Results 101 to 110 of about 701,910 (259)

Reduced Muscular Carnosine in Proximal Myotonic Myopathy—A Pilot 1H‐MRS Study

open access: yesAnnals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Myotonic dystrophy type 2 (proximal myotonic myopathy, PROMM) is a progressive multisystem disorder with muscular symptoms (proximal weakness, pain, myotonia) and systemic manifestations such as diabetes mellitus, cataracts, and cardiac arrhythmias.
Alexander Gussew   +11 more
wiley   +1 more source

Influência da Variabilidade Climática sobre a Erosividade em Belém (PA)

open access: yesRevista Brasileira de Meteorologia
Resumo A Universal Soil Loss Equation (USLE) é um modelo no qual a perda de solo é o produto de vários índices, entre eles o de erosividade da chuva (R). Este fator identifica quando ocorre o maior risco de erosão hídrica.
Carlos Eduardo Aguiar de Souza Costa   +1 more
doaj   +1 more source

Potencial erosivo e índice de anomalias de chuvas no polo de produção de grãos de Paragominas, Pará. [PDF]

open access: yes, 2014
A erosão hídrica tem causado perdas nas camadas superficiais do solo e promovido sérios danos ambientais, econômicos e sociais em sistemas de cultivos agrícolas convencionais no Brasil.
COSTA, D. C.   +2 more
core  

Whole‐Body Pattern of Muscle Degeneration and Progression in Sarcoglycanopathies

open access: yesAnnals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective To characterize whole‐body intramuscular fat distribution pattern in patients with sarcoglycanopathies and explore correlations with disease severity, duration and age at onset. Methods Retrospective, cross‐sectional, multicentric study enrolling patients with variants in one of the four sarcoglycan genes who underwent whole‐body ...
Laura Costa‐Comellas   +39 more
wiley   +1 more source

Clinically Relevant Outcome Measures in Women With Adrenoleukodystrophy

open access: yesAnnals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Adrenoleukodystrophy is a rare inherited peroxisomal disease caused by pathogenic variants in the ABCD1 gene located on the X chromosome. Although the most severe central nervous system and adrenal complications typically affect only men with adrenoleukodystrophy, the majority of women develop myeloneuropathy symptoms in adulthood.
Chenwei Yan   +3 more
wiley   +1 more source

Desenvolvimento e validação de uma escala de afetos positivos e negativos

open access: yesPsico-USF, 2013
O objetivo deste estudo foi construir e buscar evidências de validade para uma escala de afetos positivos e negativos (EA). Participaram 853 universitários do sul do Brasil (57% mulheres) com idade média de 21 anos (DP=3).
Cristian Zanon   +3 more
doaj  

Aspectos e fatores da produtividade em pesquisa, desenvolvimento e inovação Aspects and factors for productivity in R&D&I

open access: yesQuímica Nova, 2005
Comparison of national budgets for R&D is often made but it should consider the relative productivity and their factors. In Brazil, inefficiency factors as well as their causes have been diagnosed since the late 60's and solutions have been proposed within various governmental organisms, from CNPq to the strategy think tanks.
openaire   +1 more source

Adipokines and Associations With Incident Osteoporotic Fracture in Patients With Rheumatoid Arthritis

open access: yesArthritis Care &Research, EarlyView.
Objective We assessed whether circulating adipokines are associated with incident fractures in patients with rheumatoid arthritis (RA). Methods Three adipokines (adiponectin, leptin, and fibroblast growth factor [FGF]‐21) were measured using banked enrollment serum from participants in a longitudinal RA cohort.
Joshua F. Baker   +9 more
wiley   +1 more source

Validação brasileira do alcohol craving questionnaire – Short form revised (ACQ-SFR)

open access: yesClinical and Biomedical Research, 2019
Introdução: A avaliação do craving é importante para o tratamento de pacientes com Transtornos por uso de substâncias psicoativas. O objetivo deste estudo foi realizar a validação do Alcohol Craving Questionnaire-Short Form Revised- Versão Brasileira ...
Tharlise Paim Girelli   +5 more
doaj  

Perfil dos pacientes submetidos à angioplastia trasluminal coronariana com stents farmacológicos no Instituto de Cardiologia de Santa Catarina. [PDF]

open access: yes, 2007
Trabalho de Conclusão de Curso - Universidade Federal de Santa Catarina. Curso de Medicina.
Aquino, Vivian Wuerges de
core  

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