Results 11 to 20 of about 134,196 (290)
Journal of Cardiovascular Ultrasound, 2013 Fabry disease is a progressive X-linked disorder of glycosphingolipid metabolism caused by a deficiency of the α-galactosidase lysosomal enzyme. The partial or complete deficiency of the lysosomal enzyme leads to an accumulation of neutral glycosphingolipids in the vascular endothelium and visceral tissues throughout the body.
Yoon, Jae Yong +9 more
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Long-time optical transmittance measurements of silica nanofibers [PDF]
EPJ Web of Conferences, 2020 We perform long-time measurements of the optical silica transmittance during several months in different environments and with different nanofiber lengths.
Bouhadida Maha, Lebrun Sylvie
doaj +1 more source
Journal of the European Optical Society-Rapid Publications, 2023 Line-field Confocal Optical Coherence Tomography (LC-OCT) is an imaging modality based on a combination of time-domain optical coherence tomography and reflectance confocal microscopy.
Waszczuk Léna +3 more
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Orphanet Journal of Rare Diseases, 2010 Fabry disease (FD) is a progressive, X-linked inherited disorder of glycosphingolipid metabolism due to deficient or absent lysosomal α-galactosidase A activity. FD is pan-ethnic and the reported annual incidence of 1 in 100,000 may underestimate the true prevalence of the disease. Classically affected hemizygous males, with no residual α-galactosidase
openaire +3 more sources
Backaction in metasurface etalons [PDF]
, 2016 We consider the response of etalons created by a combination of a conventional mirror and a metasurface, composed of a periodic lattice of metal scatterers with a resonant response.
A. Femius Koenderink +5 more
core +11 more sources
Power scaling of LED-pumped alexandrite: The road to high gain multipass amplifiers [PDF]
EPJ Web of ConferencesOur experiment demonstrates that LED-pumping through luminescent concentrator enables sufficient pump power for viable alexandrite amplifier gain. In 10 passes we obtain a gain of 19 with 10 W output power, for 50 µs pulses at 20 Hz and 760 nm.
Thellier Elio +6 more
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Light Extraction and Brightness Enhancement of Luminescent Rectangular Slabs
Advanced Photonics Research, 2022 The extraction efficiency and the brightness are critical parameters to increase the performance of luminescent rectangular slabs such as scintillators, luminescent concentrators, or diamonds with NV centers.
Pierre Pichon +6 more
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Ultrahigh finesse Fabry-Perot superconducting resonator [PDF]
, 2007 We have built a microwave Fabry-Perot resonator made of diamond-machined copper mirrors coated with superconducting niobium. Its damping time (Tc = 130 ms at 51 GHz and 0.8 K) corresponds to a finesse of 4.6 x 109, the highest ever reached for a ...
Bernu, Julien +12 more
core +4 more sources
Romanian Journal of Neurology, 2018 Fabry disease is a rare genetic disease involving a deficiency of an enzyme. A decrease in the enzyme activity leads to a selective suffering of specific anatomic and functional structures resulting in heteromorphic clinical signs that increase the difficulty of early diagnosis.
Ioana Simina Barac +4 more
openaire +2 more sources
Electrical generation of visible surface plasmon polaritons by a nanopillars antenna array
APL Photonics, 2021 Electrical excitation of surface plasmon polaritons by inelastic tunneling electrons has been put forward as a potential nanosource that can be used in a variety of on-chip optoelectronic applications.
Cheng Zhang +4 more
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