Results 81 to 90 of about 275,755 (180)

Enzyme Replacement Therapy With Elosulfase Alfa Decreases Storage of Glycosaminoglycan in White Blood Cells of Patients With Morquio A Syndrome

Journal of Inborn Errors of Metabolism and Screening, 2015
Mucopolysaccharidosis IVA (MPS IVA; Morquio A syndrome) is a lysosomal storage disorder caused by a deficient N-acetylgalactosamine-6-sulfate sulfatase activity, leading to cellular storage of undegraded keratan sulfate.
Guilherme Baldo PhD, Fabiano Poswar MD, Andressa Federhen MSc, Camila Bittar MD, Rejane Gus PhD, Fernanda Bender MSc, Roberto Giugliani MD, PhD   +6 more
doaj   +1 more source

Vestibular and auditory deficits in Fabry disease and their response to enzyme replacement therapy [PDF]

, 2018
Progressive hearing (pHL) and vestibular (pVL) loss are frequent deficits in Fabry disease (FD). Recently, enzyme replacement therapy (ERT) with human α-galactosidase A has become available.
Hegemann, S., Palla, A., Straumann, D., Widmer, U.   +3 more
core  

ERTS [PDF]

Nature, 1973
openaire   +2 more sources

Kefahaman dan Keyakinan Guru-Guru Ekonomi Rumahtangga di Negeri Selangor dalam Penilaian Berformat Baru [PDF]

, 2001
Tujuan kajian ini ialah untuk meninjau kefahaman dan keyakinan guruguru Ekonomi Rumahtangga (ERT) dalam melaksanakan Penilaian Serformat Baru (PBS). Responden kajian terdiri dari 58 orang guru ERT di Selangor.
Zakaria, Anis
core  

Antibodies to recombinant human alpha-L-iduronidase prevent disease correction in cortical bone in MPS I mice

Molecular Therapy: Methods & Clinical Development
Mucopolysaccharidosis I (MPS I) is a lysosomal storage disorder caused by deficiency of the enzyme α-l-iduronidase (IDUA). Failure of enzyme replacement therapy (ERT) to treat skeletal disease may be due to development of anti-IDUA antibodies, found ...
Sarah C. Hurt, Steven Q. Le, Shih-hsin Kan, Quang D. Bui, Michael D. Brodt, Patricia I. Dickson   +5 more
doaj   +1 more source

ERTS [PDF]

Nature, 1974
openaire   +1 more source

Warped Discrete Cosine Transform-Based Low Bit-Rate Block Coding Using Image Downsampling

EURASIP Journal on Advances in Signal Processing, 2007
This paper presents warped discrete cosine transform (WDCT)-based low bit-rate block coding using image downsampling. While WDCT aims to improve the performance of conventional DCT by frequency warping, the WDCT has only been applicable to high bit-rate
Ertürk Sarp
doaj  

HA/HSA co-modified erlotinib–albumin nanoparticles for lung cancer treatment

Drug Design, Development and Therapy, 2018
Yuzhou Shen, Wentao Li Department of Thoracic Surgery, Shanghai Chest Hospital, Shanghai Jiao Tong University, Shanghai 200030, China Background: Aim of this study was to prepare the hyaluronic acid and human serum albumin modified erlotinib ...
Shen Y, Li W
doaj  

Comparing the efficacy of cipaglucosidase alfa plus miglustat with alglucosidase alfa for late-onset Pompe disease: an expanded network meta-analysis utilizing patient-level and aggregate data. [PDF]

J Comp Eff Res
Fu S, Hummel N, Shohet S, Johnson N, MacCulloch A, Castelli J, Kerr W, Fox B, Gielen V.   +8 more
europepmc   +1 more source

Dubious Dualism: The Reception of International Law in Canada [PDF]

, 2010
van Ert, Gib
core   +1 more source