Results 61 to 70 of about 190,515 (293)

SPG4 and Dementia: Expanding the Clinical Spectrum

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Hereditary spastic paraplegia (HSP) is a group of disorders characterized by progressive spasticity and lower limb weakness, with mutations in SPG4/SPAST being the most common cause. Detailed studies and clinical and molecular comparisons across different populations are missing.
Emanuele Panza, Arun Meyyazhagan, Eliseo Picchi, Gustavo Ribas, Ingrid Faber, Ryosuke Miyamoto, Preethi Basavaraju, Paolo Eusebi, Haripriya Kuchi Bhotla, Mario Stasi, Fabrizio Gaudiello, Francesco Patti, Filippo Maria Santorelli, Marcondes Cavalcante França Jr, José Luiz Pedroso, Orlando Graziani Povoas Barsottini, Hélio Afonso Ghizoni Teive, Peter Henry St George‐Hyslop, Toshitaka Kawarai, Antonio Orlacchio   +19 more
wiley   +1 more source

Investigation of Characteristics of Passive Heat Removal System Based on the Assembled Heat Transfer Tube

Nuclear Engineering and Technology, 2016
To get an insight into the operating characteristics of the passive residual heat removal system of molten salt reactors, a two-phase natural circulation test facility was constructed.
Xiangcheng Wu, Changqi Yan, Zhaoming Meng, Kailun Chen, Shaochuang Song, Zonghao Yang, Jie Yu   +6 more
doaj   +1 more source

GEN-IV LFR development: Status & perspectives [PDF]

, 2018
Since Lead-cooled Fast Reactors (LFR) have been conceptualized in the frame of Generation IV International Forum (GIF), great interest has focused on the development and testing of new technologies related to Heavy Liquid Metal (HLM) nuclear reactors. In
Bassini, Serena, Del Nevo, Alessandro, Di Piazza, Ivan, Giannetti, Fabio, Lorusso, Pierdomenico, Tarantino, Mariano, Utili, Marco   +6 more
core   +1 more source

Thermoreflectance Detection of Point Defects Resulting from Focused Ion Beam Milling

Advanced Engineering Materials, EarlyView.
Focused ion beam (FIB) milling is a common tool for nanoscale material processing, however irradiation damage, redeposition, and contamination can occur. We use several characterization tools to show FIB‐induced effects beyond 1 mm from the milled area.
Thomas W. Pfeifer, Eric R. Hoglund, Anton V. Ievlev, Patrick E. Hopkins   +3 more
wiley   +1 more source

Analysis of transient characteristics and design improvement of the passive residual heat removal system of NHR-200-II

Frontiers in Energy Research
NHR-200-II is a small integrated pressurized water reactor with 200 MW core thermal power. The core heat is transferred to two independent intermediate circuits via fourteen in-vessel primary heat exchangers (PHE), and the heat in the intermediate ...
Geng Yiwa, Liu Xiongbin, Li Ziyi, Huang Shuliang, Zhou Lanyu, Xue Yanfang, Li Xiaotian, Zhang Yajun   +7 more
doaj   +1 more source

Influence of thermal treatment and residues on space charge accumulation in XLPE for DC power cable application [PDF]

, 2007
Effects of cross-linking by-products (residues) of polyethylene on space charge accumulation and decay are investigated in the paper using the pulsed electro-acoustic technique.
Chen, G., Dissado, A., Fothergill, J., Fu, M.   +3 more
core   +1 more source

Harnessing Fungal Biowelding for Constructing Mycelium‐Engineered Materials

Advanced Engineering Materials, EarlyView.
Mycelium‐bound composites (MBCs) offer low‐carbon alternatives for construction, yet interfacial bonding remains a critical challenge. This review examines fungal biowelding as a biocompatible adhesive, elucidating mycelium‐mediated interfacial mechanisms and their role in material assembly. Strategies to optimize biowelding are discussed, highlighting
Xue Brenda Bai, Xinrui Sarah Niu, Zhao Qin   +2 more
wiley   +1 more source

Packaging of Macroscopic Material Payloads: Needs, Challenges, Concepts, and Future Directions

Advanced Engineering Materials, EarlyView.
This review introduces a unified framework that decomposes any macroscopic packaging system into the payload, packaging material, and packaging strategy and combines them into a conceptual packaging equation: packaging strategy = payload + packaging material.
Venkata S. R. Jampani, Manos Anyfantakis
wiley   +1 more source

Heat removal efficiency of stratum ventilation for air-side modulation [PDF]

, 2019
Stratum ventilation has significant thermal non-uniformity between the occupied and upper zones. Although the non-uniformity benefits indoor air quality and energy efficiency, it increases complexities and difficulties in the air-side modulation. In this
Cheng, Y, Huan, C, Lin, Z, Oladokun, MO, Zhang, S   +4 more
core   +2 more sources

Zein‐Based Adhesives: Sustainable Extraction and Application in Bioadhesive Technologies

Advanced Engineering Materials, EarlyView.
Zein is extracted from corn gluten meal using a simple and scalable process with high yield (~90%). The resulting protein is applied in bioadhesives modified with Ca2+ and Fe3+ ions, exhibiting substrate‐dependent adhesion. The findings demonstrate competitive bonding performance and highlight the role of ionic interactions in tuning adhesion ...
Paula Bertolino Sanvezzo, Daniela Winsley Valereto Friozi, Vinícius de Oliveira, Marcia Cristina Branciforti   +3 more
wiley   +1 more source