Results 161 to 170 of about 66,003 (314)

The Clinical Spectrum and Neurodevelopmental Pathogenesis of KPTN‐Related Disorder in a Mouse Model

Annals of Neurology, EarlyView.
Objective Pathogenic variants in Kaptin (KPTN) cause KPTN‐related disorder (KRD). KPTN modulates mTOR signaling activation within the KICSTOR complex in response to cellular amino acid levels. We define the clinical spectrum and investigate the developmental pathogenesis of KRD.
Lettie E. Rawlins, Philip H. Iffland II, John Page, Rebecca Z. Flessner, Soad M. Elziny, Irina Sbornova, Janice K. Babus, Sophie R. Bruckmeier, Ria Parikh, Merel Verhoeven, James Fasham, Joseph S. Leslie, Richard Caswell, Nishanka Ubeyratna, Olivia Wenger, Ethan M. Scott, John Schreiber, Steffen Syrbe, Annick Klabunde‐Cherwon, Martina Owens, Andrew H. Crosby, Emma L. Baple, Peter B. Crino, the KPTN Consortium, Andrea Seeley, Heather Rocha, Sabine Rudnick, Ulrich Schaatz, Tobias Haack, Eva Schwaibold, Caleb Bupp, Klaas Wierenga, John Schreiber, Thorkild Terkelsen, Sarina Kant, J. C. Herkert, Michael Wright, Boris Keren, Solveig Heide, Pamela Jackson, Pradeep Vasudevan, Helen Stewart, Perrine Charles, Andreas Hahn, Saskia Biskup, Inger‐Lise Mero, Martin Heier, Conny van Ravenswaaij‐Arts, Esther Nibbeling, Stephanie Efthymiou, Erum Afzal, Ian Ellis, Raza Maroofian, Almundher Al‐Maawali, David Coman, Anthony Morosini, Sajjad Biglari, Pooneh Nikuei, Saadet Mercimek‐Andrews, Prab Prabhakar, Raymond Louie, Kameryn Butler, Olivia Wenger, Ethan M. Scott, Andrea Seeley, Heather Rocha, Amber Begtrup, Sabine Rudnik, Ulrich Schatz, Tobias Haack, Eva Schwaibold, Caleb Bupp, Klaas Wierenga, John Schreiber, Thorkild Terkelsen, Sarina Kant, J. C. Herkert, Michael Wright, Boris Keren, Solveig Heide, Pamela Jackson, Pradeep Vasudevan, Helen Stewart, Perrine Charles, Andreas Hahn, Saskia Biskup, Inger‐Lise Mero, Martin Heier, Marijn Stokman, Conny van Ravenswaaij‐Arts, Esther Nibbeling, Stephanie Efthymiou, Erum Afzal, Kristina Zhelcheska, Henry Houlden, Ian Ellis, Reza Maroofian, Gholamreza Shariati, Hamid Galehdari, Almundher Al‐Maawali, Adila Al‐Kindi, Andrew Y. Shuen, Victoria Siu, Annick Klabunde‐Cherwon, Steffen Syrbe   +104 more
wiley   +1 more source

Engineering Tertiary Lymphoid Structures: Nanomedicine, Bioengineering, and Biomaterials for Precision Immunotherapy

Advanced NanoBiomed Research, EarlyView.
This review explains how biomaterials and nanoparticles can be used to induce or modulate tertiary lymphoid structures (TLSs), which are ectopic immune hubs that form in nonlymphoid tissues during chronic disease and cancer. By comparing different methods, the article highlights design principles for modeling TLSs or recapitulating specific TLS ...
Shaza Karaman, Mei ElGindi, Jeremy Teo
wiley   +1 more source

Photovoltaic-Related "Black Swan" Hypothesis for Electric Power System: Phenomenology, Simulations, Experiences, and Prevention. [PDF]

Sensors (Basel)
Sladic S, Zivic E.
europepmc   +1 more source

An Exploratory Study on Graphene‐Based Hybrid Epoxy Coatings for Corrosion Resistance and Self‐Healing

Asia-Pacific Journal of Chemical Engineering, EarlyView.
ABSTRACT Corrosion of metallic process equipment in chemical, marine, and offshore industries leads to significant maintenance costs and safety concerns. Conventional epoxy coatings, though widely applied, often deteriorate under harsh conditions due to microcracking, moisture ingress and lack of self‐healing capability.
Thean Nam Low, Peck Loo Kiew, Mui Yen Ho, Ping Ping Chung, Maxine Swee Li Yee, Muhammad Fadhirul Izwan Abdul Malik   +5 more
wiley   +1 more source

Enhanced sliding mode control for parallel-integrated boost converters in hybrid solar-wind systems. [PDF]

Sci Rep
Arunyuvaraj K, M VP, Aravind P.
europepmc   +1 more source

Regulation of the power production of photovoltaic DC/AC converters

Summarization: The continuously increasing demand of electric energy in modern societies, along with the increasing cost of fossil fuels are two of the main factors that led to a rapid increase on the share of photovoltaic (PV) systems in modern electricity generation and transmission grids.
Λιουδακης Εμμανουηλ(http://users.isc.tuc.gr/~elioudakis), Lioudakis Emmanouil(http://users.isc.tuc.gr/~elioudakis)   +1 more
openaire   +1 more source

Improved Dry‐Pressing Strategy for Fabricating Double‐Sided Rough YSZ Electrolyte Thin Films and Their Performance in Solid Oxide Cells

Asia-Pacific Journal of Chemical Engineering, EarlyView.
ABSTRACT This study addresses limitations of the conventional dry‐pressing method for electrolyte‐supported films—smooth surfaces, excessive thickness, and fragile supports inducing damage. We propose an innovative camphor–quartz sand composite architecture to construct a five‐layer (camphor/quartz sand/YSZ/quartz sand/camphor) system, enabling thin ...
Hong Chang, Hewei Xu, Haoyu Li, Jiachun Niu, Lina Zhang, Chenying Yao, Yiyi Zhang, Huili Chen, Chuan Dong   +8 more
wiley   +1 more source

Hybrid quasi Z source multi output converter system with performance control and real time validation for photovoltaic microgrid. [PDF]

Sci Rep
Deori P, Ahmad A, Routray A.
europepmc   +1 more source

Bridging the Gap: Integrating Energy Management with Moisture‐Electric Energy Harvesting

Advanced Physics Research, EarlyView.
This review explores energy management strategies that have been successfully applied in other energy harvesting systems, with the aim of adapting such strategies for MEG applications. Through analysis, learning, and adaptation of these existing systems, it is possible to help MEGs achieve more stable electrical output and accelerate their real‐world ...
Zhongliang Zhang, Renbo Zhu, Xiaoming Tao   +2 more
wiley   +1 more source

Current sensorless MPPT method with battery management for PV based single phase standalone system. [PDF]

Sci Rep
Genc N, Uzmus H, Kalimbetova Z, Celik MA, Ramankulov S.   +4 more
europepmc   +1 more source