Results 41 to 50 of about 30,001 (236)

CORRELATIONS BETWEEN NAILFOLD CAPILLAROSCOPY FINDINGS AND DISTINCT CLINICAL FORMS OF JUVENILE DERMATOMYOSITIS [PDF]

Romanian Journal of Rheumatology, 2019
Juvenile dermatomyositis is the most common idiopathic inflammatory myopathy in childhood. Nailfold capillaroscopy plays an important role in its assessment, being useful for diagnosis and follow-up.
Sigrid Covaci, Oana-Maria Farkas, Alexis-Virgil Cochino   +2 more
doaj   +1 more source

Incidence, Risk Factors and Management of Adverse Events in Contemporary Real‐World Care of Children with Juvenile Idiopathic Arthritis

Arthritis Care &Research, Accepted Article.
Objective We describe the frequency, risk factors, severity, and management of actionable and serious adverse events (AAE and SAE) in children with newly diagnosed Juvenile Idiopathic Arthritis (JIA) in Canada. Methods We enrolled patients within 3 months of JIA diagnosis in the Canadian Alliance of Pediatric Rheumatology Investigators (CAPRI) Registry,
Bashayer Alnuaimi, Roberta A. Berard, Jean‐Philippe Proulx‐Gauthier, Heinrike Schmeling, Michelle Batthish, Gilles Boire, Adam M. Huber, Dax G. Rumsey, Jaime Guzman, Gaëlle Chédeville, The CAPRI registry Investigators   +10 more
wiley   +1 more source

Recalcitrant Dermatomyositis Treated With Anifrolumab

ACR Open Rheumatology
Dermatomyositis is an idiopathic inflammatory myopathy which can present with distinctive skin features. Despite the many treatment modalities for the treatment of dermatomyositis some patients remain refractory to treatment.
Shivang Chaudhary, Meghan Baumer, Laura Upton, Samantha Ong, Kristin Smith, Daniel West, Adam Kilian   +6 more
doaj   +1 more source

Anti-nuclear matrix protein 2 antibody-associated juvenile dermatomyositis with gastrointestinal perforations was successfully treated with traditional therapeutic drugs combined with vedolizumab: a case report after a long-term follow-up and a review of the literature

Frontiers in Pediatrics
Gastrointestinal perforation in patients with juvenile dermatomyositis has been reported as a life-threatening complication in the literature. However, effective treatment of juvenile dermatomyositis with gastrointestinal perforation remains challenging.
Xue-mei Xu, Shuang Ye, Ying-ying Jin, Chen-xi Liu, Sheng-fang Bao, Hua Huang, Fei Ding, Zhen Yang, Yan-liang Jin   +8 more
doaj   +1 more source

Narrowband Intense Pulsed Light Treatment for Refractory Facial Rash Associated with Dermatomyositis

Clinical, Cosmetic and Investigational Dermatology, 2023
Yuxin Zheng, Suiqing Cai Department of Dermatology, Zhejiang University School of Medicine Second Affiliated Hospital, Hangzhou, People’s Republic of ChinaCorrespondence: Suiqing Cai, Department of Dermatology, Zhejiang University School of Medicine ...
Zheng Y, Cai S
doaj  

Amyopathic Dermatomyositis Associated with Histopathological Findings of Organizing Pneumonia and Pulmonary Vasculitis

Balkan Medical Journal, 2017
Background: Clinically, amyopathic dermatomyositis is a clinically distinct subgroup of dermatomyositis characterised by unique dermatological manifestations without muscle involvement. Clinically, amyopathic dermatomyositis is frequently associated with
Jeong Uk Lim, Hye Seon Kang, Yong Hyun Kim, Tae-Jung Kim   +3 more
doaj   +1 more source

Dermatomyositis as a Paraneoplastic Syndrome Secondary to Carcinoma of Cervix: A Rare Clinical Association [PDF]

Clin Case Rep
ABSTRACT Dermatomyositis (DM) is a rare idiopathic inflammatory myopathy characterized by symmetric proximal muscle weakness and distinctive cutaneous manifestations. It is frequently associated with underlying malignancies, making recognition of paraneoplastic features crucial.
Chapagain M, Adhikari P, Pudasaini N, Poudel S, Timilsina B.   +4 more
europepmc   +2 more sources

Severe Phenotype in an Indian Family With Progressive Pseudorheumatoid Arthropathy of Childhood

American Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Progressive pseudorheumatoid arthropathy of childhood (PPAC) is a rare autosomal recessive progressive condition that affects the cartilage of joints and bones. The symptoms of PPAC include stiffness of the joints, bony swelling of the toes and fingers, short stature, kyphosis, and muscle weakness.
Narinder Singh, Arpita Neogi, Liliane H. Gibbs, Jagdish Soni, Elizabeth Chao, Virginia Kimonis   +5 more
wiley   +1 more source

Interleukin‐2 Deprived State of Regulatory T cells and Their Recovery by Low‐Dose Interleukin‐2 in Patients With Inflammatory Myopathies

Arthritis &Rheumatology, EarlyView.
Objective Regeneration and expansion of Treg by low‐dose interleukin‐2 (IL‐2) therapy is considered a potential treatment strategy for a wide range of autoimmune diseases. To provide a pathophysiologically‐based rationale for low‐dose IL‐2 therapy, we investigated whether reversible defects in the Treg–IL‐2 axis emerge in inflammatory myopathies ...
Justus Ohmes, Luisa R. Monne, Sara Comdühr, Fynn Gerlach, Hanna Grasshoff, Alexander Dübbers, Antje Müller, Alexander Scheffold, Gabriela Riemekasten, Reza Akbarzadeh, Jens Y. Humrich   +10 more
wiley   +1 more source

Paraneoplastic Dermatomyositis: About 9 Patients [PDF]

, 2016
Dermatomyositis, a rare inflammatory disease possibly of autoimmune origin, produces a characteristic skin rash and symmetrical proximal myopathy. Patients with Dermatomyositis have a higher incidence rate of cancer, compared with the general population,
FZ Mernissi, H Baybay, A Lahlou, S Elloudi   +3 more
core   +1 more source