Results 11 to 20 of about 12,028 (243)
IntroductionFibrous dysplasia is a benign fibrous bone tumor that accounts for 5% to 10% of benign bone tumors. It can manifest as simple fibrous dysplasia (70%–80%), polyostotic fibrous dysplasia (20%–30%), with approximately the same incidence in men ...
Qifan Yang +4 more
doaj +2 more sources
Fibrous Dysplasia Meets Intramuscular Myxoma: Mazabraud Syndrome-First Documented Case in Pakistan. [PDF]
Background Mazabraud syndrome (MS) is a rare benign genetic disorder characterized by the coexistence of fibrous dysplasia (FD) and intramuscular myxoma (IM), with a very limited number of cases reported worldwide, and none has been documented in Pakistan until now. It typically presents in middle‐aged females and affects the lower limbs.
Faisal A +6 more
europepmc +2 more sources
Fibrous dysplasia is a disease that causes aberrant development of osteoblasts, which results in fibrous stroma replacing normal bone. Lichtenstein first described it in 1938. It is a sporadic disorder caused due to a postzygotic mutation in the
R B Revanth +5 more
doaj +1 more source
Jaffe Lichtenstein Type Polyostotic Fibrous Dysplasia with Unilateral Absent Testis [PDF]
Fibrous dysplasias are developmental bone disorders in which the medullary cavity is replaced by fibrous tissue. It can be monostotic involving a single bone or polyostotic involving multiple bones.
Anand Ramakrishnan +3 more
doaj +1 more source
Case report of rib polyostotic fibrous dysplasia
Polyostotic fibrous dysplasia is a rare benign asymptomatic tumour of the ribs not requiring surgery on most occasions. We present here a case with left 10th and 11th rib fibrous dysplasia which was causing a hinderance to the Urologist for renal stone ...
Mohamed Magdy Abd Elalim +3 more
semanticscholar +1 more source
Background Intramedullary nailing (IN) seems to be the best primary surgical treatment for patients with either polyostotic fibrous dysplasia or McCune–Albright syndrome (PFD/MAS) when the femur and tibia are totally affected by fibrous dysplasia (FD ...
E. Ippolito +5 more
semanticscholar +1 more source
Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases.
Yang Il Park +2 more
doaj +1 more source
Polyostotic Fibrous Dysplasia in a Six-year-Old Boy
Fibrous dysplasia (FD) is a rare congenital benign bone disease that manifests as a defect in the bone remodeling process, affecting the function, differentiation, and maturation of osteoblasts.
N. Manevska +4 more
semanticscholar +1 more source
ABSTRACT This study aimed to evaluate the prevalence of and risk factors for coxa vara deformity in patients with fibrous dysplasia/McCune‐Albright syndrome (FD/MAS). This study was conducted at the National Institutes of Health and Leiden University Medical Center. All patients with any subtype of FD/MAS, FD involving the proximal femur, one or more X‐
Maartje E. Meier +7 more
wiley +1 more source

