Results 151 to 160 of about 4,675 (181)
Some of the next articles are maybe not open access.
Clinical Radiology, 2001
Erdheim-Chester disease (ECD) is a rare histiocytic infiltrative disease, characterized by long bone sclerosis. We describe two confirmed cases of ECD, both of which demonstrate non-malignant retroperitoneal and peri-renal infiltration causing dilatation of the upper renal tracts. The cases are illustrated with contrast studies, computed tomography (CT)
D, Murray +4 more
exaly +3 more sources
Erdheim-Chester disease (ECD) is a rare histiocytic infiltrative disease, characterized by long bone sclerosis. We describe two confirmed cases of ECD, both of which demonstrate non-malignant retroperitoneal and peri-renal infiltration causing dilatation of the upper renal tracts. The cases are illustrated with contrast studies, computed tomography (CT)
D, Murray +4 more
exaly +3 more sources
American Journal of Neuroradiology, 2023
Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis. The disease is widely variable in its severity, ranging from incidental findings in asymptomatic patients to a fatal multisystem illness. CNS involvement occurs in up to one-half of patients, most often leading to diabetes insipidus and cerebellar dysfunction.
J.C. Benson +7 more
+5 more sources
Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis. The disease is widely variable in its severity, ranging from incidental findings in asymptomatic patients to a fatal multisystem illness. CNS involvement occurs in up to one-half of patients, most often leading to diabetes insipidus and cerebellar dysfunction.
J.C. Benson +7 more
+5 more sources
Archives of Neurology, 2012
Erdheim-Chester disease is a rare systemic non-Langerhans cell histiocytosis requiring clinical, radiographic, and pathologic findings to confirmthediagnosis.Bonepain,the most common presenting symptom, occurs in 50% of cases, and there is near-universal symmetric sclerosis of the metaphyses and diaphyses of the long bones.
Eric M, Liotta +4 more
openaire +4 more sources
Erdheim-Chester disease is a rare systemic non-Langerhans cell histiocytosis requiring clinical, radiographic, and pathologic findings to confirmthediagnosis.Bonepain,the most common presenting symptom, occurs in 50% of cases, and there is near-universal symmetric sclerosis of the metaphyses and diaphyses of the long bones.
Eric M, Liotta +4 more
openaire +4 more sources
Mimics of Erdheim–Chester disease
British Journal of Haematology, 2021SummaryErdheim–Chester disease (ECD) is a rare histiocytic neoplasm with frequent multiorgan involvement. An accurate diagnosis of ECD requires the correlation of clinical features, histopathologic and radiologic findings. We describe a case series of patients with a referral diagnosis of ECD, whereby the diagnosis was changed to non‐histiocytic ...
Jithma P. Abeykoon +12 more
openaire +2 more sources
Diagnosing Erdheim–Chester disease
Annals of the Rheumatic Diseases, 2013Although we generally agree with Juanos-Iborra et al 1 who noted that some of the most common manifestations of Erdheim–Chester disease (ECD) at time of onset (such as skeletal, constitutional or even neurological symptoms) may lack adequate specificity for a timely and prompt diagnosis, it is conceivable that the same manifestations, if unexplained ...
Cavalli G +3 more
openaire +3 more sources
Erdheim–Chester disease in a child
Medical and Pediatric Oncology, 2003[No abstract available]
CLERICO, Anna +5 more
openaire +3 more sources
Systemic Erdheim–Chester disease
Virchows Archiv, 2008Erdheim-Chester disease is a rare xanthomatosis that may present with characteristic radiologic and histologic features. There have been conflicting reports regarding the nature of this process, including whether it represents a reactive or neoplastic lesion. We present the clinical histories, pathologic findings, and an analysis of clonality using the
Brendan Craig, Dickson +8 more
openaire +2 more sources
Clinical Orthopaedics and Related Research, 1984
In a 57-year-old woman dizziness, staggering, altered mental status, and bilateral pain and cramping in the lower extremities developed. Extensive investigation yielded evidence of renal and long-bone lesions, with the latter being primarily metaphyseal and diaphyseal. Needle biopsy of the tibial marrow revealed the presence of lipid-laden histiocytes,
G G, Poehling, D M, Adair, H A, Haupt
openaire +2 more sources
In a 57-year-old woman dizziness, staggering, altered mental status, and bilateral pain and cramping in the lower extremities developed. Extensive investigation yielded evidence of renal and long-bone lesions, with the latter being primarily metaphyseal and diaphyseal. Needle biopsy of the tibial marrow revealed the presence of lipid-laden histiocytes,
G G, Poehling, D M, Adair, H A, Haupt
openaire +2 more sources
Radiotherapy for Erdheim-Chester disease
International Journal of Clinical Oncology, 2007A 42-year-old woman suffered from pain in both legs, and fever. She was diagnosed with Erdheim-Chester disease (ECD), based upon bone biopsy. Initially, she received steroid therapy, which led to temporary improvement. However, bone pain in the right femur was so progressive that, as a trial course of radiation therapy, she was given a total dose of 18
Katsunori, Matsui +2 more
openaire +2 more sources
Imaging in Erdheim-Chester Disease
RadioGraphicsErdheim-Chester disease (ECD) is a rare, multisystemic, inflammatory, non-Langerhans cell histiocytic neoplasm. The discovery of recurrent and somatic mutations in the mitogen-activated protein kinase signaling pathway, most commonly BRAFV600E, has led to a reclassification of ECD from an inflammatory disorder to a neoplastic process.
Yashant Aswani +9 more
openaire +2 more sources