Results 101 to 110 of about 1,726,170 (370)
The effect of disorder on the fracture nucleation process
, 2001 The statistical properties of failure are studied in a fiber bundle model with thermal noise. We show that the macroscopic failure is produced by a thermal activation of microcracks.
A. Guarino +22 more
core +1 more source
The Diverse Neuromuscular Spectrum of VPS13A Disease
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective VPS13A disease (chorea‐acanthocytosis) is a rare neurodegenerative disorder caused by biallelic variants in VPS13A, typically presenting with hyperkinetic movement disorders, while neuromuscular signs are often mild. The aim of the project was to investigate the frequency and severity of neuromuscular impairment in VPS13A disease ...
Anne Buchberger +16 more
wiley +1 more source
Dynamic model of fiber bundles [PDF]
Europhysics Letters (EPL), 2004 A realistic continuous-time dynamics for fiber bundles is introduced and studied both analytically and numerically. The equation of motion reproduces known stationary-state results in the deterministic limit while the system under non-vanishing stress always breaks down in the presence of noise.
M. Y. Choi +3 more
openaire +4 more sources
INF2‐Related Charcot–Marie–Tooth Disease in a Japanese Cohort: Genetic and Clinical Insights
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Background INF2 mutations cause focal segmental glomerulosclerosis (FSGS) and Charcot–Marie–Tooth disease (CMT). Accurate genetic diagnosis is critical, as INF2‐related FSGS is typically resistant to immunotherapy yet rarely recurs after transplantation, and its associated neuropathy can mimic treatable immune‐mediated disorders such as ...
Chikashi Yano +27 more
wiley +1 more source
Theory Research of Curved Surface Reflection RIM-FOS under the Typical Optical Fiber Beam Structure
Chemical Engineering Transactions, 2016 This paper has completed the theoretical modeling of the cured surface reflection RIM-FOS under the typical optical fiber bundle structure. Firstly, the modeling of the fiber’s axial symmetry distribution structure is made by analytical method to get the
H. Hua, L.Q. Zhong
doaj +1 more source
Connections on the path bundle of a principal fiber bundle
Differential Geometry and its Applications, 1994 zbMATH Open Web Interface contents unavailable due to conflicting licenses.
openaire +3 more sources
The Whyburn construction and fiber bundles
General Topology and its Applications, 1977 Abstract Whyburn's unifying constructions is shown to be a function from one category of bundles over locally compact base spaces to another category of bundles over the same base spaces. This functor one-point compactifiles the fiber, commutes with the pullback functor and takes trivial bundles to trivial bundles.
Stephen Kuhn, Victor Schneider
openaire +2 more sources
SNUPN‐Related Muscular Dystrophy: Novel Phenotypic, Pathological and Functional Protein Insights
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective SNUPN‐related muscular dystrophy or LGMDR29 is a new entity that covers from a congenital or childhood onset pure muscular dystrophy to more complex phenotypes combining neurodevelopmental features, cataracts, or spinocerebellar ataxia. So far, 12 different variants have been described.
Nuria Muelas +18 more
wiley +1 more source
Retinal nerve fiber bundle tracing and analysis in human eye by polarization sensitive OCT.
Biomedical Optics Express, 2015 We present a new semi-automatic processing method for retinal nerve fiber bundle tracing based on polarization sensitive optical coherence tomography (PS-OCT) data sets.
Mitsuro Sugita +9 more
semanticscholar +1 more source
Diffusion Tractography Biomarker for Epilepsy Severity in Children With Drug‐Resistant Epilepsy
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective To develop a novel deep‐learning model of clinical DWI tractography that can accurately predict the general assessment of epilepsy severity (GASE) in pediatric drug‐resistant epilepsy (DRE) and test if it can screen diverse neurocognitive impairments identified through neuropsychological assessments.
Jeong‐Won Jeong +7 more
wiley +1 more source