Sarcomatous transformation (Leiomyosarcoma) in polyostotic fibrous dysplagia
Malignant changes in polyostotic fibrous dysplasia are very rare. Most common malignancies reported are osteosarcoma and fibrosarcoma, chondrosarcoma and malignant fibrous histiocytoma. Here, we report a previously diagnosed case of fibrous dysplasia who
M K Garg+5 more
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Fibro-osseous lesion of maxilla. Report of two cases in a family with review of literature [PDF]
Fibrous dysplasia is a disturbance of bone metabolism that is classified as a benign fibro-osseous lesion. Fibrous connective tissue containing abnormal bone, replaces normal bone. The etiology of fibrous dysplasia is unknown.
Kaur, Bhawandeep+2 more
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Prevention of pathological fracture in fibrous dysplasia of proximal femur in a 24-year-old female a rare presentation - a case report [PDF]
Fibrous dysplasia (FD) was historically mentioned in the medical literature in 1938 by Dr. Lichtenstein and in 1942 by Dr. Lichtenstein and Jaffe. The term Jaffe-Lichtenstein syndrome is sometimes used synonymously with monostotic FD or to denote cases ...
Mhatre, Jayesh, Modi, Nihar, Supe, Amit
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Radioiodine treatment in McCune-Albright syndrome with hyperthyroidism
McCune-Albright syndrome (MAS) is a sporadic disease characterized by polyostotic fibrous dysplasia, "café-au-lait" spots and hyperfunctional endocrinopathies.
Dhritiman Chakraborty+5 more
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Clinical, microscopic and imaging findings associated to Mccune-Albright syndrome: report of two cases [PDF]
McCune-Albright syndrome is characterized by the triad café-au-lait cutaneous spots, polyostotic fibrous dysplasia and endocrinopathies. This article presents two cases of McCune-Albright syndrome in a middle-aged woman and a young girl.
BRENTEGANI, Luiz Guilherme+4 more
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Management of fibro-osseous lesions of the craniofacial area: presentation of 19 cases and review of the literature [PDF]
Introduction: Fibro-osseous lesions constitute a rare benign type of pathology with a non-odontogenic lineage that affect the craniofacial area. According to Waldrom's classification, these lesions are divided into: fibrous dysplasia (FD), cemento ...
Baquero Ruiz de la Hermosa, María del Carmen+6 more
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Polyostotic fibrous dysplasia without craniofacial involvement: An unusual presentation
Fibrous dysplasia (FD) is a benign bone disorder resulting into the replacement of bone with fibrous tissue. These fibrous bones are prone for deformities, pain, and pathological fractures, hence requiring treatment.
Seema Sharma+3 more
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Shepherd’s Crook Deformity with Pathological Femur Neck Fracture in a Patient with Fibrous Dysplasia Managed with Proximal Femoral Nailing and Valgus Osteotomy [PDF]
Fibrous dysplasia is a rare condition in which bone is replaced by fibroosseous tissue. It is a benign condition, divided into monostotic and polyostotic fibrous dysplasia, which accounts for about 5-7% of all benign bone tumours. Here, authors reported
Neetin P Mahajan+4 more
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Use of Denosumab in Children With Osteoclast Bone Dysplasias: Report of Three Cases. [PDF]
Denosumab has been used successfully to treat disease-associated osteoclast overactivity, including giant cell tumor of bone. Given its mechanism of action, denosumab is a potent potential treatment of other osteoclast bone dysplasias including central ...
Bernthal, Nicholas M+8 more
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Evolução da displasia fibrosa óssea na síndrome de McCune Albright [PDF]
McCune Albright syndrome is a rare disorder characterized by polyostotic fibrous dysplasia, café-au-lait spots and some endocrine hyperfunction, mostly precocious puberty.
Dias-da-Silva, Magnus Régios [UNIFESP]+3 more
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