Results 61 to 70 of about 2,727 (206)

Familial pattern of large vestibular aqueduct syndrome in a Chinese family [PDF]

, 2013
Large Vestibular Aqueduct Syndrome (LVAS) is the most common radiographic malformation in children with early onset of hearing loss. Usually its occurrence is non-familial, however intriguingly a portion of patients with LVAS is found to have evidence ...
Ab Aziz, A, Asma, A, Hazmi, M
core  

Bone-Conducted oVEMP Latency Delays Assist in the Differential Diagnosis of Large Air-Conducted oVEMP Amplitudes

Frontiers in Neurology, 2020
Background: A sensitive test for Superior Semicircular Canal Dehiscence (SCD) is the air-conducted, ocular vestibular evoked myogenic potential (AC oVEMP). However, not all patients with large AC oVEMPs have SCD.
Rachael L. Taylor, Rachael L. Taylor, John S. Magnussen, Belinda Kwok, Belinda Kwok, Allison S. Young, Berina Ihtijarevic, Berina Ihtijarevic, Emma C. Argaet, Emma C. Argaet, Nicole Reid, Cheryl Rivas, Jacob M. Pogson, Jacob M. Pogson, Sally M. Rosengren, Sally M. Rosengren, G. Michael Halmagyi, G. Michael Halmagyi, Miriam S. Welgampola, Miriam S. Welgampola, Miriam S. Welgampola   +20 more
doaj   +1 more source

Enlarged vestibular aqueduct in cochlear implant patients [PDF]

, 2009
Vidgad vestibularakvedukt (EVA) är en inneröremissbildning och en vanlig orsak till ärftlig hörselnedsättning. Hörselnedsättningen är ofta av kombinerad typ och orsaken till den konduktiva komponenten antas ligga i innerörat. EVA diagnostiseras med hjälp
Hatt, Sanne, Öinert, Adam
core  

Neural Plasticity and Hearing‐Speech Development in Children with Auditory Brainstem Implants for Congenital Hearing Loss Due to Severe Inner Ear Malformation

Advanced Science, Volume 12, Issue 29, August 7, 2025.
Data from a prospective cohort with 112 auditory brainstem implant users are analyzed. Younger age at implantation (<3 years), less severe inner‐ear malformation (common cavity, cochlear aplasia, and hypoplasia), and more intraoperative eABR evoked electrodes (≥60%) are associated with better hearing and speech outcomes.
Yu Zhang, Yongchuan Chai, Yiwen Zhang, Huan Jia, Zhaoyan Wang, Zhihua Zhang, Zhili Wang, Jie Chen, Xue Wang, Yun Li, Ying Chen, Hao Wu   +11 more
wiley   +1 more source

AAVR Expression is Essential for AAV Vector Transduction in Sensory Hair Cells

Advanced Science, Volume 12, Issue 29, August 7, 2025.
Decreased sensitivity to AAV vector transduction in the outer hair cells (OHCs) of adult mice is primarily attributed to reduction of AAVR (Kiaa0319l; Au040320). Knockout of AAVR reduces AAV vector transduction efficiency in both inner hair cells (IHCs) and OHCs in neonatal mice.
Fan Wu, Guisheng Chen, Rui Hu, Peiwen Liu, Jintao Lou, Wenji Zhao, Zuhong He, Suhua Sha, Yiqing Zheng   +8 more
wiley   +1 more source

Stimulation from Cochlear Implant Electrodes Assists with Recovery from Asymmetric Perceptual Tilt: Evidence from the Subjective Visual Vertical Test [PDF]

, 2016
Vestibular end organ impairment is highly prevalent in children who have sensorineural hearing loss (SNHL) rehabilitated with cochlear implants (CIs). As a result, spatial perception is likely to be impacted in this population.
Blake C. Papsin, Carmen L. McKnight, Joshua J. Gnanasegaram, Karen A. Gordon, Sharon L. Cushing, William J. Parkes   +5 more
core   +1 more source

Unilateral Congenital Cartilaginous Rests of the Neck: A Case Report and Literature Review

Clinical Case Reports, Volume 13, Issue 8, August 2025.
ABSTRACT Unilateral congenital cartilaginous rests of the neck (CCRN) are rare, typically benign anomalies that can be clinically mistaken for other cervical lesions. Accurate diagnosis and effective management require a combination of thorough clinical evaluation, appropriate imaging, surgical excision, and histopathological confirmation.
Sayna Sabertehrani, Fateme Faramarzirad, Mehdi Gheisari, Khatere Zahedi   +3 more
wiley   +1 more source

Resolving the genetic heterogeneity of prelingual hearing loss within one family: Performance comparison and application of two targeted next generation sequencing approaches. [PDF]

, 2014
published_or_final_versio
A Yin, AE Shearer, AE Shearer, AJ Coffey, AM Sulonen, C Petit, C Petit, CC Morton, DL Dinwiddie, Dongyi Han, Fei Ji, G Van Camp, HM Woo, Huijun Yuan, I Schrauwen, Jing Cheng, JM Schultz, KwongWai Choy, Liyang Liu, LM Astuto, M Sotomayor, MA DePristo, MA Musarella, Michael Zhang, MJ Clark, NE Morton, PJ Coucke, R Tewhey, RJ Smith, SE Calvo, TA Sivakumaran, V Plagnol, W Tang, Weidong Shen, X Lin, X Liu, Xuegong Zhang, Xueya Zhou, Y Yuan, Ye Cao, Yu Lu, Z Brownstein, Zhanguo Jin   +42 more
core   +1 more source

Imaging of inner ear malformations: a primer for radiologists [PDF]

, 2021
In the multidisciplinary management of patients with inner ear malformations (IEMs), the correct diagnosis makes the differences in terms of clinical and surgical treatment.
Feraco P., Gagliardo C., Piccinini S.
core   +1 more source

Clinical Validation of Manual Measurement of Cochlea Length With Post‐Operative Electrode Insertion Depth: A Pilot Study

Laryngoscope Investigative Otolaryngology, Volume 10, Issue 4, August 2025.
ABSTRACT Objective To clinically validate manual measurement of cochlear length from pre‐operative image of cochlea with post‐operative image of cochlear implant (CI) electrode. Methods Temporal bone computer tomography (CT) scans of 23 ears were available for this pilot study.
Fei Wang, Dharmikkumar Anaghan, Anandhan Dhanasingh, Lian Hui   +3 more
wiley   +1 more source