Results 101 to 110 of about 1,027,919 (286)
Brasil e Portugal - Afinidades eletiva no trato da política e da cultura [PDF]
Este trabajo trata de las afinidades que han existido entre Portugal y Brasil en la primera mitad del siglo XX, cuando al amparo del Estado Novo instalado en ambos países, por Antonio de Oliveira Salazar y Getúlio Vargas, respectivamente, se crearon ...
Castilho Costa, Maria Cristina
core +1 more source
SPG4 and Dementia: Expanding the Clinical Spectrum
ABSTRACT Objective Hereditary spastic paraplegia (HSP) is a group of disorders characterized by progressive spasticity and lower limb weakness, with mutations in SPG4/SPAST being the most common cause. Detailed studies and clinical and molecular comparisons across different populations are missing.
Emanuele Panza +19 more
wiley +1 more source
RNA Sequencing Resolves Cryptic Pathogenic Variants in Mitochondrial Disease
ABSTRACT Objective Mitochondrial diseases are the most common inherited metabolic disorders, characterized by pronounced clinical and genetic heterogeneity that complicates molecular diagnosis. Although DNA‐based sequencing approaches have become standard in genetic testing, up to half of patients remain without a definitive diagnosis.
Zhimei Liu +21 more
wiley +1 more source
Quando o assunto é o “Estado Novo” e envolve o mundo do trabalho, a tradição historiográfica se pauta, em geral, pelo que Mikhail Bakhtin denominou “hábitos monológicos”. Tudo parece se passar como se fosse possível apagar os sinais que nos levariam a captar vozes destoantes do grande coro da suposta unanimidade nacional orquestrada pelo regime.
openaire +1 more source
A Systematic Comparison of Alpha‐Synuclein Seed Amplification Assays for Increasing Reproducibility
ABSTRACT Seed amplification assays (SAAs) enable ultrasensitive detection of misfolded α‐synuclein across biofluids and tissues. Yet, heterogeneity in protocols limits cross‐study comparability and clinical translation. Here, we review α‐synuclein SAA methods and their performance across various biological matrices.
Manuela Amaral‐do‐Nascimento +3 more
wiley +1 more source
O movimento sindical durante o Estado Novo : estado actual da investigação [PDF]
In this article, that establishes the ‘state of the art’ of syndicalism during Portugal’s New State, through the analysis of the sustaining principles of the corporative system, the author attempts to demonstrate how the national trade unions, as ...
Helder Miguel Marques
core
Modernidade, Cultura e Poder: Aspectos da cidade do Recife durante o Estado Novo
O Golpe de 1937 levou Agamenon Magalhães à interventoria do estado de Pernambuco. A política cultural empregada por Agamenon permitiu que a modernidade consagrasse seus moldes autoritários. Nosso objetivo é analisar a relação entre as práticas cotidianas
Paulo Raphael Feldhues
doaj
«Es necesario que nosotros, intelectuales, nos apoderemos de Brasil». Redes de intelectuales de derechas durante el Estado Novo brasileño (1937-1945) [PDF]
A través del estudio de las redes de intelectuales durante el Estado Novo brasileño, buscamos comprender, de forma sintética y desde un enfoque novedoso, las relaciones en que se vieron inmersos los intelectuales de derechas y la manera en la que ...
Gabriela de Lima Grecco
doaj
ABSTRACT Background X‐linked adrenoleukodystrophy (X‐ALD) is a neurometabolic disorder caused by pathogenic variants in ABCD1, leading to slowly progressive spinal cord disease in nearly all affected men. Sensitive biomarkers to quantify disease severity and predict progression are needed for clinical care and trial design.
Eda G. Kabak +4 more
wiley +1 more source
Il corporativismo nell’Estado Novo. Dalla promulgazione della Rerum Novarum al primo dopoguerra
Daniele Serapiglia
doaj +1 more source

