Familial primary pulmonary hypertension

Annals of Internal Medicine, 1966
Excerpt Primary pulmonary hypertension is a disease characterized by increased arterial pressure in the pulmonary circulation caused by changes which appear to be intrinsic to the pulmonary vascula...
J D, Rogge, M E, Mishkin, P D, Genovese
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Familial Pulmonary Capillary Hemangiomatosis Resulting in Primary Pulmonary Hypertension

Annals of Internal Medicine, 1988
We describe the first cases of familial pulmonary capillary hemangiomatosis, a disorder in which capillaries in the lungs proliferate. Three siblings died from primary pulmonary hypertension. One developed pulmonary congestion preterminally after vasodilator treatment. The inheritance pattern seems autosomal recessive.
D, Langleben +7 more
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Familial Primary Pulmonary Hypertension

Chest, 1994
Often, insights into a disease are gained by studying the exceptional cases, the outliers. For the population with primary pulmonary hypertension (PPH), it is the patients with the familial or hereditary form that are the outliers, representing only 6 percent of the recent NHLBI PPH Registry population.
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FAMILIAL PRIMARY PULMONARY HYPERTENSION AND ASSOCIATED OCULAR FINDINGS

Retina, 2001
Familial primary pulmonary hypertension (PPH) is a rare, fatal, autosomal dominant disease that results in right heart failure from idiopathic obliteration of the pulmonary arteries. Patients develop stagnation of venous blood flow and elevated venous pressure.The authors retrospectively reviewed the clinical records of three patients diagnosed with ...
Saran BR +3 more
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hypertension, pulmonary
humans
female

male
adult
3. good health

middle aged
pedigree
electrocardiography