Results 81 to 90 of about 1,744,424 (375)
Local load-sharing fiber bundle model in higher dimensions. [PDF]
We consider the local load-sharing fiber bundle model in one to five dimensions. Depending on the breaking threshold distribution of the fibers, there is a transition where the fracture process becomes localized. In the localized phase, the model behaves
S. Sinha +2 more
semanticscholar +1 more source
The Diverse Neuromuscular Spectrum of VPS13A Disease
ABSTRACT Objective VPS13A disease (chorea‐acanthocytosis) is a rare neurodegenerative disorder caused by biallelic variants in VPS13A, typically presenting with hyperkinetic movement disorders, while neuromuscular signs are often mild. The aim of the project was to investigate the frequency and severity of neuromuscular impairment in VPS13A disease ...
Anne Buchberger +16 more
wiley +1 more source
The effect of disorder on the fracture nucleation process
The statistical properties of failure are studied in a fiber bundle model with thermal noise. We show that the macroscopic failure is produced by a thermal activation of microcracks.
A. Guarino +22 more
core +1 more source
Fiber bundle model with highly disordered breaking thresholds. [PDF]
We present a study of the fiber bundle model using equal load-sharing dynamics where the breaking thresholds of the fibers are drawn randomly from a power-law distribution of the form p(b)∼b-1 in the range 10-β to 10β.
C. Roy, S. Kundu, S. S. Manna
semanticscholar +1 more source
INF2‐Related Charcot–Marie–Tooth Disease in a Japanese Cohort: Genetic and Clinical Insights
ABSTRACT Background INF2 mutations cause focal segmental glomerulosclerosis (FSGS) and Charcot–Marie–Tooth disease (CMT). Accurate genetic diagnosis is critical, as INF2‐related FSGS is typically resistant to immunotherapy yet rarely recurs after transplantation, and its associated neuropathy can mimic treatable immune‐mediated disorders such as ...
Chikashi Yano +27 more
wiley +1 more source
SNUPN‐Related Muscular Dystrophy: Novel Phenotypic, Pathological and Functional Protein Insights
ABSTRACT Objective SNUPN‐related muscular dystrophy or LGMDR29 is a new entity that covers from a congenital or childhood onset pure muscular dystrophy to more complex phenotypes combining neurodevelopmental features, cataracts, or spinocerebellar ataxia. So far, 12 different variants have been described.
Nuria Muelas +18 more
wiley +1 more source
Streamline tractography locally traces peak directions extracted from fiber orientation distribution (FOD) functions, lacking global information about the trend of the whole fiber bundle. Therefore, it is prone to producing erroneous tracks while missing
Yuanjing Feng +6 more
doaj +1 more source
Reconstruction and dissection of the entire human visual pathway using diffusion tensor MRI
The human visual system comprises elongated fiber pathways that represent a serious challenge for diffusion tensor imaging (DTI) and fiber tractography: while tracking of frontal fiber bundles may be compromised by the nearby presence of air-filled ...
Sabine Hofer +2 more
doaj +1 more source
Diffusion Tractography Biomarker for Epilepsy Severity in Children With Drug‐Resistant Epilepsy
ABSTRACT Objective To develop a novel deep‐learning model of clinical DWI tractography that can accurately predict the general assessment of epilepsy severity (GASE) in pediatric drug‐resistant epilepsy (DRE) and test if it can screen diverse neurocognitive impairments identified through neuropsychological assessments.
Jeong‐Won Jeong +7 more
wiley +1 more source
An accurate fracture estimation of carbon fiber reinforced plastic (CFRP) is indispensable for adequate design with reliability and economization of high pressure hydrogen tank made by filament winding (FW) method for automobile.
Shinichiro TAKEMOTO, Nobuhiro YOSHIKAWA
doaj +1 more source

