Durable Disease Control With Nivolumab in Malignant Epithelioid Angiomyolipoma: A Case Report [PDF]
Introduction Epithelioid angiomyolipoma is a subtype of perivascular epithelioid cell tumors that may exhibit malignant behavior. While mammalian target of rapamycin inhibitors are commonly used for systemic treatment, the efficacy of immune checkpoint ...
Hiroki Shimoda +9 more
doaj +3 more sources
ASPSCR1: TFE3 FusionāPositive Epithelioid Angiomyolipoma/PEComa Lacking Melanocytic Markers: A Case Report [PDF]
Introduction Epithelioid angiomyolipoma is a rare perivascular epithelioid cell tumor subtype with malignant potential. Its morphology mimics renal cell carcinoma, posing diagnostic challenges.
Yuka Kondo +8 more
doaj +3 more sources
Renal necrotic epithelioid angiomyolipoma: A case report [PDF]
Epithelioid angiomyolipoma is a rare variant of angiomyolipoma, with necrosis being one of its unfavourable prognostic indicators. We report a 39-year-old woman with necrotic epithelioid angiomyolipoma of the left kidney.
Gede Wirya Kusuma Duarsa +6 more
doaj +2 more sources
Epithelioid angiomyolipoma of the kidney in an adult male with tuberous sclerosis [PDF]
Epithelioid angiomyolipoma is a rare variant of angiomyolipoma and a part of the microphthalmia transcription factor (MiTF) tumors. We report a case of epithelioid angiomyolipoma of the kidney that occurred in a 40-year-old male.
Nada Shaker, Douglas Wu, Anil Parwani
doaj +2 more sources
Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature review [PDF]
Hepatic epithelioid angiomyolipoma is a rare mesenchymal liver tumor within the perivascular epithelioid cell tumor family, known for its uncertain malignancy and potential for aggressive behavior.
Da Teng +3 more
doaj +2 more sources
Renal Epithelioid Angiomyolipoma: A Case Report. [PDF]
ABSTRACT Angiomyolipoma (AML) is a rare benign mesenchymal tumor, constituting less than 10% of renal masses, and occurs sporadically or in association with tuberous sclerosis complex (TSC). AML is generally categorized into classic AML and epithelioid angiomyolipoma (EAML), with the latter comprising approximately 4.6% of AML cases.
Mehramouz B +3 more
europepmc +2 more sources
Spontaneous rupture and hemorrhage of renal epithelioid angiomyolipoma misdiagnosed to renal carcinoma: a case report [PDF]
Background Renal epithelioid angiomyolipoma is a rare and unique subtype of classic angiomyolipoma, characterized by the presence of epithelioid cells.
Wenhao Zhang +5 more
doaj +2 more sources
Clinicopathological features and diagnostic challenges of hepatic epithelioid angiomyolipoma: a retrospective analysis of 27 cases [PDF]
BackgroundHepatic epithelioid angiomyolipoma, a rare mesenchymal tumor, poses significant diagnostic challenges due to its rarity and non-specific presentation.
Erming Cai +4 more
doaj +2 more sources
p53 aberration and TFE3 gene amplification may be predictors of adverse prognosis in epithelioid angiomyolipoma of the kidney [PDF]
Background Although epithelioid angiomyolipoma of the kidney has been studied by several groups, the reported prevalence of malignant behavior remains uncertain and there are not yet definitive predictive biomarkers.
Yanning Zhang +3 more
doaj +2 more sources
Renal Epithelioid Angiomyolipoma in Children [PDF]
Renal angiomyolipoma is a rare cause of renal tumor in children. Most are associated with tuberous sclerosis, and the classic type is observed more commonly.
Dhruv Mahajan +4 more
doaj +2 more sources

