Clinical management for epidermolysis bullosa dystrophica [PDF]
Journal of Applied Oral Science, 2008 Epidermolysis bullosa (EB) consists of a group of genetic hereditary disorders in which patients frequently present fragile skin and mucosa that form blisters following minor trauma.
Thais M. Oliveira +4 more
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Topical gene therapy for severe recessive dystrophic epidermolysis bullosa: clinical outcomes and multidisciplinary management in three patients treated with beremagene geperpavec (B-VEC) in Italy – a case series [PDF]
Drugs in ContextRecessive dystrophic epidermolysis bullosa is a severe inherited blistering disorder characterized by chronic wounds, fibrosis and systemic complications. Beremagene geperpavec (B-VEC), a topical HSV1-based gene therapy delivering full-length COL7A1, has
Michela Brena +2 more
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Role of regional anaesthesia in a patient with epidermolysis bullosa dystrophica for emergency surgery [PDF]
Indian Journal of Anaesthesia, 2021 Thirumurugan Arikrishnan +3 more
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Epidermolysis bullosa dystrophica inversa: case report of a novel genetic mutation, involving a rare genodermatoses [PDF]
Indian Dermatology Online Journal, 2023 Abhijit S Chakraborty +3 more
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Anaesthetic management in patients with epidermolysis bullosa dystrophica [PDF]
Anaesthesia, 1988 Summary Successful anaesthetic management of two patients with severe epidermolysis bullosa dystrophica was accomplished with the use of ketamine—diazepam dissociative anaesthesia in one and brachial plexus block in the other. The classification and pathology of epidermolysis bullosa is considered, and the problems associated with ...
R, Hagen, C, Langenberg
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Spinal Anaesthesia in a Patient with Epidermolysis Bullosa Dystrophica [PDF]
Anaesthesia and Intensive Care, 2000 An adult patient with epidermolysis bullosa dystrophica underwent uneventful spinal anaesthesia. Insertion of a Quincke spinal needle proved easier and produced less skin distortion than insertion of a pencil-point spinal needle. Taping of intravenous lines is an alternative to the more usually recommended approach of suturing.
M R, Patch, R D, Woodey
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Scrape to Nail the Diagnosis: A “Mitey” Challenge in an Erythroderma [PDF]
Journal of Clinical and Diagnostic Research, 2023 Norwegian (crusted) scabies is a highly contagious form of scabies which can evolve into erythroderma at times. We herein report a case of a 29-year-old male patient, an established case of epidermolysis bullosa dystrophica (EBD), presented to us with ...
S Praveen Kumar +3 more
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Oral and perioral soft tissue lesions and oral functions in patients with dystrophic epidermolysis bullosa [PDF]
Vojnosanitetski Pregled, 2022 Background/Aim. Dystrophic epidermolysis bullosa (DEB) is characterized by distinct systemic and skin changes, as well as numerous oral manifestations. The aim of the study was to examine oral and perioral soft tissues and oral functions in DEB patients ...
Čolović Aleksandra +4 more
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Indian Journal of Dermatology, 2022 Epidermolysis bullosa (EB) is a group of rare inherited conditions that results in blistering of the skin and mucous membranes. Mutations in the PLEC gene cause epidermolysis bullosa simplex (EBS).
Sunitha Tella +4 more
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Oral health status in children with inherited dystrophic epidermolysis bullosa [PDF]
Vojnosanitetski Pregled, 2017 Background/Aim. Epidermolysis bullosa is a group of rare, genetic connective tissue diseases that cause blisters in the skin and mucosal membranes.
Čolović Aleksandra +3 more
doaj +1 more source