Results 211 to 220 of about 277,046 (301)

Elevated circulating cell-free mitochondrial DNA in fabry disease: insights into inflammatory activation. [PDF]

Front Immunol
Yuan Y, Zhang X, Zhao Y, Wang Y, Huang J, Wang Q, Song X, Deng J, Wang Z, Yuan Y, Zhang W.   +10 more
europepmc   +1 more source

The variability of giraffe skull morphology

Journal of Anatomy, EarlyView.
What does giraffe skull shape tell us about their development and evolution? Abstract Giraffe (Giraffa spp.) are among the most unique and charismatic extant animals, largely due to their distinct morphology. The evolutionary and developmental origin of ossicones is a key factor in giraffid biology, yet other features building their characteristic head
Nikolaos Kargopoulos, Jesús Marugán‐Lobón, Anusuya Chinsamy‐Turan, Bernard R. Agwanda, Michael Butler Brown, Stephanie Fennessy, Sara Ferguson, Rigardt Hoffman, Fredrick Lala, Arthur Muneza, Ogeto Mwebi, Moses Otiende, Alice Petzold, Sven Winter, Abdoul Razack Moussa Zabeirou, Julian Fennessy   +15 more
wiley   +1 more source

Clinical outcomes of exclusive enzyme therapy (laronidase) in a cohort of patients with mucopolysaccharidosis type I. [PDF]

Orphanet J Rare Dis
Guffon N, Pettazzoni M, Pangaud N, Reynes N, Le Peillet Feuillet E, Journeau P, Fouilhoux A.   +6 more
europepmc   +1 more source

The Interactive Impact of Regulation, Entrepreneurship, and Cultural Values on Technology Adoption: Renewable Energy in the EU

Journal of Management Studies, EarlyView.
Abstract How can diverse sources legitimize new technology when it lacks economic parity? Government policies that endorse nascent technologies play a central role through regulatory legitimation. Yet, we know less about whether inducement policies that incentivize adoption or imposition policies that mandate it are more effective, and how that ...
Raquel Antolín‐López, Jeffrey G. York, Theodore L. Waldron, Javier Martínez‐del‐Rio   +3 more
wiley   +1 more source

First multicenter real-world analysis of switching to next-generation enzyme replacement therapies in late-onset Pompe disease. [PDF]

J Neurol
Mendelsohn DH, Rosenbohm A, Güttsches AK, Kornblum C, Knop KC, Fangerau T, Nguyen-Younossi N, Shahyrova G, Garcia-Angarita N, Schoser B, Wenninger S.   +10 more
europepmc   +1 more source

Long-Term Enzyme Replacement Therapy and Renal Outcomes in Fabry Disease: A Systematic Review and Meta-Analysis. [PDF]

Biomedicines
Chen CY, Li CT, Lin CJ, Shih HM, Liu SJ, Sun FJ, Wu CJ.   +6 more
europepmc   +1 more source

“I Paid A Bribe”—Lessons and Insights From Crowdsourced Corruption Reporting in India

Regulation &Governance, EarlyView.
ABSTRACT Preventing and reducing corruption has proven to be an enormous challenge. An important step in this process is to produce and use good metrics to identify where anti‐corruption resources would be most beneficial. Most measures of corruption, however, rely on surveys of perceptions or bribery incidence.
Ina Kubbe, Bonnie J. Palifka, Lasse Buschmann Alsbirk   +2 more
wiley   +1 more source

Long-term safety outcomes and patient preferences for home-based intravenous enzyme replacement therapy (ERT) in Pompe disease and Mucopolysaccharidosis Type I (MPS-I): final results of two-year observation. [PDF]

Orphanet J Rare Dis
Toscano A, Musumeci O, Sacchini M, Ravaglia S, Siciliano G, Fiumara A, Verrecchia E, Fischetto R, Crescimanno G, Taurisano R, Sechi A, Gasperini S, Cianci V, Maggi L, Brighina F, Barone R, Cianflone A, Balzarini M, Parini R, Scarpa M.   +19 more
europepmc   +1 more source

Contestation and Compromise in Shaping the European Union's Corporate Sustainability due Diligence Directive: Implications for Global Value Chain Governance

Regulation &Governance, EarlyView.
ABSTRACT This paper explores the European Union's Corporate Sustainability Due Diligence Directive (CS3D) in the context of ongoing debates on private and public governance of global value chains (GVCs). Conceptually, it draws on neo‐Gramscian perspectives to analyze how contestation and compromise between distinct stakeholders and dynamics of hegemony
Louise Curran, Matthew Alford, Khalid Nadvi   +2 more
wiley   +1 more source

Clinical Practice of Multidisciplinary Team-Guided Comprehensive Management for Pediatric Patients with Fabry Disease: A Single-Center Case Series. [PDF]

J Multidiscip Healthc
Liu Y, Liu X, Yang M, Wang Q, Xu W, Zeng J, Han T, Mao H, Qian S.   +8 more
europepmc   +1 more source