Results 171 to 180 of about 1,294 (181)

Design and efficient synthesis of novel GM2 analogues with respect to the elucidation of the function of GM2 activator

Glycoconjugate Journal, 2008
Akihiro Imamura, Yu-Teh Li, Hideharu Ishida   +2 more
exaly  

Synthesis of novel NBD-GM1 and NBD-GM2 for the transfer activity of GM2-activator protein by a FRET-based assay system

Glycobiology, 2005
Günter Schwarzmann, Konrad Sandhoff
exaly  

Assay of the GM2-ganglioside cleaving hexosaminidase activity of skin fibroblasts for GM2-gangliosidoses

Clinica Chimica Acta, 1983
openaire   +2 more sources

Structural Analysis of Lipid Complexes of GM2-Activator Protein

Journal of Molecular Biology, 2003
exaly  

Photoaffinity labelling of the Human GM2-activator protein. Mechanistic insight into ganglioside GM2 degradation

FEBS Journal, 2004
Daniel Hoffmann, Thomas Kolter, Konrad Sandhoff   +2 more
exaly  

The GM2 activator protein, its roles as a co-factor in GM2 hydrolysis and as a general glycolipid transport protein

Lipids and Lipid Metabolism, 1998
exaly  

GM2 gangliosidoses

openaire   +1 more source

New mouse models of GM2 gangliosidoses

Lab Animal
openaire   +1 more source

Isolation of a cDNA encoding the human GM2 activator protein

FEBS Letters, 1989
exaly  

Gangliosidoses: Understanding disease evolution in GM1 and GM2

Molecular Genetics and Metabolism
Roberto Giugliani, Paul Harmatz, Bénédicte Héron, Andreas Hahn, Marc Patterson, Aurélie Bourchany, Daniel A.D. Valle, Rita Maria Elisa Barone, Brigitte Chabrol, Anna Ardissone, Spyros Batzios, Maurizio Scarpa, Susanne A. Schneider, Nicoleta Carp, Christian Freitag, Aidan Gill, Laura López de Frutos   +16 more
openaire   +1 more source