This Highlight summarizes a recent review on reversible metal electrodeposition (RMED) for dynamic spectral modulation. RMED systems enable adaptive thermal management by regulating solar irradiation and mid‐infrared thermal emission and are evolving from single‐band optical modulation toward multispectral platforms that synergistically control solar ...
Qizhang Li, Po‐Chun Hsu
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Revisiting Inherited Metabolic Diseases (IMDs) Through the Lens of Selective Autophagy
ABSTRACT Selective autophagy is increasingly recognized as a fundamental quality‐control mechanism that complements bulk autophagy by enabling the targeted degradation of specific intracellular cargos, including mitochondria, endoplasmic reticulum (ER), lipid droplets, glycogen, peroxisomes, ferritin, ribosomes, and protein aggregates.
Marianna Maddaluno +3 more
wiley +1 more source
A puzzling case of left ventricular hypertrophy in an elderly man. [PDF]
Ching S, Chan K.
europepmc +1 more source
ABSTRACT Fabry disease is a rare, progressive, X‐linked disease resulting from α‐galactosidase A enzyme deficiency due to GLA gene variants. Current treatments include intravenous enzyme replacement therapy (ERT) and the oral pharmacologic chaperone migalastat.
Peter Nordbeck +5 more
wiley +1 more source
AI-assisted longitudinal cardiac phenotyping identifies domain-specific remodeling patterns in Fabry cardiomyopathy. [PDF]
Sung KT +8 more
europepmc +1 more source
Raised Amylase as a Potential Marker of Vascular Dysfunction and Inflammation in Fabry Disease
ABSTRACT Fabry disease (FD) is a X‐linked disorder caused by deficiency of alpha‐galactosidase A (AGAL), leading to progressive accumulation of globotriaosylceramide (Gb3) and globotriaosylsphingosine (lyso‐Gb3). While renal, cardiac and cerebrovascular complications are well described, pancreatic involvement remains poorly characterised.
Simona D'Amore +2 more
wiley +1 more source
Generation of two induced pluripotent stem cell lines from Fabry disease patients carrying GLA mutations. [PDF]
Patra D +6 more
europepmc +1 more source
A Nearly Perfect Implementation of a Broadband Optical Null Media via Space‐Folding
A space‐folding optical null medium with impedance‐matching layers enables broadband directional wave projection and wavefront engineering. By tailoring the folding ratio and dilution ratio, the structure maintains near‐unity transmittance over 5–9 GHz.
Yichao Liu, Jiale Li, Fei Sun, Qin Liao
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Clinical and Biochemical Improvement After Switching From Agalsidase Alfa to Beta in a Boy With Classic Fabry Disease: A Case Report. [PDF]
Koga N +7 more
europepmc +1 more source
Integration of Refractive Microlenses on BP/MoS2 Photodiodes for Enhanced Infrared Photodetection
This study demonstrates the successful integration of black phosphorus/molybdenum disulfide infrared photodetectors with refractive microlenses to significantly enhance detection. The design achieves a 20‐fold photocurrent enhancement, enabling a room‐temperature detectivity of 1.83 × 109 cmHz1/2W−1, and demonstrates high‐resolution (1023 × 768) single‐
Varsha Ashwin Vedaraj +11 more
wiley +1 more source

