Results 101 to 110 of about 82,602 (277)

Impact of ER stress and the unfolded protein response on Fabry disease

EBioMedicine
Summary: Fabry disease (FD) is a lysosomal storage disorder caused by pathogenic missense and nonsense variants in the α-galactosidase A (GLA) gene, leading to absent or reduced enzyme activity.
Malte Lenders, Elisa Rudolph, Eva Brand
doaj   +1 more source

Ultra-narrow (sub-MHz) linewidth emission from discrete mode laser diodes [PDF]

, 2007
A class of laser which exhibits ultra-narrow sub MHz linewidth emission necessary for numerous applications in optical communications and sensors is described.
Kelly, Brian, J. O'Gorman, O'Gorman, J., Besnard, P., Jones, D., Besnard, Pascal, D. Jones, Guignard, Celine, Barry, Liam P., P. Besnard, C. Guignard, J. Patchell, L. P. Barry, B. Kelly, Patchell, J., O'Gorman, James   +15 more
core   +1 more source

Inherited metabolic epilepsies–established diseases, new approaches

Epilepsia Open, EarlyView.
Abstract Inherited metabolic epilepsies (IMEs) represent the inherited metabolic disorders (IMDs) in which epilepsy is a prevailing component, often determining other neurodevelopmental outcomes associated with the disorder. The different metabolic pathways affected by individual IMEs are the basis of their rarity and heterogeneity.
Itay Tokatly Latzer, Phillip L. Pearl
wiley   +1 more source

Energy-resolved transport of ultracold atoms across the Anderson transition: theory and experiment

New Journal of Physics
In a recent experiment (Yu et al 2026 arXiv: https://arxiv.org/abs/2602.07654 ), energy-resolved measurements of an atomic matter wave spreading in a speckle potential enabled the direct observation of the three-dimensional Anderson transition.
Jean-Philippe Banon, Sacha Barré, Ke Xie, Hoa Mai Quach, Xudong Yu, Yukun Guo, Myneni Niranjan, Alain Aspect, Vincent Josse, Nicolas Cherroret   +9 more
doaj   +1 more source

Fluorene‐based blue emitters: On the path to electrically pumped organic lasers

FlexMat, EarlyView.
Electrically pumped efficient operation remains unrealized, a major challenge in optoelectronics. Fluorene‐based blue‐emitting semiconductors are promising gain media, thanks to their structural tunability and favorable emission properties. This review summarizes recent advances, highlights their reliability and versatility in lasing, and outlines key ...
Yong Yan, Hao Li, Mengna Yu, Huiyin Wang, Jiangqiang He, Menghan Wu, Quanyou Feng, Linghai Xie   +7 more
wiley   +1 more source

Recent progress and challenges in top‐emitting quantum dot light‐emitting diodes

FlexMat, EarlyView.
This review summarizes recent advances in top‐emitting quantum‐dot light‐emitting diodes (TE‐QLEDs), including device architectures, microcavity engineering, angular‐emission management, and operational stability, highlighting optical–electrical–thermal co‐optimization as the key pathway toward reliable, high‐performance TE‐QLEDs. Abstract Top‐emitting
Chengyi Chen, Yuqi Liang, Mian Wei, Qiulei Xu, Huimin Zhang, Zhenghui Wu, Huaibin Shen   +6 more
wiley   +1 more source

One Hundred Years of the German Soil Science Society (DBG) 1926–2026: Origins, Facts, and Background of an Eventful History

Journal of Plant Nutrition and Soil Science, EarlyView.
ABSTRACT On its 100th anniversary in 2026, the German Soil Science Society (DBG) is looking back not only on an eventful history with traditions and impressive achievements but also with painful interruptions and ruptures. One curious fact is that the DBG was initially founded as the national section of the International Soil Science Society (ISSS ...
Karl‐Heinz Feger
wiley   +1 more source

Economic approaches to measuring labor exploitation in agriculture: A systematic literature review of indicators and methodologies

Journal of the Science of Food and Agriculture, EarlyView.
Abstract Agriculture remains highly vulnerable to labor exploitation, affecting almost two million workers worldwide and drawing increasing attention, particularly within the framework of Sustainable Development Goal 8 of the United Nations 2030 Agenda. However, the informal nature of exploitation and fragmented data complicate its analysis.
Claudio Mirabella, Emanuele Schimmenti, Antonino Galati, Valeria Borsellino   +3 more
wiley   +1 more source

Heart failure in two male patients with late‐onset Fabry mutation (IVS4 + 919G > A)

ESC Heart Failure, Volume 12, Issue 2, Page 1508-1513, April 2025.
Xufei Yang, Chunlan Deng, Xiaogang Guo, Hui Yan   +3 more
wiley   +1 more source

Resonant States Reveal Strong Light–Matter Coupling in Nanophotonic Cavities

Laser &Photonics Reviews, EarlyView.
Photonic resonant states reveal characteristics of coupled light–matter systems that would otherwise be hidden by damping. Their trajectories (when tuning the optical resonance) undergo a qualitative change at the onset of strong coupling: They start swapping positions.
Jan David Fischbach, Sergei Gladyshev, Adrià Canós Valero, Markus Nyman, Thomas Weiss, Carsten Rockstuhl   +5 more
wiley   +1 more source