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Epidermolysis bullosa dystrophica
1990Epidermolysis bullosa dystrophica (EBD) is a heterogeneous group of inherited mechanobullous diseases that produce separation in the deep portion of the basement membrane zone beneath the lamina densa (dermolytic separation) [1, 2] (Figure 16.1). Dystrophic scarring results from repeated blistering and serves as a clinical marker of these diseases ...
Robert A. Briggaman, Eugene A. Bauer
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Epidermolysis Bullosa Dystrophica Inversa in a Child
Pediatric Dermatology, 1990Abstract: A 4‐year‐old child with dystrophic epidermolysis bullosa inverse is described. Clinical features were blistering of the skin, erosions, scarring and milia formation. The areas involved included the trunk, with preference for the axillary and inguinal folds, the neck and sacral area, and proximal extremities.
Bruckner-Tuderman L +2 more
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Epidermolysis Bullosa Dystrophica in Children
Radiology, 1968Epidermolysis bullosa is a rare hereditary skin disease, in which slight trauma disrupts the cohesion between the epidermis and the dermis, resulting in the formation of vesicles, bullae, and ulcers. Sorsby (4) described three principal types of this disease.
M H, Becker, C A, Swinyard
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Esophageal involvement in epidermolysis bullosa dystrophica
American Journal of Roentgenology, 1983The clinical and radiographic findings in four cases of epidermolysis bullosa dystrophica of the esophagus are presented. The patients were 5-67 years old. All had typical skin lesions and dysphagia. The most impressive radiographic finding was bulla formation in virtually any part of the esophagus. The bullae would resolve or ulcerate.
J M, Tishler, S Y, Han, C A, Helman
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Pityriasis Rosea in a Patient with Epidermolysis Bullosa Dystrophica
Journal of Cutaneous Pathology, 1979A patient with clinical and histologic features of epidermolysis bullosa dystrophica‐recessive (EBD‐R) developed superimposed clinical lesions of pityriasis rosea (PR). Electron microscopy showed distinct “blebbing” of basal cells at the basement membrane zone in clinically normal skin of a non‐predilected area, as well as in scarred skin from a ...
C G, Mathias +4 more
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Surgical Correction of the Hand in Epidermolysis Bullosa Dystrophica
Hand, 1979Epidermolysis bullosa dystrophica (polydysplastic type) is a rare congenital skin anomaly which, in the hands, because they are exposed to repeated trauma, results in a severe “mitten”-like deformity. Functional benefit was obtained in three patients by separation of the digits and application of split-thickness grafts, Wolfe grafts or “split-off ...
M J, Gough, R E, Page
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Esophageal Epidermolysis Bullosa Dystrophica?
Annals of Internal Medicine, 1975Excerpt To the editor: The discussion of gastrointestinal manifestations in epidermolysis bullosa dystrophica (recessive) by Orlando and colleagues (Ann Intern Med81:203-206, 1974) was most informa...
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Epidermolysis Bullosa Dystrophica: Report of Two Cases
The Journal of the American Dental Association, 1972Oral conditions of patients with an advanced form of epidermolysis bullosa dystrophica, a rare disease of unknown cause, include poorly calcified teeth and hypoplastic enamel. Generally, the patients cannot use good oral hygiene techniques because of trauma to the gingival tissues.
E F, Howden, T R, Oldenburg
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A Study of the Linkage Relations of Epidermolysis bullosa dystrophica
Human Heredity, 1979Two large families from the Faroe Islands presenting epidermolysis bullosa of the dystrophic type were subjected to extensive linkage analyses with 22 serological markers. No significant evidence in support of linkage with any of these loci was provided.
H D, Joensen +4 more
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Squamous cell carcinoma in Epidermolysis bullosa dystrophica
Hand, 1975Abstract A case of Epidermolysis bullosa dystrophica (polydysplastic type) is described. Bilateral upper limb amputations were performed for squamous cell carcinomata and treatment of the pseudosyndactyly and malignant lesions is discussed.
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