Displasia fibrosa de senos paranasales. Presentación de Caso [PDF]
Introduction: Fibrous dysplasia is a developmental defect characterized by focal sequestration of normal osteoblastic activity of bone in the absence of maturation of its components.
Toledo-Valdés, Carmen +2 more
core
An integrated approach for rare disease detection and classification in Spanish pediatric medical reports. [PDF]
Duque A +5 more
europepmc +1 more source
Parosmia como debut de una Displasia Fibrosa
Fibrous Dysplasia is a rare benign bone disorder with unknown aetiology; consists in replacement of normal medullary bone by fibroosseous tissue, causing distortion and overgrowth of the bones involved.
Galindo Ortego, Javier +2 more
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Developing a Standardised Dataset for Natural History Studies in Fibrous Dysplasia/McCune-Albright Syndrome. [PDF]
Priego Zurita AL +19 more
europepmc +1 more source
[Brown tumor due to hyperparathyroidism secondary to chronic kidney disease: A clinical case]. [PDF]
Contreras-Vargas LM +9 more
europepmc +1 more source
[Diagnosis and treatment in a series of patients with cardiac corrected transposition of the great arteries (double discordance)]. [PDF]
De Rubens-Figueroa J +4 more
europepmc +1 more source
Displasia fibrosa: do diagnóstico à cirurgia
Apresenta-se o caso de uma adolescente de 13 anos de idade com queixas de dor inguinal esquerda com 3 anos de evolução, sem alterações relevantes ao exame objectivo. Imagiologicamente foi identificada lesão radiotransparente na região metafisária proximal e colo femoral esquerdos, associada a uma fractura incompleta. Pela manutenção das queixas álgicas,
Ramalho,Diogo +4 more
openaire +1 more source
Displasia fibrosa poliostótica con afectación de raquis cervical.
The fibrous dysplasia is a benign although progressive dysfunction, in which a gene mutation originates the production of fibrous disorganized bony matrix.
Modrego, Francisco Jaiver +5 more
core
Comparison of real-world kidney outcomes with predicted outcomes at the time of diagnosis and post-biopsy in a cohort of children with IgA nephropathy. [PDF]
Cabral MF +12 more
europepmc +1 more source
Bone health in cerebral palsy and introduction of a novel therapy. [PDF]
Scheinberg MA +5 more
europepmc +1 more source

