth J. Warrington, Amr H. Sawalha   +3 more
wiley   +1 more source

Safety of Immune Checkpoint Inhibitors in Cancer Patients With Preexisting Autoimmune Vasculitis

ACR Open Rheumatology, Volume 8, Issue 3, March 2026.
Objective Immune checkpoint inhibitors (ICIs) are effective cancer therapies but often cause serious immune‐related adverse events (irAEs). Patients with preexisting autoimmune diseases, including vasculitis, are excluded from trials. We aimed to evaluate the frequency, severity, and outcomes of vasculitis flares and irAEs in this population.
Juan Sevillano, Noha Abdel‐Wahab, Yixuan Zhou, Juan I. Ruiz, Maria E. Suarez‐Almazor   +4 more
wiley   +1 more source

Mendelian Randomization and Double Machine Learning Modeling Reveal Brain Imaging‐Derived Phenotypes as Functional Contributors to 18 Autoimmune Inflammatory Diseases

Advanced Science, Volume 13, Issue 14, 9 March 2026.
This schematic integrates the eight statistically significant causal relationships identified between 1,366 brain imaging‐derived phenotypes (IDPs) and 18 autoimmune inflammatory diseases (AIDs). Arrows indicate the direction of causality inferred from bidirectional two‐sample MR analyses.
Jinbin Chen, Xin Wang, Haifeng Ding, Bosheng Zheng, Keni Zeng, Chuying Hu, Jiayi Liu, Xiao Zhu, Haibing Yu   +8 more
wiley   +1 more source

Doença inflamatória intestinal com gangrena cutânea mimetizando a poliarterite nodosa Intestinal inflammatory disease with cuvaneous gangrene simulating polyarteritis nodosa

Revista Brasileira de Reumatologia, 2003
Descrevemos o caso de uma paciente com retocolite ulcerativa que apresentou gangrena cutânea secundária à trombose microvascular. Esta rara complicação da doença inflamatória intestinal é decorrente do estado de hipercoagulabilidade observado na sua fase
Adriana de H. Mafaldo Diógenes, Jane Teresa A. Soares, Aleksander Snioka Prokopowitsch, Eduardo Ferreira Borba Neto, Célio Roberto Gonçalves, Maurício Levy Neto   +5 more
doaj   +1 more source