Management of Osteogenesis Imperfecta Complicated by Severe Pneumonia in a Resource-Limited Setting: A Case Report. [PDF]
Case Rep PediatrIntroduction Osteogenesis imperfecta (OI) is a rare genetic disorder characterized by bone fragility, skeletal deformities, and multisystem involvement, with respiratory complications representing a major cause of morbidity and mortality. Intrinsic pulmonary abnormalities, restrictive physiology from scoliosis, and impaired secretion clearance increase
Shah BK +6 more
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Restorative Management of Dentinogenesis Imperfecta in an adult - A case report [PDF]
Nigerian Dental Journal, 2020 Dentinogenesis Imperfecta is a localized mesodermal dysplasia affecting both the primary and permanent dentition. First described in the late 19th century, it is characterized by discolored and translucent teeth ranging from grey to brownish-blue or ...
A.O. Awotile, L.L. Enone, A. Oyapero
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Phenotypic Properties of Collagen in Dentinogenesis Imperfecta Associated with Osteogenesis Imperfecta [PDF]
International Journal of Nanomedicine, 2019 Salwa Ibrahim,1,* Adam P Strange,2,* Sebastian Aguayo,2,3 Albatool Shinawi,1 Nabilah Harith,1 Nurjehan Mohamed-Ibrahim,1 Samera Siddiqui,2 Susan Parekh,1 Laurent Bozec4 1Department of Paediatric Dentistry, UCL Eastman Dental Institute, University College
Ibrahim S +8 more
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Immunocytochemical detection of dentin matrix proteins in primary teeth from patients with dentinogenesis imperfecta associated with osteogenesis imperfecta [PDF]
European Journal of Histochemistry, 2014 Dentinogenesis imperfecta determines structural alterations of the collagen structure still not completely elucidated. Immunohistochemical analysis was used to assay Type I and VI collagen, various non-collagenous proteins distribution in human primary ...
G. Orsini +6 more
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Journal of Indian Academy of Oral Medicine and Radiology, 2003 Osteogenesis Imperfecta is a genetic disorder affecting approximately 20,000 U.S. population with multiple fracture of the bone. The, actual literature of the number of patients suffering from Osteogenesis Impcrfecta in Indian Population is still nor ...
Prabal Pal
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Full Mouth Rehabilitation of Two Siblings with Dentinogenesis Imperfecta Type II Using Different Treatment Modalities [PDF]
International Journal of Environmental Research and Public Health, 2020 Murad Alrashdi, Shuo Chen
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Oral manifestations and rehabilitation of a patient with osteogenesis imperfecta [PDF]
Srpski Arhiv za Celokupno Lekarstvo, 2021 Introduction. Osteogenesis imperfecta is a rare heritable connective tissue disorder characterized by increased fragility of the bony tissue. The incidence of orofacial alterations associated with osteogenesis imperfecta is variable and includes ...
Milanović Milena +5 more
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Tratamiento integral y control a 12 años de paciente con Dentinogénesis Imperfecta tipo I
Revista de Odontopediatria Latinoamericana, 2021 La Dentinogénesis Imperfecta es una anomalía dentaria determinada genéticamente y caracterizada clínicamente por una apariencia ámbar opalescente de la dentina.
Ingrid Clarisa Guitelman +2 more
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Dentinogenesis imperfecta: The Genetic Causes and Outcomes [PDF]
, 2021 Dentinogenesis imperfecta (DI) is a genetic disorder characterized by dentin discoloration, tooth development irregularities, and decreased tooth strength. This autosomal dominant disorder is identified in individuals of all ages.
Johnson, Sydney P, Ms.
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Dentinogénesis imperfecta tipo II: Reporte de un caso
Revista de Odontopediatria Latinoamericana, 2021 La Dentinogénesis Imperfecta es un desorden genético de carácter hereditario autosómico dominante, que se caracteriza por defectos en la dentina de ambas denticiones.
Magdalena San Martín +3 more
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