Results 61 to 70 of about 8,831 (160)

Desmoid Fibromatosis Presenting with Gastrointestinal Manifestations in a Patient with Ehlers-Danlos Syndrome: A Case Report [PDF]

Journal of Clinical and Diagnostic Research
Ehlers-Danlos syndrome comprises 13 hereditary connective tissue disorders associated with skin hyperelasticity, joint hypermobility, atrophic scarring, and blood vessel fragility.
Elias Lugo-Fagundo, Edmund M Weisberg, Ryan C Rizk, Elliot K Fishman   +3 more
doaj   +1 more source

Aggressive Desmoplastic Small Round Cell Tumor in an Adult: A Case Report and Literature Review

Clinical Case Reports, Volume 14, Issue 5, May 2026.
ABSTRACT Desmoplastic small round cell tumor (DSRCT) is a rare and highly aggressive sarcoma that predominantly affects adolescents and young adults. It is defined by a characteristic chromosomal translocation, t(11;22) (p13;q12), resulting in the EWS–WT1 fusion gene.
Seyed Amir Aledavood, Ehsan Soltani, Mahsa Akbari Oryani, Hourieh Soleimani, Noushin Saleki   +4 more
wiley   +1 more source

Medical treatment of mammary desmoid-type fibromatosis: which benefit?

, 2017
Background Breast fibromatosis is a rare disease characterized by monoclonal fibroblast proliferation. It has no ability to metastasize but has a high local recurrence rate and often infiltrates surrounding tissues.
Lodi, Massimo, Louise Scheer, Sébastien Molière, Massimo Lodi, Carole Mathelin, Jean-Emmanuel Kurtz, Scheer, Louise, Molière, Sébastien, Mathelin, Carole, Kurtz, Jean-Emmanuel   +9 more
core   +1 more source

Resection and postoperative radiation therapy for desmoid fibromatosis of the chest wall in a young woman

Surgical Case Reports, 2021
Background Surgery is an effective treatment for desmoid fibromatosis, but it may be difficult, depending on the location or local spread of the tumor, and the decision to perform surgery must be made carefully.
Daiki Noda, Miyuki Abe, Yohei Takumi, Kentaro Anami, Michiyo Miyawaki, Hideya Takeuchi, Atsushi Osoegawa, Kenji Sugio   +7 more
doaj   +1 more source

Oncogenic driver and therapeutic target: Prolactin signalling axis in retroperitoneal sarcoma

Clinical and Translational Medicine, Volume 16, Issue 5, May 2026.
Retroperitoneal sarcoma cells can secrete prolactin into the bloodstream, inducing hyperprolactinaemia, which subsequently triggers metabolic reprogramming, such as glucose metabolism. SOX4 can function as a transcription factor that facilitates PRL transcription.
Fu'an Xie, Lingwei Gu, Kunrong Yang, Shuai Wang, Mengmeng Xiao, Guangting Yan, Quan Zhang, Rubing Liang, Aobo Zhuang, Zhe Xi, Yujia Niu, Yanhua Chen, Xiaogang Xia, Linlin Qu, Bin Zhao, Weibing Li, Ting Wu, Chundong Yu, Chenghua Luo, Houzhao Wang, Lanlan Lian, Wengang Li   +21 more
wiley   +1 more source

A Unique Collaboration Between Otolaryngology, Cardiothoracic Surgery, and Spine Surgery for Paraspinal Desmoid-Type Fibromatosis: A Case Report and Systematic Review

Journal of Spine Practice
Purpose Desmoid-type fibromatosis is a rare, aggressive tumor of mesenchymal origin that mimics malignancy. Though non-metastasizing, desmoid tumors exhibit local invasion and tissue destruction with high rates of recurrence, leading to severe morbidity.
Nikhil Dholaria, Ali A. Baaj, Chetan Gujrathi   +2 more
doaj   +1 more source

11‐year‐old girl presenting with blurred vision and progressive right arm weakness

Brain Pathology, Volume 36, Issue 6, November 2026.
Trung Toan Tran, Thi My Hanh Luong, Bérengère Dadone‐Montaudié, Hong Nhung Ta, Thai Hoc Nguyen, Fanny Burel‐Vandenbos, Gia Du Pham   +6 more
wiley   +1 more source

Decoding the Hexosamine Biosynthesis Pathway: Implications for Novel Therapeutic Strategies in Sarcoma

Journal of Cellular Physiology, Volume 241, Issue 5, May 2026.
ABSTRACT Cancer cells rewire their metabolism to sustain a high proliferation rate. Sensing external cues is essential to match the metabolic fluxes of the cells to the external stimuli. As part of the glucose metabolism, the hexosamine biosynthesis pathway (HBP) is considered a nutrient‐sensing pathway. The HBP produces UDP‐GlcNAc, a key precursor for
Pegah Rahimizadeh, Richard Miallot, Chelsea De Bellis, Philippe Jolivet, Joanna Przybyl   +4 more
wiley   +1 more source

Mesenteric desmoid tumor in its cystic form: Case report of a very rare variant

Radiology Case Reports
Desmoid tumors, also known as deep fibromatosis or desmoid-type fibromatosis, represent a rare subset of deep fibromatoses. It is a locally aggressive tumor, with no specific symptoms, and no metastatic potential.
Nourrelhouda Bahlouli, Kaouthar Imrani, Esseti Sara, Fatima Chait, Faraj Chaimae, Moatassimbillah Nabil, Ittimad Nassar, Sassi Samia, Derqaoui Sabrine, Bernoussi Zakia, Babana Alaoui Amina, Touhami Ouazzani Youssef, Lahjomri Ismail, Hadj Omar El Malki, Ifrine Lahcen, Belkouchi Abdelkader, Belkouchi Omar   +16 more
doaj   +1 more source

Aggressive juvenile fibromatosis of the paranasal sinuses: case report and brief review

Journal of Hematology & Oncology, 2008
Desmoid fibromatoses are benign, slow growing fibroblastic neoplasms, arising from musculoaponeurotic stromal elements. Desmoids are characterized by local invasion, with a high rate of local recurrence and a tendency to destroy adjacent structures and ...
Lakhan Shaheen E, Eager Robert M, Harle Lindsey   +2 more
doaj   +1 more source