Results 111 to 120 of about 5,767 (207)
Glutaric aciduria type 1 (GA1) is an inherited neurometabolic disorder, in which deficiency of glutaryl‐CoA dehydrogenase leads to accumulation of glutaric acid (GA) and 3‐hydroxyglutaric acid (3‐HG).
Denis Cyr +3 more
doaj +1 more source
: As an enzyme, β-mannanase (BM) can be widely used as feed additive to improve the growth performance of animals. This experiment aimed to determine the effect of the addition of BM to low-energy diet on the immune function and intestinal microflora of ...
Xiaodan Zhang +4 more
doaj +1 more source
Método para reconstrução in silico de redes metabólicas de fungos : um estudo de caso para o Paracoccidioides lutzii [PDF]
Dissertação (mestrado)—Universidade de Brasília, Instituto de Ciências Exatas, Departamento de Ciência da Computação, 2014.Os fungos produzem uma variedade de metabólitos com aplicações na indústria e na medicina, ao mesmo tempo que podem ser patógenos ...
Silva, Waldeyr Mendes Cordeiro da
core
Background Polyhydroxyalkanoates (PHAs), biodegradable polymers, can be synthesised and degraded by a number of bacteria. With a range of monomer composition and molecular weight, these polymers can be used for packaging to medical applications. However,
Yixin Che +7 more
doaj +1 more source
Intraventricular Baclofen for Treatment of Severe Dystonia Associated with Glutaryl-CoA Dehydrogenase Deficiency (GA1): Report of Two Cases. [PDF]
Ghatan S +3 more
europepmc +1 more source
Genetic Screening of Selected Disease-Causing Mutations in Glutaryl-CoA Dehydrogenase Gene among Indian Patients with Glutaric Aciduria Type I. [PDF]
Tp KV +4 more
europepmc +1 more source
Glutaryl-CoA dehydrogenase: a key biomarker linking lysine degradation to hepatocellular carcinoma metastasis and prognosis via NF-KB signaling pathway. [PDF]
Hu Q +6 more
europepmc +1 more source
Pyropheophytin a accompanies pheophytin a in darkened light grown cells of Euglena [PDF]
Rüdiger, W. +4 more
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Prevention of Disease in Glutaryl-CoA Dehydrogenase Deficiency (GDD) 859 [PDF]
G F Hoffmann +9 more
openaire +1 more source

